PubMed:2303461
Annnotations
sentences
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 0-95 | Sentence | denotes | A missense mutation at Ile172----Asn or Arg356----Trp causes steroid 21-hydroxylase deficiency. |
T2 | 96-232 | Sentence | denotes | Congenital adrenal hyperplasia (CAH) is a common recessive genetic disease caused mainly by steroid 21-hydroxylase (P450c21) deficiency. |
T3 | 233-309 | Sentence | denotes | Many forms of CAH exist resulting from various mutations of the CYP21B gene. |
T4 | 310-412 | Sentence | denotes | We sequenced CYP21B cDNA from a normal person and its genes from a patient with simple virilizing CAH. |
T5 | 413-482 | Sentence | denotes | When comparing several CYP21B sequences, we found it was polymorphic. |
T6 | 483-636 | Sentence | denotes | In the patient, a single base substitution replaced Ile172 (ATC) with Asn (AAC) in one allele while Arg356 (CGG) was converted to Trp (TGG) in the other. |
T7 | 637-796 | Sentence | denotes | A normal P450c21 cDNA clone was transfected into COS-1 cells to produce 21-hydroxylase activity toward its substrates, progesterone and 17-hydroxyprogesterone. |
T8 | 797-923 | Sentence | denotes | Mutants corresponding to Asn172 or Trp356 mutation were constructed by site-directed mutagenesis of the normal c21 cDNA clone. |
T9 | 924-1067 | Sentence | denotes | They failed to produce active enzyme toward either substrate upon transfection into COS-1 cells, demonstrating that these mutations caused CAH. |
T10 | 1068-1214 | Sentence | denotes | Aligning sequences with other P450s, Ile172 could be located in the membrane anchoring domain and Arg356 in the substrate-binding site of P450c21. |
T11 | 1215-1350 | Sentence | denotes | Both mutations are present in the CYP21A1P pseudogene, suggesting that they may be transferred from CYP21A1P by gene conversion events. |
T1 | 0-95 | Sentence | denotes | A missense mutation at Ile172----Asn or Arg356----Trp causes steroid 21-hydroxylase deficiency. |
T2 | 96-232 | Sentence | denotes | Congenital adrenal hyperplasia (CAH) is a common recessive genetic disease caused mainly by steroid 21-hydroxylase (P450c21) deficiency. |
T3 | 233-309 | Sentence | denotes | Many forms of CAH exist resulting from various mutations of the CYP21B gene. |
T4 | 310-412 | Sentence | denotes | We sequenced CYP21B cDNA from a normal person and its genes from a patient with simple virilizing CAH. |
T5 | 413-482 | Sentence | denotes | When comparing several CYP21B sequences, we found it was polymorphic. |
T6 | 483-636 | Sentence | denotes | In the patient, a single base substitution replaced Ile172 (ATC) with Asn (AAC) in one allele while Arg356 (CGG) was converted to Trp (TGG) in the other. |
T7 | 637-796 | Sentence | denotes | A normal P450c21 cDNA clone was transfected into COS-1 cells to produce 21-hydroxylase activity toward its substrates, progesterone and 17-hydroxyprogesterone. |
T8 | 797-923 | Sentence | denotes | Mutants corresponding to Asn172 or Trp356 mutation were constructed by site-directed mutagenesis of the normal c21 cDNA clone. |
T9 | 924-1067 | Sentence | denotes | They failed to produce active enzyme toward either substrate upon transfection into COS-1 cells, demonstrating that these mutations caused CAH. |
T10 | 1068-1214 | Sentence | denotes | Aligning sequences with other P450s, Ile172 could be located in the membrane anchoring domain and Arg356 in the substrate-binding site of P450c21. |
T11 | 1215-1350 | Sentence | denotes | Both mutations are present in the CYP21A1P pseudogene, suggesting that they may be transferred from CYP21A1P by gene conversion events. |
DisGeNET
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T0 | 323-329 | gene:1589 | denotes | CYP21B |
T1 | 408-411 | disease:C0520463 | denotes | CAH |
R1 | T0 | T1 | associated_with | CYP21B,CAH |
PubmedHPO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 96-126 | HP_0008258 | denotes | Congenital adrenal hyperplasia |
T2 | 107-126 | HP_0008221 | denotes | adrenal hyperplasia |
DisGeNET5_variant_disease
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
2303461-0#23#36#geners6475 | 23-36 | geners6475 | denotes | Ile172----Asn |
2303461-0#40#53#geners7769409 | 40-53 | geners7769409 | denotes | Arg356----Trp |
2303461-0#61#94#diseaseC0268287 | 61-94 | diseaseC0268287 | denotes | steroid 21-hydroxylase deficiency |
23#36#geners647561#94#diseaseC0268287 | 2303461-0#23#36#geners6475 | 2303461-0#61#94#diseaseC0268287 | associated_with | Ile172----Asn,steroid 21-hydroxylase deficiency |
40#53#geners776940961#94#diseaseC0268287 | 2303461-0#40#53#geners7769409 | 2303461-0#61#94#diseaseC0268287 | associated_with | Arg356----Trp,steroid 21-hydroxylase deficiency |
DisGeNET5_gene_disease
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
2303461-1#92#114#gene1589 | 188-210 | gene1589 | denotes | steroid 21-hydroxylase |
2303461-1#116#123#gene1589 | 212-219 | gene1589 | denotes | P450c21 |
2303461-1#0#30#diseaseC0001627 | 96-126 | diseaseC0001627 | denotes | Congenital adrenal hyperplasia |
2303461-3#13#19#gene1589 | 323-329 | gene1589 | denotes | CYP21B |
2303461-3#98#101#diseaseC0520463 | 408-411 | diseaseC0520463 | denotes | CAH |
92#114#gene15890#30#diseaseC0001627 | 2303461-1#92#114#gene1589 | 2303461-1#0#30#diseaseC0001627 | associated_with | steroid 21-hydroxylase,Congenital adrenal hyperplasia |
116#123#gene15890#30#diseaseC0001627 | 2303461-1#116#123#gene1589 | 2303461-1#0#30#diseaseC0001627 | associated_with | P450c21,Congenital adrenal hyperplasia |
13#19#gene158998#101#diseaseC0520463 | 2303461-3#13#19#gene1589 | 2303461-3#98#101#diseaseC0520463 | associated_with | CYP21B,CAH |
PubCasesHPO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
AB1 | 96-126 | HP:0008258 | denotes | Congenital adrenal hyperplasia |
mondo_disease
Id | Subject | Object | Predicate | Lexical cue | mondo_id |
---|---|---|---|---|---|
T1 | 69-94 | Disease | denotes | 21-hydroxylase deficiency | http://purl.obolibrary.org/obo/MONDO_0008728 |
T2 | 96-126 | Disease | denotes | Congenital adrenal hyperplasia | http://purl.obolibrary.org/obo/MONDO_0015898 |
T3 | 107-126 | Disease | denotes | adrenal hyperplasia | http://purl.obolibrary.org/obo/MONDO_0018479 |
T4 | 128-131 | Disease | denotes | CAH | http://purl.obolibrary.org/obo/MONDO_0018479|http://purl.obolibrary.org/obo/MONDO_0015898 |
T6 | 155-170 | Disease | denotes | genetic disease | http://purl.obolibrary.org/obo/MONDO_0003847 |
T7 | 247-250 | Disease | denotes | CAH | http://purl.obolibrary.org/obo/MONDO_0018479|http://purl.obolibrary.org/obo/MONDO_0015898 |
T9 | 408-411 | Disease | denotes | CAH | http://purl.obolibrary.org/obo/MONDO_0018479|http://purl.obolibrary.org/obo/MONDO_0015898 |
T11 | 1063-1066 | Disease | denotes | CAH | http://purl.obolibrary.org/obo/MONDO_0018479|http://purl.obolibrary.org/obo/MONDO_0015898 |
NCBITAXON
Id | Subject | Object | Predicate | Lexical cue | db_id |
---|---|---|---|---|---|
T1 | 377-384 | OrganismTaxon | denotes | patient | 9606 |
T2 | 490-497 | OrganismTaxon | denotes | patient | 9606 |
Anatomy-UBERON
Id | Subject | Object | Predicate | Lexical cue | uberon_id |
---|---|---|---|---|---|
T1 | 107-114 | Body_part | denotes | adrenal | http://purl.obolibrary.org/obo/UBERON_0002369 |
T2 | 1136-1144 | Body_part | denotes | membrane | http://purl.obolibrary.org/obo/GO_0016020|http://purl.obolibrary.org/obo/UBERON_0000094|http://purl.obolibrary.org/obo/UBERON_0000158 |
HP-phenotype
Id | Subject | Object | Predicate | Lexical cue | hp_id |
---|---|---|---|---|---|
T1 | 96-126 | Phenotype | denotes | Congenital adrenal hyperplasia | HP:0008258 |
T2 | 128-131 | Phenotype | denotes | CAH | HP:0008258 |
T3 | 247-250 | Phenotype | denotes | CAH | HP:0008258 |
T4 | 408-411 | Phenotype | denotes | CAH | HP:0008258 |
T5 | 1063-1066 | Phenotype | denotes | CAH | HP:0008258 |