PubMed:17273972
Annnotations
PMID_GLOBAL
Id | Subject | Object | Predicate | Lexical cue | mondo_id |
---|---|---|---|---|---|
T1 | 107-132 | DiseaseOrPhenotypicFeature | denotes | Deletion 22q11.2 syndrome | 0008644 |
T2 | 174-182 | DiseaseOrPhenotypicFeature | denotes | syndrome | 0002254 |
T3 | 269-297 | DiseaseOrPhenotypicFeature | denotes | (velocardiofacial) syndromes | 0008564|0008644|0018923 |
T6 | 527-552 | DiseaseOrPhenotypicFeature | denotes | 22q11.2 deletion syndrome | 0018923 |
T7 | 778-797 | DiseaseOrPhenotypicFeature | denotes | Shprintzen syndrome | 0008564|0008644|0018923 |
T10 | 1020-1023 | DiseaseOrPhenotypicFeature | denotes | can | 0012833 |
TEST-DiseaseOrPhenotypicFeature
Id | Subject | Object | Predicate | Lexical cue | #label |
---|---|---|---|---|---|
T1 | 88-105 | DiseaseOrPhenotypicFeature | denotes | 22q11.2 deletions | DISEASE |
T2 | 107-132 | DiseaseOrPhenotypicFeature | denotes | Deletion 22q11.2 syndrome | D004062 |
T3 | 269-297 | DiseaseOrPhenotypicFeature | denotes | (velocardiofacial) syndromes | D004062 |
T4 | 527-552 | DiseaseOrPhenotypicFeature | denotes | 22q11.2 deletion syndrome | D004062 |
T5 | 778-797 | DiseaseOrPhenotypicFeature | denotes | Shprintzen syndrome | D004062 |
TEST-OrganismTaxon
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 0-5 | OrganismTaxon | denotes | Human |
Test-SequenceVariant
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 749-754 | SequenceVariant | denotes | H194Q |
Test-GeneOrGeneProduct
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 6-10 | GeneOrGeneProduct | denotes | TBX1 |
T2 | 334-360 | GeneOrGeneProduct | denotes | T-box transcription factor |
T3 | 366-370 | GeneOrGeneProduct | denotes | TBX1 |
T4 | 454-458 | GeneOrGeneProduct | denotes | TBX1 |
T5 | 913-941 | GeneOrGeneProduct | denotes | stabilization of the protein |
T6 | 988-992 | GeneOrGeneProduct | denotes | TBX1 |
Test-merged
Id | Subject | Object | Predicate | Lexical cue | #label |
---|---|---|---|---|---|
T5 | 778-797 | DiseaseOrPhenotypicFeature | denotes | Shprintzen syndrome | D004062 |
T4 | 527-552 | DiseaseOrPhenotypicFeature | denotes | 22q11.2 deletion syndrome | D004062 |
T3 | 269-297 | DiseaseOrPhenotypicFeature | denotes | (velocardiofacial) syndromes | D004062 |
T2 | 107-132 | DiseaseOrPhenotypicFeature | denotes | Deletion 22q11.2 syndrome | D004062 |
T1 | 88-105 | DiseaseOrPhenotypicFeature | denotes | 22q11.2 deletions | DISEASE |
T72605 | 0-5 | OrganismTaxon | denotes | Human | |
T6 | 988-992 | GeneOrGeneProduct | denotes | TBX1 | |
T40572 | 913-941 | GeneOrGeneProduct | denotes | stabilization of the protein | |
T41249 | 454-458 | GeneOrGeneProduct | denotes | TBX1 | |
T50773 | 366-370 | GeneOrGeneProduct | denotes | TBX1 | |
T68578 | 334-360 | GeneOrGeneProduct | denotes | T-box transcription factor | |
T5046 | 6-10 | GeneOrGeneProduct | denotes | TBX1 | |
T32535 | 749-754 | SequenceVariant | denotes | H194Q |
Test-merged-2
Id | Subject | Object | Predicate | Lexical cue | #label |
---|---|---|---|---|---|
T32535 | 749-754 | SequenceVariant | denotes | H194Q | |
T5046 | 6-10 | GeneOrGeneProduct | denotes | TBX1 | |
T68578 | 334-360 | GeneOrGeneProduct | denotes | T-box transcription factor | |
T50773 | 366-370 | GeneOrGeneProduct | denotes | TBX1 | |
T41249 | 454-458 | GeneOrGeneProduct | denotes | TBX1 | |
T40572 | 913-941 | GeneOrGeneProduct | denotes | stabilization of the protein | |
T6 | 988-992 | GeneOrGeneProduct | denotes | TBX1 | |
T72605 | 0-5 | OrganismTaxon | denotes | Human | |
T1 | 88-105 | DiseaseOrPhenotypicFeature | denotes | 22q11.2 deletions | DISEASE |
T2 | 107-132 | DiseaseOrPhenotypicFeature | denotes | Deletion 22q11.2 syndrome | D004062 |
T3 | 269-297 | DiseaseOrPhenotypicFeature | denotes | (velocardiofacial) syndromes | D004062 |
T4 | 527-552 | DiseaseOrPhenotypicFeature | denotes | 22q11.2 deletion syndrome | D004062 |
T5 | 778-797 | DiseaseOrPhenotypicFeature | denotes | Shprintzen syndrome | D004062 |
sentences
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
TextSentencer_T1 | 0-106 | Sentence | denotes | Human TBX1 missense mutations cause gain of function resulting in the same phenotype as 22q11.2 deletions. |
TextSentencer_T2 | 107-298 | Sentence | denotes | Deletion 22q11.2 syndrome is the most frequent known microdeletion syndrome and is associated with a highly variable phenotype, including DiGeorge and Shprintzen (velocardiofacial) syndromes. |
TextSentencer_T3 | 299-553 | Sentence | denotes | Although haploinsufficiency of the T-box transcription factor gene TBX1 is thought to cause the phenotype, to date, only four different point mutations in TBX1 have been reported in association with six of the major features of 22q11.2 deletion syndrome. |
TextSentencer_T4 | 554-698 | Sentence | denotes | Although, for the two truncating mutations, loss of function was previously shown, the pathomechanism of the missense mutations remains unknown. |
TextSentencer_T5 | 699-960 | Sentence | denotes | We report a novel heterozygous missense mutation, H194Q, in a familial case of Shprintzen syndrome and show that this and the two previously reported missense mutations result in gain of function, possibly through stabilization of the protein dimer DNA complex. |
TextSentencer_T6 | 961-1135 | Sentence | denotes | We therefore conclude that TBX1 gain-of-function mutations can result in the same phenotypic spectrum as haploinsufficiency caused by loss-of-function mutations or deletions. |
T1 | 0-106 | Sentence | denotes | Human TBX1 missense mutations cause gain of function resulting in the same phenotype as 22q11.2 deletions. |
T2 | 107-298 | Sentence | denotes | Deletion 22q11.2 syndrome is the most frequent known microdeletion syndrome and is associated with a highly variable phenotype, including DiGeorge and Shprintzen (velocardiofacial) syndromes. |
T3 | 299-553 | Sentence | denotes | Although haploinsufficiency of the T-box transcription factor gene TBX1 is thought to cause the phenotype, to date, only four different point mutations in TBX1 have been reported in association with six of the major features of 22q11.2 deletion syndrome. |
T4 | 554-698 | Sentence | denotes | Although, for the two truncating mutations, loss of function was previously shown, the pathomechanism of the missense mutations remains unknown. |
T5 | 699-960 | Sentence | denotes | We report a novel heterozygous missense mutation, H194Q, in a familial case of Shprintzen syndrome and show that this and the two previously reported missense mutations result in gain of function, possibly through stabilization of the protein dimer DNA complex. |
T6 | 961-1135 | Sentence | denotes | We therefore conclude that TBX1 gain-of-function mutations can result in the same phenotypic spectrum as haploinsufficiency caused by loss-of-function mutations or deletions. |
DisGeNET
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T0 | 366-370 | gene:6899 | denotes | TBX1 |
T1 | 527-552 | disease:C0012236 | denotes | 22q11.2 deletion syndrome |
T2 | 366-370 | gene:6899 | denotes | TBX1 |
T3 | 527-552 | disease:C0220704 | denotes | 22q11.2 deletion syndrome |
T4 | 454-458 | gene:6899 | denotes | TBX1 |
T5 | 527-552 | disease:C0012236 | denotes | 22q11.2 deletion syndrome |
T6 | 454-458 | gene:6899 | denotes | TBX1 |
T7 | 527-552 | disease:C0220704 | denotes | 22q11.2 deletion syndrome |
R1 | T0 | T1 | associated_with | TBX1,22q11.2 deletion syndrome |
R2 | T2 | T3 | associated_with | TBX1,22q11.2 deletion syndrome |
R3 | T4 | T5 | associated_with | TBX1,22q11.2 deletion syndrome |
R4 | T6 | T7 | associated_with | TBX1,22q11.2 deletion syndrome |
PubCasesORDO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
AB1 | 270-297 | ORDO:567 | denotes | velocardiofacial) syndromes |
AB2 | 778-797 | ORDO:567 | denotes | Shprintzen syndrome |
tmVarCorpus
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 749-754 | ProteinMutation:p|SUB|H|194|Q | denotes | H194Q |