PMC:1189074 / 12478-13069 JSONTXT

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{"target":"http://pubannotation.org/docs/sourcedb/PMC/sourceid/1189074","sourcedb":"PMC","sourceid":"1189074","source_url":"http://www.ncbi.nlm.nih.gov/pmc/1189074","text":"Urine organic acid analysis revealed that MCAD−/− mice developed an organic acid profile similar to MCAD-deficient human patients. Specifically, when fasted for 18 h, MCAD−/− mice developed significantly elevated concentrations of adipic, suberic, and sebacic acids and hexanoylglycine as compared to MCAD+/+ controls, which showed trace to no detectable amounts of the same organic acids (Table 1). Adipic acid is not specific to MCAD deficiency. 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