Id |
Subject |
Object |
Predicate |
Lexical cue |
TextSentencer_T1 |
0-105 |
Sentence |
denotes |
Serine for glycine substitutions in type I collagen in two cases of type IV osteogenesis imperfecta (OI). |
TextSentencer_T2 |
106-169 |
Sentence |
denotes |
Additional evidence for a regional model of OI pathophysiology. |
TextSentencer_T3 |
170-335 |
Sentence |
denotes |
Serine for glycine substitutions in type I collagen have been described in seven cases of lethal type II osteogenesis imperfecta (OI), and six cases of nonlethal OI. |
TextSentencer_T4 |
336-478 |
Sentence |
denotes |
We describe here two cases of moderately severe type IV OI with serine substitutions at alpha 1(I) Gly352 and alpha 2(I) Gly922, respectively. |
TextSentencer_T5 |
479-581 |
Sentence |
denotes |
In both cases, G-->A point mutations were detected by RNase A cleavage of RNA/RNA and RNA/DNA hybrids. |
TextSentencer_T6 |
582-759 |
Sentence |
denotes |
These cases extend the location for serine substitutions producing the moderately severe OI phenotype to the alpha 2(I) chain and the amino-terminal end of the alpha 1(I) chain. |
TextSentencer_T7 |
760-848 |
Sentence |
denotes |
Their location supports a regional model of OI pathophysiology for serine substitutions. |
TextSentencer_T8 |
849-960 |
Sentence |
denotes |
The proband with alpha 2(I) Gly922-->Ser has both normal and overmodified forms of both type I collagen chains. |
TextSentencer_T9 |
961-1026 |
Sentence |
denotes |
The overmodified form has delayed migration of all CNBr peptides. |
TextSentencer_T10 |
1027-1076 |
Sentence |
denotes |
Helix thermal stability is decreased 4 degrees C. |
TextSentencer_T11 |
1077-1154 |
Sentence |
denotes |
The fibroblast collagen protein and RNA of her unaffected parents are normal. |
TextSentencer_T12 |
1155-1235 |
Sentence |
denotes |
However, the father was demonstrated to be a mosaic carrier using leukocyte DNA. |
TextSentencer_T13 |
1236-1443 |
Sentence |
denotes |
The fibroblasts of the proband whose serine substitution is at alpha 1(I) Gly352 synthesize type I procollagen chains with delayed electrophoretic migration; normally migrating forms are difficult to detect. |
TextSentencer_T14 |
1444-1493 |
Sentence |
denotes |
Only alpha 1(I) CB 8 displayed delayed migration. |
TextSentencer_T15 |
1494-1541 |
Sentence |
denotes |
Helix thermal stability is reduced 2 degrees C. |
TextSentencer_T16 |
1542-1574 |
Sentence |
denotes |
Parental genomic DNA was normal. |
T1 |
0-105 |
Sentence |
denotes |
Serine for glycine substitutions in type I collagen in two cases of type IV osteogenesis imperfecta (OI). |
T2 |
106-169 |
Sentence |
denotes |
Additional evidence for a regional model of OI pathophysiology. |
T3 |
170-335 |
Sentence |
denotes |
Serine for glycine substitutions in type I collagen have been described in seven cases of lethal type II osteogenesis imperfecta (OI), and six cases of nonlethal OI. |
T4 |
336-478 |
Sentence |
denotes |
We describe here two cases of moderately severe type IV OI with serine substitutions at alpha 1(I) Gly352 and alpha 2(I) Gly922, respectively. |
T5 |
479-581 |
Sentence |
denotes |
In both cases, G-->A point mutations were detected by RNase A cleavage of RNA/RNA and RNA/DNA hybrids. |
T6 |
582-759 |
Sentence |
denotes |
These cases extend the location for serine substitutions producing the moderately severe OI phenotype to the alpha 2(I) chain and the amino-terminal end of the alpha 1(I) chain. |
T7 |
760-848 |
Sentence |
denotes |
Their location supports a regional model of OI pathophysiology for serine substitutions. |
T8 |
849-960 |
Sentence |
denotes |
The proband with alpha 2(I) Gly922-->Ser has both normal and overmodified forms of both type I collagen chains. |
T9 |
961-1026 |
Sentence |
denotes |
The overmodified form has delayed migration of all CNBr peptides. |
T10 |
1027-1076 |
Sentence |
denotes |
Helix thermal stability is decreased 4 degrees C. |
T11 |
1077-1154 |
Sentence |
denotes |
The fibroblast collagen protein and RNA of her unaffected parents are normal. |
T12 |
1155-1235 |
Sentence |
denotes |
However, the father was demonstrated to be a mosaic carrier using leukocyte DNA. |
T13 |
1236-1443 |
Sentence |
denotes |
The fibroblasts of the proband whose serine substitution is at alpha 1(I) Gly352 synthesize type I procollagen chains with delayed electrophoretic migration; normally migrating forms are difficult to detect. |
T14 |
1444-1493 |
Sentence |
denotes |
Only alpha 1(I) CB 8 displayed delayed migration. |
T15 |
1494-1541 |
Sentence |
denotes |
Helix thermal stability is reduced 2 degrees C. |
T16 |
1542-1574 |
Sentence |
denotes |
Parental genomic DNA was normal. |