PubMed:8931695
Annnotations
sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TextSentencer_T1 | 0-91 | Sentence | denotes | Phenotypic and genotypic overlap between atelosteogenesis type 2 and diastrophic dysplasia. |
| TextSentencer_T2 | 92-363 | Sentence | denotes | Mutations in the diastrophic dysplasia sulfate transporter gene DTDST have been associated with a family of chondrodysplasias that comprises, in order of increasing severity, diastrophic dysplasia (DTD), atelosteogenesis type 2 (AO2), and achondrogenesis type 1B (ACG1B). |
| TextSentencer_T3 | 364-606 | Sentence | denotes | To learn more about the molecular basis of DTDST chondrodysplasias and about genotype-phenotype correlations, we studied fibroblast cultures of three new patients: one with AO-2, one with DTD, and one with an intermediate phenotype (AO2/DTD). |
| TextSentencer_T4 | 607-693 | Sentence | denotes | Reduced incorporation of inorganic sulfate into macromolecules was found in all three. |
| TextSentencer_T5 | 694-846 | Sentence | denotes | Each of the three patients was found to be heterozygous for a c862t transition predicting a R279W substitution in the third extracellular loop of DTDST. |
| TextSentencer_T6 | 847-1256 | Sentence | denotes | In two patients (DTD and AO2/DTD), no other structural mutation was found, but polymerase chain reaction amplification and single-strand conformation polymorphism analysis of fibroblast cDNA showed reduced mRNA levels of the wild-type DTDST allele: these two patients may be compound heterozygotes for the "Finnish" mutation (as yet uncharacterized at the DNA level), which causes reduced expression of DTDST. |
| TextSentencer_T7 | 1257-1437 | Sentence | denotes | The third patient (with AO2) had the R279W mutation compounded with a novel mutation, the deletion of cytosine 418 (delta c418), predicting a frameshift with premature termination. |
| TextSentencer_T8 | 1438-1586 | Sentence | denotes | Also the delta c418 allele was underrepresented in the cDNA, in accordance with previous observations that premature stop codons reduce mRNA levels. |
| TextSentencer_T9 | 1587-1718 | Sentence | denotes | The presence of the DTDST R279W mutation in a total of 11 patients with AO2 or DTD emphasizes the overlap between these conditions. |
| TextSentencer_T10 | 1719-1865 | Sentence | denotes | This mutation has not been found so far in 8 analyzed ACG1B patients, suggesting that it allows some residual activity of the sulfate transporter. |
| T1 | 0-91 | Sentence | denotes | Phenotypic and genotypic overlap between atelosteogenesis type 2 and diastrophic dysplasia. |
| T2 | 92-363 | Sentence | denotes | Mutations in the diastrophic dysplasia sulfate transporter gene DTDST have been associated with a family of chondrodysplasias that comprises, in order of increasing severity, diastrophic dysplasia (DTD), atelosteogenesis type 2 (AO2), and achondrogenesis type 1B (ACG1B). |
| T3 | 364-606 | Sentence | denotes | To learn more about the molecular basis of DTDST chondrodysplasias and about genotype-phenotype correlations, we studied fibroblast cultures of three new patients: one with AO-2, one with DTD, and one with an intermediate phenotype (AO2/DTD). |
| T4 | 607-693 | Sentence | denotes | Reduced incorporation of inorganic sulfate into macromolecules was found in all three. |
| T5 | 694-846 | Sentence | denotes | Each of the three patients was found to be heterozygous for a c862t transition predicting a R279W substitution in the third extracellular loop of DTDST. |
| T6 | 847-1256 | Sentence | denotes | In two patients (DTD and AO2/DTD), no other structural mutation was found, but polymerase chain reaction amplification and single-strand conformation polymorphism analysis of fibroblast cDNA showed reduced mRNA levels of the wild-type DTDST allele: these two patients may be compound heterozygotes for the "Finnish" mutation (as yet uncharacterized at the DNA level), which causes reduced expression of DTDST. |
| T7 | 1257-1437 | Sentence | denotes | The third patient (with AO2) had the R279W mutation compounded with a novel mutation, the deletion of cytosine 418 (delta c418), predicting a frameshift with premature termination. |
| T8 | 1438-1586 | Sentence | denotes | Also the delta c418 allele was underrepresented in the cDNA, in accordance with previous observations that premature stop codons reduce mRNA levels. |
| T9 | 1587-1718 | Sentence | denotes | The presence of the DTDST R279W mutation in a total of 11 patients with AO2 or DTD emphasizes the overlap between these conditions. |
| T10 | 1719-1865 | Sentence | denotes | This mutation has not been found so far in 8 analyzed ACG1B patients, suggesting that it allows some residual activity of the sulfate transporter. |
DisGeNET
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T0 | 131-150 | gene:1836 | denotes | sulfate transporter |
| T1 | 109-130 | disease:C0220726 | denotes | diastrophic dysplasia |
| T2 | 131-150 | gene:1836 | denotes | sulfate transporter |
| T3 | 200-217 | disease:C0343284 | denotes | chondrodysplasias |
| T4 | 131-150 | gene:1836 | denotes | sulfate transporter |
| T5 | 290-293 | disease:C0220726 | denotes | DTD |
| T6 | 131-150 | gene:1836 | denotes | sulfate transporter |
| T7 | 296-319 | disease:C1850554 | denotes | atelosteogenesis type 2 |
| T8 | 131-150 | gene:1836 | denotes | sulfate transporter |
| T9 | 356-361 | disease:C0265274 | denotes | ACG1B |
| T10 | 131-150 | gene:1836 | denotes | sulfate transporter |
| T11 | 331-354 | disease:C0265274 | denotes | achondrogenesis type 1B |
| T12 | 131-150 | gene:1836 | denotes | sulfate transporter |
| T13 | 321-324 | disease:C1850554 | denotes | AO2 |
| T14 | 407-412 | gene:1836 | denotes | DTDST |
| T15 | 413-430 | disease:C0343284 | denotes | chondrodysplasias |
| R1 | T0 | T1 | associated_with | sulfate transporter,diastrophic dysplasia |
| R2 | T2 | T3 | associated_with | sulfate transporter,chondrodysplasias |
| R3 | T4 | T5 | associated_with | sulfate transporter,DTD |
| R4 | T6 | T7 | associated_with | sulfate transporter,atelosteogenesis type 2 |
| R5 | T8 | T9 | associated_with | sulfate transporter,ACG1B |
| R6 | T10 | T11 | associated_with | sulfate transporter,achondrogenesis type 1B |
| R7 | T12 | T13 | associated_with | sulfate transporter,AO2 |
| R8 | T14 | T15 | associated_with | DTDST,chondrodysplasias |
DisGeNET5_variant_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 8931695-8#26#31#geners104893915 | 1613-1618 | geners104893915 | denotes | R279W |
| 8931695-8#72#75#diseaseC1850554 | 1659-1662 | diseaseC1850554 | denotes | AO2 |
| 8931695-8#79#82#diseaseC0220726 | 1666-1669 | diseaseC0220726 | denotes | DTD |
| 26#31#geners10489391572#75#diseaseC1850554 | 8931695-8#26#31#geners104893915 | 8931695-8#72#75#diseaseC1850554 | associated_with | R279W,AO2 |
| 26#31#geners10489391579#82#diseaseC0220726 | 8931695-8#26#31#geners104893915 | 8931695-8#79#82#diseaseC0220726 | associated_with | R279W,DTD |
DisGeNET5_gene_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 8931695-1#39#58#gene1836 | 131-150 | gene1836 | denotes | sulfate transporter |
| 8931695-1#239#262#diseaseC0265274 | 331-354 | diseaseC0265274 | denotes | achondrogenesis type 1B |
| 8931695-1#264#269#diseaseC0265274 | 356-361 | diseaseC0265274 | denotes | ACG1B |
| 8931695-2#43#48#gene1836 | 407-412 | gene1836 | denotes | DTDST |
| 8931695-2#49#66#diseaseC0343284 | 413-430 | diseaseC0343284 | denotes | chondrodysplasias |
| 8931695-8#20#25#gene1836 | 1607-1612 | gene1836 | denotes | DTDST |
| 8931695-8#72#75#diseaseC1850554 | 1659-1662 | diseaseC1850554 | denotes | AO2 |
| 8931695-8#79#82#diseaseC0220726 | 1666-1669 | diseaseC0220726 | denotes | DTD |
| 39#58#gene1836239#262#diseaseC0265274 | 8931695-1#39#58#gene1836 | 8931695-1#239#262#diseaseC0265274 | associated_with | sulfate transporter,achondrogenesis type 1B |
| 39#58#gene1836264#269#diseaseC0265274 | 8931695-1#39#58#gene1836 | 8931695-1#264#269#diseaseC0265274 | associated_with | sulfate transporter,ACG1B |
| 43#48#gene183649#66#diseaseC0343284 | 8931695-2#43#48#gene1836 | 8931695-2#49#66#diseaseC0343284 | associated_with | DTDST,chondrodysplasias |
| 20#25#gene183672#75#diseaseC1850554 | 8931695-8#20#25#gene1836 | 8931695-8#72#75#diseaseC1850554 | associated_with | DTDST,AO2 |
| 20#25#gene183679#82#diseaseC0220726 | 8931695-8#20#25#gene1836 | 8931695-8#79#82#diseaseC0220726 | associated_with | DTDST,DTD |
PubCasesORDO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| AB1 | 109-130 | ORDO:628 | denotes | diastrophic dysplasia |
| TI1 | 41-64 | ORDO:56304 | denotes | atelosteogenesis type 2 |
| TI2 | 69-90 | ORDO:628 | denotes | diastrophic dysplasia |
| AB2 | 267-288 | ORDO:628 | denotes | diastrophic dysplasia |
| AB3 | 296-319 | ORDO:56304 | denotes | atelosteogenesis type 2 |
NCBIDiseaseCorpus
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease:C535395 | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease:C536170 | denotes | diastrophic dysplasia |
| T3 | 109-130 | Modifier:C536170 | denotes | diastrophic dysplasia |
| T4 | 200-217 | DiseaseClass:D010009 | denotes | chondrodysplasias |
| T5 | 267-288 | SpecificDisease:C536170 | denotes | diastrophic dysplasia |
| T6 | 290-293 | SpecificDisease:C536170 | denotes | DTD |
| T7 | 296-319 | SpecificDisease:C535395 | denotes | atelosteogenesis type 2 |
| T8 | 321-324 | SpecificDisease:C535395 | denotes | AO2 |
| T9 | 331-354 | SpecificDisease:C536016 | denotes | achondrogenesis type 1B |
| T10 | 356-361 | SpecificDisease:C536016 | denotes | ACG1B |
| T11 | 407-430 | SpecificDisease:OMIM:222600 | denotes | DTDST chondrodysplasias |
| T12 | 537-541 | SpecificDisease:C535395 | denotes | AO-2 |
| T13 | 552-555 | SpecificDisease:C536170 | denotes | DTD |
| T14 | 597-600 | SpecificDisease:C535395 | denotes | AO2 |
| T15 | 601-604 | SpecificDisease:C536170 | denotes | DTD |
| T16 | 864-867 | SpecificDisease:C536170 | denotes | DTD |
| T17 | 872-875 | SpecificDisease:C535395 | denotes | AO2 |
| T18 | 876-879 | SpecificDisease:C536170 | denotes | DTD |
| T19 | 1281-1284 | SpecificDisease:C535395 | denotes | AO2 |
| T20 | 1659-1662 | SpecificDisease:C535395 | denotes | AO2 |
| T21 | 1666-1669 | SpecificDisease:C536170 | denotes | DTD |
| T22 | 1773-1778 | Modifier:C536016 | denotes | ACG1B |
ncbi-valid-gpt-nr-ng
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-294 | CompositeMention | denotes | diastrophic dysplasia (DTD) |
| T5 | 296-325 | CompositeMention | denotes | atelosteogenesis type 2 (AO2) |
| T6 | 331-362 | CompositeMention | denotes | achondrogenesis type 1B (ACG1B) |
| T7 | 413-430 | DiseaseClass | denotes | chondrodysplasias |
| T8 | 537-541 | SpecificDisease | denotes | AO-2 |
| T9 | 552-555 | SpecificDisease | denotes | DTD |
| T10 | 597-604 | CompositeMention | denotes | AO2/DTD |
ncbi-valid-gpt-r-g
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 407-430 | DiseaseClass | denotes | DTDST chondrodysplasias |
| T11 | 537-541 | SpecificDisease | denotes | AO-2 |
| T12 | 552-555 | SpecificDisease | denotes | DTD |
| T13 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T14 | 864-879 | CompositeMention | denotes | DTD and AO2/DTD |
| T15 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T16 | 1659-1669 | CompositeMention | denotes | AO2 or DTD |
| T17 | 1773-1778 | SpecificDisease | denotes | ACG1B |
ncbi-valid-gpt-nr-g
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 413-430 | DiseaseClass | denotes | chondrodysplasias |
| T11 | 537-541 | SpecificDisease | denotes | AO-2 |
| T12 | 552-555 | SpecificDisease | denotes | DTD |
| T13 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T14 | 840-843 | SpecificDisease | denotes | DTD |
| T15 | 872-879 | CompositeMention | denotes | AO2/DTD |
| T16 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T17 | 1659-1669 | CompositeMention | denotes | AO2 or DTD |
| T18 | 1773-1778 | Modifier | denotes | ACG1B |
ncbi-valid
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 109-130 | Modifier | denotes | diastrophic dysplasia |
| T4 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T5 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T6 | 290-293 | SpecificDisease | denotes | DTD |
| T7 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T8 | 321-324 | SpecificDisease | denotes | AO2 |
| T9 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T10 | 356-361 | SpecificDisease | denotes | ACG1B |
| T11 | 407-430 | SpecificDisease | denotes | DTDST chondrodysplasias |
| T12 | 537-541 | SpecificDisease | denotes | AO-2 |
| T13 | 552-555 | SpecificDisease | denotes | DTD |
| T14 | 597-600 | SpecificDisease | denotes | AO2 |
| T15 | 601-604 | SpecificDisease | denotes | DTD |
| T16 | 864-867 | SpecificDisease | denotes | DTD |
| T17 | 872-875 | SpecificDisease | denotes | AO2 |
| T18 | 876-879 | SpecificDisease | denotes | DTD |
| T19 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T20 | 1659-1662 | SpecificDisease | denotes | AO2 |
| T21 | 1666-1669 | SpecificDisease | denotes | DTD |
| T22 | 1773-1778 | Modifier | denotes | ACG1B |
ncbi-valid-gpt-r-ng
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 413-430 | DiseaseClass | denotes | chondrodysplasias |
| T11 | 537-541 | SpecificDisease | denotes | AO-2 |
| T12 | 552-555 | SpecificDisease | denotes | DTD |
| T13 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T14 | 840-843 | SpecificDisease | denotes | DTD |
| T15 | 872-879 | CompositeMention | denotes | AO2/DTD |
| T16 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T17 | 1659-1662 | SpecificDisease | denotes | AO2 |
| T18 | 1666-1669 | SpecificDisease | denotes | DTD |
| T19 | 1773-1778 | SpecificDisease | denotes | ACG1B |
ncbi-valid-gemini-nr-ng
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 407-430 | CompositeMention | denotes | DTDST chondrodysplasias |
| T11 | 537-541 | SpecificDisease | denotes | AO-2 |
| T12 | 552-555 | SpecificDisease | denotes | DTD |
| T13 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T14 | 872-875 | SpecificDisease | denotes | AO2 |
| T15 | 1082-1085 | SpecificDisease | denotes | DTD |
| T16 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T17 | 1773-1778 | SpecificDisease | denotes | ACG1B |
ncbi-valid-gemini-nr-g
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 407-430 | DiseaseClass | denotes | DTDST chondrodysplasias |
| T11 | 537-541 | SpecificDisease | denotes | AO-2 |
| T12 | 552-555 | SpecificDisease | denotes | DTD |
| T13 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T14 | 840-843 | SpecificDisease | denotes | DTD |
| T15 | 872-875 | SpecificDisease | denotes | AO2 |
| T16 | 1250-1253 | SpecificDisease | denotes | DTD |
| T17 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T18 | 1773-1778 | SpecificDisease | denotes | ACG1B |
ncbi-valid-gemini-r-g
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 413-430 | Modifier | denotes | chondrodysplasias |
| T11 | 537-541 | SpecificDisease | denotes | AO-2 |
| T12 | 552-555 | SpecificDisease | denotes | DTD |
| T13 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T14 | 872-875 | SpecificDisease | denotes | AO2 |
| T15 | 1659-1669 | CompositeMention | denotes | AO2 or DTD |
| T16 | 1773-1778 | SpecificDisease | denotes | ACG1B |
ncbi-valid-deepseek-nr-ng
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 156-159 | SpecificDisease | denotes | DTD |
| T4 | 290-293 | SpecificDisease | denotes | DTD |
| T5 | 321-324 | SpecificDisease | denotes | AO2 |
| T6 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T7 | 356-361 | SpecificDisease | denotes | ACG1B |
| T8 | 537-541 | SpecificDisease | denotes | AO-2 |
| T9 | 552-555 | SpecificDisease | denotes | DTD |
| T10 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T11 | 872-875 | SpecificDisease | denotes | AO2 |
| T12 | 1082-1085 | SpecificDisease | denotes | DTD |
| T13 | 1773-1778 | SpecificDisease | denotes | ACG1B |
ncbi-valid-deepseek-nr-g
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 0-91 | CompositeMention | denotes | Phenotypic and genotypic overlap between atelosteogenesis type 2 and diastrophic dysplasia. |
| T2 | 109-150 | Modifier | denotes | diastrophic dysplasia sulfate transporter |
| T3 | 156-161 | SpecificDisease | denotes | DTDST |
| T4 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T5 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T6 | 290-293 | SpecificDisease | denotes | DTD |
| T7 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T8 | 321-324 | SpecificDisease | denotes | AO2 |
| T9 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T10 | 356-361 | SpecificDisease | denotes | ACG1B |
| T11 | 407-430 | Modifier | denotes | DTDST chondrodysplasias |
| T12 | 537-541 | SpecificDisease | denotes | AO-2 |
| T13 | 552-555 | SpecificDisease | denotes | DTD |
| T14 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T15 | 840-843 | SpecificDisease | denotes | DTD |
| T16 | 864-867 | SpecificDisease | denotes | DTD |
| T17 | 872-879 | CompositeMention | denotes | AO2/DTD |
| T18 | 1082-1085 | SpecificDisease | denotes | DTD |
| T19 | 1250-1253 | SpecificDisease | denotes | DTD |
| T20 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T21 | 1607-1610 | SpecificDisease | denotes | DTD |
| T22 | 1659-1662 | SpecificDisease | denotes | AO2 |
| T23 | 1666-1669 | SpecificDisease | denotes | DTD |
ncbi-valid-deepseek-r-g
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 109-130 | SpecificDisease | denotes | diastrophic dysplasia |
| T4 | 156-159 | SpecificDisease | denotes | DTD |
| T5 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T6 | 290-293 | SpecificDisease | denotes | DTD |
| T7 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T8 | 321-324 | SpecificDisease | denotes | AO2 |
| T9 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T10 | 356-361 | SpecificDisease | denotes | ACG1B |
| T11 | 407-410 | SpecificDisease | denotes | DTD |
| T12 | 537-541 | SpecificDisease | denotes | AO-2 |
| T13 | 552-555 | SpecificDisease | denotes | DTD |
| T14 | 597-604 | CompositeMention | denotes | AO2/DTD |
ncbi-valid-deepseek-r-ng
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 131-161 | CompositeMention | denotes | sulfate transporter gene DTDST |
| T4 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T5 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T6 | 573-595 | Modifier | denotes | intermediate phenotype |
| T7 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T8 | 756-772 | Modifier | denotes | c862t transition |
| T9 | 786-804 | Modifier | denotes | R279W substitution |
| T10 | 1072-1081 | Modifier | denotes | wild-type |
| T11 | 1347-1371 | Modifier | denotes | deletion of cytosine 418 |
| T12 | 1373-1383 | Modifier | denotes | delta c418 |
| T13 | 1415-1436 | Modifier | denotes | premature termination |
ncbi-valid-gemini-r-ng
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 407-430 | CompositeMention | denotes | DTDST chondrodysplasias |
| T11 | 537-541 | SpecificDisease | denotes | AO-2 |
| T12 | 552-555 | SpecificDisease | denotes | DTD |
| T13 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T14 | 840-843 | SpecificDisease | denotes | DTD |
| T15 | 872-879 | CompositeMention | denotes | AO2/DTD |
| T16 | 1154-1161 | Modifier | denotes | Finnish |
| T17 | 1250-1253 | SpecificDisease | denotes | DTD |
| T18 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T19 | 1773-1778 | SpecificDisease | denotes | ACG1B |
ncbi-valid-gemini-r-m
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 407-412 | Modifier | denotes | DTDST |
| T11 | 413-430 | DiseaseClass | denotes | chondrodysplasias |
| T12 | 537-541 | SpecificDisease | denotes | AO-2 |
| T13 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T14 | 872-875 | SpecificDisease | denotes | AO2 |
| T15 | 1250-1253 | SpecificDisease | denotes | DTD |
| T16 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T17 | 1773-1778 | SpecificDisease | denotes | ACG1B |
ncbi-valid-gpt-r-m
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 407-430 | DiseaseClass | denotes | DTDST chondrodysplasias |
| T11 | 537-541 | SpecificDisease | denotes | AO-2 |
| T12 | 552-555 | SpecificDisease | denotes | DTD |
| T13 | 597-600 | SpecificDisease | denotes | AO2 |
| T14 | 601-604 | SpecificDisease | denotes | DTD |
| T15 | 840-843 | SpecificDisease | denotes | DTD |
| T16 | 872-875 | SpecificDisease | denotes | AO2 |
| T17 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T18 | 1659-1662 | SpecificDisease | denotes | AO2 |
| T19 | 1666-1669 | SpecificDisease | denotes | DTD |
| T20 | 1773-1778 | SpecificDisease | denotes | ACG1B |
ncbi-valid-deepseek-r-m
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T4 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T5 | 290-293 | SpecificDisease | denotes | DTD |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 321-324 | SpecificDisease | denotes | AO2 |
| T8 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T9 | 356-361 | SpecificDisease | denotes | ACG1B |
| T10 | 407-410 | SpecificDisease | denotes | DTD |
| T11 | 413-430 | DiseaseClass | denotes | chondrodysplasias |
| T12 | 537-541 | SpecificDisease | denotes | AO-2 |
| T13 | 552-555 | SpecificDisease | denotes | DTD |
| T14 | 597-604 | CompositeMention | denotes | AO2/DTD |
NCBI-Disease-Develop
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T462 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 | C535395 |
| T463 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia | C536170 |
| T464 | 109-130 | Modifier | denotes | diastrophic dysplasia | C536170 |
| T465 | 200-217 | DiseaseClass | denotes | chondrodysplasias | D010009 |
| T466 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia | C536170 |
| T467 | 290-293 | SpecificDisease | denotes | DTD | C536170 |
| T468 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 | C535395 |
| T469 | 321-324 | SpecificDisease | denotes | AO2 | C535395 |
| T470 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B | C536016 |
| T471 | 356-361 | SpecificDisease | denotes | ACG1B | C536016 |
| T472 | 407-430 | SpecificDisease | denotes | DTDST chondrodysplasias | OMIM:222600 |
| T473 | 537-541 | SpecificDisease | denotes | AO-2 | C535395 |
| T474 | 552-555 | SpecificDisease | denotes | DTD | C536170 |
| T475 | 597-600 | SpecificDisease | denotes | AO2 | C535395 |
| T476 | 601-604 | SpecificDisease | denotes | DTD | C536170 |
| T477 | 864-867 | SpecificDisease | denotes | DTD | C536170 |
| T478 | 872-875 | SpecificDisease | denotes | AO2 | C535395 |
| T479 | 876-879 | SpecificDisease | denotes | DTD | C536170 |
| T480 | 1281-1284 | SpecificDisease | denotes | AO2 | C535395 |
| T481 | 1659-1662 | SpecificDisease | denotes | AO2 | C535395 |
| T482 | 1666-1669 | SpecificDisease | denotes | DTD | C536170 |
| T483 | 1773-1778 | Modifier | denotes | ACG1B | C536016 |
NCBI-Disease-Corpus-All
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T462 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 | C535395 |
| T463 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia | C536170 |
| T464 | 109-130 | Modifier | denotes | diastrophic dysplasia | C536170 |
| T465 | 200-217 | DiseaseClass | denotes | chondrodysplasias | D010009 |
| T466 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia | C536170 |
| T467 | 290-293 | SpecificDisease | denotes | DTD | C536170 |
| T468 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 | C535395 |
| T469 | 321-324 | SpecificDisease | denotes | AO2 | C535395 |
| T470 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B | C536016 |
| T471 | 356-361 | SpecificDisease | denotes | ACG1B | C536016 |
| T472 | 407-430 | SpecificDisease | denotes | DTDST chondrodysplasias | OMIM:222600 |
| T473 | 537-541 | SpecificDisease | denotes | AO-2 | C535395 |
| T474 | 552-555 | SpecificDisease | denotes | DTD | C536170 |
| T475 | 597-600 | SpecificDisease | denotes | AO2 | C535395 |
| T476 | 601-604 | SpecificDisease | denotes | DTD | C536170 |
| T477 | 864-867 | SpecificDisease | denotes | DTD | C536170 |
| T478 | 872-875 | SpecificDisease | denotes | AO2 | C535395 |
| T479 | 876-879 | SpecificDisease | denotes | DTD | C536170 |
| T480 | 1281-1284 | SpecificDisease | denotes | AO2 | C535395 |
| T481 | 1659-1662 | SpecificDisease | denotes | AO2 | C535395 |
| T482 | 1666-1669 | SpecificDisease | denotes | DTD | C536170 |
| T483 | 1773-1778 | Modifier | denotes | ACG1B | C536016 |
NCBI-Disease-Corpus-2stage-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 109-130 | Modifier | denotes | diastrophic dysplasia |
| T4 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T5 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T8 | 413-430 | DiseaseClass | denotes | chondrodysplasias |
| T9 | 537-541 | SpecificDisease | denotes | AO-2 |
| T10 | 552-555 | SpecificDisease | denotes | DTD |
| T11 | 597-600 | CompositeMention | denotes | AO2 |
| T12 | 601-604 | CompositeMention | denotes | DTD |
| T13 | 864-867 | SpecificDisease | denotes | DTD |
| T14 | 872-875 | CompositeMention | denotes | AO2 |
| T15 | 876-879 | CompositeMention | denotes | DTD |
| T16 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T17 | 1659-1662 | SpecificDisease | denotes | AO2 |
| T18 | 1666-1669 | SpecificDisease | denotes | DTD |
| T19 | 1773-1778 | SpecificDisease | denotes | ACG1B |
NCBI-Disease-Corpus-rezarta-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 109-130 | Modifier | denotes | diastrophic dysplasia |
| T4 | 200-217 | DiseaseClass | denotes | chondrodysplasias |
| T5 | 267-288 | SpecificDisease | denotes | diastrophic dysplasia |
| T6 | 296-319 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T7 | 331-354 | SpecificDisease | denotes | achondrogenesis type 1B |
| T8 | 413-430 | DiseaseClass | denotes | chondrodysplasias |
| T9 | 597-604 | CompositeMention | denotes | AO2/DTD |
| T10 | 872-879 | CompositeMention | denotes | AO2/DTD |
| T11 | 1659-1662 | SpecificDisease | denotes | AO2 |
| T12 | 1666-1669 | SpecificDisease | denotes | DTD |
| T13 | 1773-1778 | SpecificDisease | denotes | ACG1B |
NCBI-Disease-Corpus-4oGuideline-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 109-130 | SpecificDisease | denotes | diastrophic dysplasia |
| T4 | 267-294 | SpecificDisease | denotes | diastrophic dysplasia (DTD) |
| T5 | 296-325 | SpecificDisease | denotes | atelosteogenesis type 2 (AO2) |
| T6 | 331-362 | SpecificDisease | denotes | achondrogenesis type 1B (ACG1B) |
| T7 | 537-541 | SpecificDisease | denotes | AO-2 |
| T8 | 552-555 | SpecificDisease | denotes | DTD |
| T9 | 864-867 | SpecificDisease | denotes | DTD |
| T10 | 1281-1284 | SpecificDisease | denotes | AO2 |
| T11 | 1659-1662 | SpecificDisease | denotes | AO2 |
| T12 | 1666-1669 | SpecificDisease | denotes | DTD |
| T13 | 1773-1778 | SpecificDisease | denotes | ACG1B |
NCBI-Disease-Corpus-Simple-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 41-64 | SpecificDisease | denotes | atelosteogenesis type 2 |
| T2 | 69-90 | SpecificDisease | denotes | diastrophic dysplasia |
| T3 | 109-130 | SpecificDisease | denotes | diastrophic dysplasia |
| T4 | 267-294 | SpecificDisease | denotes | diastrophic dysplasia (DTD) |
| T5 | 296-325 | SpecificDisease | denotes | atelosteogenesis type 2 (AO2) |
| T6 | 331-362 | SpecificDisease | denotes | achondrogenesis type 1B (ACG1B) |
| T7 | 537-541 | Modifier | denotes | AO-2 |
| T8 | 552-555 | Modifier | denotes | DTD |
| T9 | 573-605 | CompositeMention | denotes | intermediate phenotype (AO2/DTD) |
| T10 | 864-867 | Modifier | denotes | DTD |
| T11 | 872-879 | Modifier | denotes | AO2/DTD |
| T12 | 1281-1284 | Modifier | denotes | AO2 |
| T13 | 1659-1662 | SpecificDisease | denotes | AO2 |
| T14 | 1666-1669 | SpecificDisease | denotes | DTD |
| T15 | 1773-1778 | SpecificDisease | denotes | ACG1B |