Id |
Subject |
Object |
Predicate |
Lexical cue |
TextSentencer_T1 |
0-152 |
Sentence |
denotes |
Alternative splicing in COL1A1 mRNA leads to a partial null allele and two In-frame forms with structural defects in non-lethal osteogenesis imperfecta. |
TextSentencer_T2 |
153-292 |
Sentence |
denotes |
We have identified a novel multiexon genomic deletion in one COL1A1 collagen allele that results in three alternative forms of mutant mRNA. |
TextSentencer_T3 |
293-415 |
Sentence |
denotes |
This mutation occurs in a 9-year-old girl and her father, both affected with severe type III osteogenesis imperfecta (OI). |
TextSentencer_T4 |
416-547 |
Sentence |
denotes |
We previously reported detection of a mismatch in their alpha1(I) amino acids 558-861 region by RNA/RNA hybrid analysis (Grange, D. |
TextSentencer_T5 |
548-565 |
Sentence |
denotes |
K., Gottesman, G. |
TextSentencer_T6 |
566-579 |
Sentence |
denotes |
S., Lewis, M. |
TextSentencer_T7 |
580-598 |
Sentence |
denotes |
B., and Marini, J. |
TextSentencer_T8 |
599-627 |
Sentence |
denotes |
C. (1990) Nucleic Acids Res. |
TextSentencer_T9 |
628-643 |
Sentence |
denotes |
18, 4227-4236). |
TextSentencer_T10 |
644-763 |
Sentence |
denotes |
Single Strand Conformational Polymorphism further localized the mRNA mutation to the amino acids 579-679 coding region. |
TextSentencer_T11 |
764-963 |
Sentence |
denotes |
At the gene level, polymerase chain reaction (PCR) amplification of patient leukocyte DNA from the exon 33-38 region yielded the normal 1004-base pair (bp) fragment and an additional 442-bp fragment. |
TextSentencer_T12 |
964-1148 |
Sentence |
denotes |
Sequencing of the shorter genomic PCR product confirmed the presence of a 562-bp deletion, extending from the last 3 nucleotides (nt) of exon 34 to 156 nt from the 3'-end of intron 36. |
TextSentencer_T13 |
1149-1267 |
Sentence |
denotes |
The genomic deletion was also detected in the clinically normal grandmother, who was confirmed to be a mosaic carrier. |
TextSentencer_T14 |
1268-1402 |
Sentence |
denotes |
PCR amplification and RNase protection experiments were used to investigate the mRNA structure and occurrence of alternative splicing. |
TextSentencer_T15 |
1403-1505 |
Sentence |
denotes |
One form of the mutant cDNA has a deletion with end points that are identical to the genomic deletion. |
TextSentencer_T16 |
1506-1659 |
Sentence |
denotes |
This results in a combination deletion/insertion, with a deletion of amino acids 603-639 followed by an insertion of 156 nt from the 3'-end of intron 36. |
TextSentencer_T17 |
1660-1714 |
Sentence |
denotes |
In addition, we found two alternatively spliced forms. |
TextSentencer_T18 |
1715-1786 |
Sentence |
denotes |
One form uses a cryptic donor site in exon 34 and the exon 37 acceptor. |
TextSentencer_T19 |
1787-1861 |
Sentence |
denotes |
The second form uses the normal exon 32 splice donor and exon 37 acceptor. |
TextSentencer_T20 |
1862-1937 |
Sentence |
denotes |
Use of the cryptic donor results in a coding sequence that is out-of-frame. |
TextSentencer_T21 |
1938-2051 |
Sentence |
denotes |
Both the retained intron form and the use of the exon 32 donor site result in coding sequences that are in-frame. |
TextSentencer_T22 |
2052-2186 |
Sentence |
denotes |
This is the first report of a collagen defect in OI with alternative splicing generating both in-frame and out-of-frame forms of mRNA. |
TextSentencer_T23 |
2187-2315 |
Sentence |
denotes |
Although the in-frame forms constitute more than 60% of the mRNA from the mutant allele, no mutant protein chain was identified. |
TextSentencer_T24 |
2316-2465 |
Sentence |
denotes |
Collagen produced by cultured OI osteoblasts showed a significant increase in the relative amount of type III collagen but no mutant alpha1(I) chain. |
T1 |
0-152 |
Sentence |
denotes |
Alternative splicing in COL1A1 mRNA leads to a partial null allele and two In-frame forms with structural defects in non-lethal osteogenesis imperfecta. |
T2 |
153-292 |
Sentence |
denotes |
We have identified a novel multiexon genomic deletion in one COL1A1 collagen allele that results in three alternative forms of mutant mRNA. |
T3 |
293-415 |
Sentence |
denotes |
This mutation occurs in a 9-year-old girl and her father, both affected with severe type III osteogenesis imperfecta (OI). |
T4 |
416-547 |
Sentence |
denotes |
We previously reported detection of a mismatch in their alpha1(I) amino acids 558-861 region by RNA/RNA hybrid analysis (Grange, D. |
T5 |
548-565 |
Sentence |
denotes |
K., Gottesman, G. |
T6 |
566-579 |
Sentence |
denotes |
S., Lewis, M. |
T7 |
580-598 |
Sentence |
denotes |
B., and Marini, J. |
T8 |
599-627 |
Sentence |
denotes |
C. (1990) Nucleic Acids Res. |
T9 |
628-643 |
Sentence |
denotes |
18, 4227-4236). |
T10 |
644-763 |
Sentence |
denotes |
Single Strand Conformational Polymorphism further localized the mRNA mutation to the amino acids 579-679 coding region. |
T11 |
764-963 |
Sentence |
denotes |
At the gene level, polymerase chain reaction (PCR) amplification of patient leukocyte DNA from the exon 33-38 region yielded the normal 1004-base pair (bp) fragment and an additional 442-bp fragment. |
T12 |
964-1148 |
Sentence |
denotes |
Sequencing of the shorter genomic PCR product confirmed the presence of a 562-bp deletion, extending from the last 3 nucleotides (nt) of exon 34 to 156 nt from the 3'-end of intron 36. |
T13 |
1149-1267 |
Sentence |
denotes |
The genomic deletion was also detected in the clinically normal grandmother, who was confirmed to be a mosaic carrier. |
T14 |
1268-1402 |
Sentence |
denotes |
PCR amplification and RNase protection experiments were used to investigate the mRNA structure and occurrence of alternative splicing. |
T15 |
1403-1505 |
Sentence |
denotes |
One form of the mutant cDNA has a deletion with end points that are identical to the genomic deletion. |
T16 |
1506-1659 |
Sentence |
denotes |
This results in a combination deletion/insertion, with a deletion of amino acids 603-639 followed by an insertion of 156 nt from the 3'-end of intron 36. |
T17 |
1660-1714 |
Sentence |
denotes |
In addition, we found two alternatively spliced forms. |
T18 |
1715-1786 |
Sentence |
denotes |
One form uses a cryptic donor site in exon 34 and the exon 37 acceptor. |
T19 |
1787-1861 |
Sentence |
denotes |
The second form uses the normal exon 32 splice donor and exon 37 acceptor. |
T20 |
1862-1937 |
Sentence |
denotes |
Use of the cryptic donor results in a coding sequence that is out-of-frame. |
T21 |
1938-2051 |
Sentence |
denotes |
Both the retained intron form and the use of the exon 32 donor site result in coding sequences that are in-frame. |
T22 |
2052-2186 |
Sentence |
denotes |
This is the first report of a collagen defect in OI with alternative splicing generating both in-frame and out-of-frame forms of mRNA. |
T23 |
2187-2315 |
Sentence |
denotes |
Although the in-frame forms constitute more than 60% of the mRNA from the mutant allele, no mutant protein chain was identified. |
T24 |
2316-2465 |
Sentence |
denotes |
Collagen produced by cultured OI osteoblasts showed a significant increase in the relative amount of type III collagen but no mutant alpha1(I) chain. |