PubMed:11087738
Annnotations
sentences
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 0-181 | Sentence | denotes | A 7-kDa prion protein (PrP) fragment, an integral component of the PrP region required for infectivity, is the major amyloid protein in Gerstmann-Sträussler-Scheinker disease A117V. |
T2 | 182-318 | Sentence | denotes | Gerstmann-Sträussler-Scheinker disease (GSS) is a cerebral amyloidosis associated with mutations in the prion protein (PrP) gene (PRNP). |
T3 | 319-537 | Sentence | denotes | The aim of this study was to characterize amyloid peptides purified from brain tissue of a patient with the A117V mutation who was Met/Val heterozygous at codon 129, Val(129) being in coupling phase with mutant Val117. |
T4 | 538-626 | Sentence | denotes | The major peptide extracted from amyloid fibrils was a approximately 7-kDa PrP fragment. |
T5 | 627-798 | Sentence | denotes | Sequence analysis and mass spectrometry showed that this fragment had ragged N and C termini, starting mainly at Gly88 and Gly90 and ending with Arg148, Glu152, or Asn153. |
T6 | 799-919 | Sentence | denotes | Only Val was present at positions 117 and 129, indicating that the amyloid protein originated from mutant PrP molecules. |
T7 | 920-1086 | Sentence | denotes | In addition to the approximately 7-kDa peptides, the amyloid fraction contained N- and C-terminal PrP fragments corresponding to residues 23-41, 191-205, and 217-228. |
T8 | 1087-1267 | Sentence | denotes | Fibrillogenesis in vitro with synthetic peptides corresponding to PrP fragments extracted from brain tissue showed that peptide PrP-(85-148) readily assembled into amyloid fibrils. |
T9 | 1268-1415 | Sentence | denotes | Peptide PrP-(191-205) also formed fibrillary structures although with different morphology, whereas peptides PrP-(23-41) and PrP-(217-228) did not. |
T10 | 1416-1563 | Sentence | denotes | These findings suggest that the processing of mutant PrP isoforms associated with Gerstmann-Sträussler-Scheinker disease may occur extracellularly. |
T11 | 1564-1867 | Sentence | denotes | It is conceivable that full-length PrP and/or large PrP peptides are deposited in the extracellular compartment, partially degraded by proteases and further digested by tissue endopeptidases, originating a approximately 7-kDa protease-resistant core that is similar in patients with different mutations. |
T12 | 1868-1976 | Sentence | denotes | Furthermore, the present data suggest that C-terminal fragments of PrP may participate in amyloid formation. |
Glycosmos6-MAT
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 392-397 | http://purl.obolibrary.org/obo/MAT_0000098 | denotes | brain |
T2 | 1182-1187 | http://purl.obolibrary.org/obo/MAT_0000098 | denotes | brain |
DisGeNET5_variant_disease
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
11087738-0#175#180#geners74315402 | 175-180 | geners74315402 | denotes | A117V |
11087738-0#136#174#diseaseC0017495 | 136-174 | diseaseC0017495 | denotes | Gerstmann-Sträussler-Scheinker disease |
11087738-2#108#113#geners74315402 | 427-432 | geners74315402 | denotes | A117V |
11087738-2#42#49#diseaseC0002726 | 361-368 | diseaseC0002726 | denotes | amyloid |
175#180#geners74315402136#174#diseaseC0017495 | 11087738-0#175#180#geners74315402 | 11087738-0#136#174#diseaseC0017495 | associated_with | A117V,Gerstmann-Sträussler-Scheinker disease |
108#113#geners7431540242#49#diseaseC0002726 | 11087738-2#108#113#geners74315402 | 11087738-2#42#49#diseaseC0002726 | associated_with | A117V,amyloid |
DisGeNET5_gene_disease
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
11087738-0#8#21#gene5621 | 8-21 | gene5621 | denotes | prion protein |
11087738-0#23#26#gene5621 | 23-26 | gene5621 | denotes | PrP |
11087738-0#67#70#gene5621 | 67-70 | gene5621 | denotes | PrP |
11087738-0#136#174#diseaseC0017495 | 136-174 | diseaseC0017495 | denotes | Gerstmann-Sträussler-Scheinker disease |
11087738-11#67#70#gene5621 | 1935-1938 | gene5621 | denotes | PrP |
11087738-11#90#97#diseaseC0002726 | 1958-1965 | diseaseC0002726 | denotes | amyloid |
8#21#gene5621136#174#diseaseC0017495 | 11087738-0#8#21#gene5621 | 11087738-0#136#174#diseaseC0017495 | associated_with | prion protein,Gerstmann-Sträussler-Scheinker disease |
23#26#gene5621136#174#diseaseC0017495 | 11087738-0#23#26#gene5621 | 11087738-0#136#174#diseaseC0017495 | associated_with | PrP,Gerstmann-Sträussler-Scheinker disease |
67#70#gene5621136#174#diseaseC0017495 | 11087738-0#67#70#gene5621 | 11087738-0#136#174#diseaseC0017495 | associated_with | PrP,Gerstmann-Sträussler-Scheinker disease |
67#70#gene562190#97#diseaseC0002726 | 11087738-11#67#70#gene5621 | 11087738-11#90#97#diseaseC0002726 | associated_with | PrP,amyloid |
PubCasesHPO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
AB1 | 241-252 | HP:0011034 | denotes | amyloidosis |
DisGeNET
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T0 | 8-21 | gene:5621 | denotes | prion protein |
T1 | 136-174 | disease:C0017495 | denotes | Gerstmann-Sträussler-Scheinker disease |
T2 | 23-26 | gene:5621 | denotes | PrP |
T3 | 136-174 | disease:C0017495 | denotes | Gerstmann-Sträussler-Scheinker disease |
T4 | 67-70 | gene:5621 | denotes | PrP |
T5 | 136-174 | disease:C0017495 | denotes | Gerstmann-Sträussler-Scheinker disease |
R1 | T0 | T1 | associated_with | prion protein,Gerstmann-Sträussler-Scheinker disease |
R2 | T2 | T3 | associated_with | PrP,Gerstmann-Sträussler-Scheinker disease |
R3 | T4 | T5 | associated_with | PrP,Gerstmann-Sträussler-Scheinker disease |
mondo_disease
Id | Subject | Object | Predicate | Lexical cue | mondo_id |
---|---|---|---|---|---|
T1 | 117-124 | Disease | denotes | amyloid | http://purl.obolibrary.org/obo/MONDO_0019065 |
T2 | 136-174 | Disease | denotes | Gerstmann-Sträussler-Scheinker disease | http://purl.obolibrary.org/obo/MONDO_0007656 |
T3 | 182-220 | Disease | denotes | Gerstmann-Sträussler-Scheinker disease | http://purl.obolibrary.org/obo/MONDO_0007656 |
T4 | 222-225 | Disease | denotes | GSS | http://purl.obolibrary.org/obo/MONDO_0007656 |
T5 | 241-252 | Disease | denotes | amyloidosis | http://purl.obolibrary.org/obo/MONDO_0019065 |
T6 | 361-368 | Disease | denotes | amyloid | http://purl.obolibrary.org/obo/MONDO_0019065 |
T7 | 571-578 | Disease | denotes | amyloid | http://purl.obolibrary.org/obo/MONDO_0019065 |
T8 | 866-873 | Disease | denotes | amyloid | http://purl.obolibrary.org/obo/MONDO_0019065 |
T9 | 973-980 | Disease | denotes | amyloid | http://purl.obolibrary.org/obo/MONDO_0019065 |
T10 | 1251-1258 | Disease | denotes | amyloid | http://purl.obolibrary.org/obo/MONDO_0019065 |
T11 | 1498-1536 | Disease | denotes | Gerstmann-Sträussler-Scheinker disease | http://purl.obolibrary.org/obo/MONDO_0007656 |
T12 | 1958-1965 | Disease | denotes | amyloid | http://purl.obolibrary.org/obo/MONDO_0019065 |
Anatomy-MAT
Id | Subject | Object | Predicate | Lexical cue | mat_id |
---|---|---|---|---|---|
T1 | 392-397 | Body_part | denotes | brain | http://purl.obolibrary.org/obo/MAT_0000098 |
T2 | 1182-1187 | Body_part | denotes | brain | http://purl.obolibrary.org/obo/MAT_0000098 |
HP-phenotype
Id | Subject | Object | Predicate | Lexical cue | hp_id |
---|---|---|---|---|---|
T1 | 241-252 | Phenotype | denotes | amyloidosis | HP:0011034 |
NCBITAXON
Id | Subject | Object | Predicate | Lexical cue | db_id |
---|---|---|---|---|---|
T1 | 410-417 | OrganismTaxon | denotes | patient | 9606 |
Anatomy-UBERON
Id | Subject | Object | Predicate | Lexical cue | uberon_id |
---|---|---|---|---|---|
T1 | 392-397 | Body_part | denotes | brain | http://purl.obolibrary.org/obo/UBERON_0000955|http://purl.obolibrary.org/obo/UBERON_6110636 |
T3 | 398-404 | Body_part | denotes | tissue | http://purl.obolibrary.org/obo/UBERON_0000479 |
T4 | 1182-1187 | Body_part | denotes | brain | http://purl.obolibrary.org/obo/UBERON_0000955|http://purl.obolibrary.org/obo/UBERON_6110636 |
T6 | 1188-1194 | Body_part | denotes | tissue | http://purl.obolibrary.org/obo/UBERON_0000479 |
T7 | 1547-1562 | Body_part | denotes | extracellularly | http://purl.obolibrary.org/obo/GO_0005576 |
T8 | 1650-1663 | Body_part | denotes | extracellular | http://purl.obolibrary.org/obo/GO_0005576 |
T9 | 1733-1739 | Body_part | denotes | tissue | http://purl.obolibrary.org/obo/UBERON_0000479 |