PubMed:7479827
Annnotations
DisGeNET
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T0 | 1320-1325 | gene:37 | denotes | VLCAD |
| T1 | 1340-1356 | disease:C0342784 | denotes | VLCAD deficiency |
| T2 | 1320-1325 | gene:37 | denotes | VLCAD |
| T3 | 1447-1461 | disease:C0878544 | denotes | cardiomyopathy |
| R1 | T0 | T1 | associated_with | VLCAD,VLCAD deficiency |
| R2 | T2 | T3 | associated_with | VLCAD,cardiomyopathy |
DisGeNET5_gene_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 7479827-5#43#48#gene37 | 716-721 | gene37 | denotes | VLCAD |
| 7479827-5#171#185#diseaseC0018790 | 844-858 | diseaseC0018790 | denotes | cardiac arrest |
| 7479827-8#47#52#gene37 | 1320-1325 | gene37 | denotes | VLCAD |
| 7479827-8#67#83#diseaseC3887523 | 1340-1356 | diseaseC3887523 | denotes | VLCAD deficiency |
| 7479827-8#174#188#diseaseC0878544 | 1447-1461 | diseaseC0878544 | denotes | cardiomyopathy |
| 43#48#gene37171#185#diseaseC0018790 | 7479827-5#43#48#gene37 | 7479827-5#171#185#diseaseC0018790 | associated_with | VLCAD,cardiac arrest |
| 47#52#gene3767#83#diseaseC3887523 | 7479827-8#47#52#gene37 | 7479827-8#67#83#diseaseC3887523 | associated_with | VLCAD,VLCAD deficiency |
| 47#52#gene37174#188#diseaseC0878544 | 7479827-8#47#52#gene37 | 7479827-8#174#188#diseaseC0878544 | associated_with | VLCAD,cardiomyopathy |
UBERON-AE
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| PD-UBERON-AE-B_T1 | 227-232 | http://purl.obolibrary.org/obo/UBERON_0000948 | denotes | heart |
| PD-UBERON-AE-B_T2 | 361-366 | http://purl.obolibrary.org/obo/UBERON_0002107 | denotes | liver |
sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TextSentencer_T1 | 0-142 | Sentence | denotes | Molecular basis of human mitochondrial very-long-chain acyl-CoA dehydrogenase deficiency causing cardiomyopathy and sudden death in childhood. |
| TextSentencer_T2 | 143-233 | Sentence | denotes | beta-Oxidation of long-chain fatty acids provides the major source of energy in the heart. |
| TextSentencer_T3 | 234-414 | Sentence | denotes | Defects in enzymes of the beta-oxidation pathway cause sudden, unexplained death in childhood, acute hepatic encephalopathy or liver failure, skeletal myopathy, and cardiomyopathy. |
| TextSentencer_T4 | 415-575 | Sentence | denotes | Very-long-chain acyl-CoA dehydrogenase [VLCAD; very-long-chain-acyl-CoA:(acceptor) 2,3-oxidoreductase, EC 1.3.99.13] catalyzes the first step in beta-oxidation. |
| TextSentencer_T5 | 576-672 | Sentence | denotes | We have isolated the human VLCAD cDNA and gene and determined the complete nucleotide sequences. |
| TextSentencer_T6 | 673-878 | Sentence | denotes | Polymerase chain reaction amplification of VLCAD mRNA and genomic exons defined the molecular defects in two patients with VLCAD deficiency who presented with unexplained cardiac arrest and cardiomyopathy. |
| TextSentencer_T7 | 879-1041 | Sentence | denotes | In one, a homozygous mutation in the consensus dinucleotide of the donor splice site (g+1-->a) was associated with universal skipping of the prior exon (exon 11). |
| TextSentencer_T8 | 1042-1272 | Sentence | denotes | The second patient was a compound heterozygote, with a missense mutation, C1837-->T, changing the arginine at residue 613 to tryptophan on one allele and a single base deletion at the intron-exon 6 boundary as the second mutation. |
| TextSentencer_T9 | 1273-1492 | Sentence | denotes | This initial delineation of human mutations in VLCAD suggests that VLCAD deficiency reduces myocardial fatty acid beta-oxidation and energy production and is associated with cardiomyopathy and sudden death in childhood. |
| T1 | 0-142 | Sentence | denotes | Molecular basis of human mitochondrial very-long-chain acyl-CoA dehydrogenase deficiency causing cardiomyopathy and sudden death in childhood. |
| T2 | 143-233 | Sentence | denotes | beta-Oxidation of long-chain fatty acids provides the major source of energy in the heart. |
| T3 | 234-414 | Sentence | denotes | Defects in enzymes of the beta-oxidation pathway cause sudden, unexplained death in childhood, acute hepatic encephalopathy or liver failure, skeletal myopathy, and cardiomyopathy. |
| T4 | 415-575 | Sentence | denotes | Very-long-chain acyl-CoA dehydrogenase [VLCAD; very-long-chain-acyl-CoA:(acceptor) 2,3-oxidoreductase, EC 1.3.99.13] catalyzes the first step in beta-oxidation. |
| T5 | 576-672 | Sentence | denotes | We have isolated the human VLCAD cDNA and gene and determined the complete nucleotide sequences. |
| T6 | 673-878 | Sentence | denotes | Polymerase chain reaction amplification of VLCAD mRNA and genomic exons defined the molecular defects in two patients with VLCAD deficiency who presented with unexplained cardiac arrest and cardiomyopathy. |
| T7 | 879-1041 | Sentence | denotes | In one, a homozygous mutation in the consensus dinucleotide of the donor splice site (g+1-->a) was associated with universal skipping of the prior exon (exon 11). |
| T8 | 1042-1272 | Sentence | denotes | The second patient was a compound heterozygote, with a missense mutation, C1837-->T, changing the arginine at residue 613 to tryptophan on one allele and a single base deletion at the intron-exon 6 boundary as the second mutation. |
| T9 | 1273-1492 | Sentence | denotes | This initial delineation of human mutations in VLCAD suggests that VLCAD deficiency reduces myocardial fatty acid beta-oxidation and energy production and is associated with cardiomyopathy and sudden death in childhood. |
PubCasesHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TI1 | 97-111 | HP:0001638 | denotes | cardiomyopathy |
| AB1 | 335-357 | HP:0002480 | denotes | hepatic encephalopathy |
| AB2 | 376-393 | HP:0003756 | denotes | skeletal myopathy |
| AB3 | 399-413 | HP:0001638 | denotes | cardiomyopathy |
| AB4 | 844-858 | HP:0001695 | denotes | cardiac arrest |
| AB5 | 863-877 | HP:0001638 | denotes | cardiomyopathy |
| AB6 | 1447-1461 | HP:0001638 | denotes | cardiomyopathy |
PubCasesORDO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TI1 | 39-88 | ORDO:26793 | denotes | very-long-chain acyl-CoA dehydrogenase deficiency |
| AB1 | 796-812 | ORDO:26793 | denotes | VLCAD deficiency |
| AB2 | 1340-1356 | ORDO:26793 | denotes | VLCAD deficiency |
performance-test
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| PD-UBERON-AE-B_T1 | 361-366 | http://purl.obolibrary.org/obo/UBERON_0002107 | denotes | liver |
| PD-UBERON-AE-B_T2 | 227-232 | http://purl.obolibrary.org/obo/UBERON_0000948 | denotes | heart |
NCBIDiseaseCorpus
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 39-88 | SpecificDisease:C536353 | denotes | very-long-chain acyl-CoA dehydrogenase deficiency |
| T2 | 97-111 | SpecificDisease:D009202 | denotes | cardiomyopathy |
| T3 | 116-128 | SpecificDisease:D003645 | denotes | sudden death |
| T4 | 289-314 | SpecificDisease:D003645 | denotes | sudden, unexplained death |
| T5 | 335-357 | SpecificDisease:D006501 | denotes | hepatic encephalopathy |
| T6 | 361-374 | SpecificDisease:D017093 | denotes | liver failure |
| T7 | 376-393 | SpecificDisease:D009135 | denotes | skeletal myopathy |
| T8 | 399-413 | SpecificDisease:D009202 | denotes | cardiomyopathy |
| T9 | 796-812 | SpecificDisease:C536353 | denotes | VLCAD deficiency |
| T10 | 844-858 | SpecificDisease:D006323 | denotes | cardiac arrest |
| T11 | 863-877 | SpecificDisease:D009202 | denotes | cardiomyopathy |
| T12 | 1340-1356 | SpecificDisease:C536353 | denotes | VLCAD deficiency |
| T13 | 1447-1461 | SpecificDisease:D009202 | denotes | cardiomyopathy |
| T14 | 1466-1478 | SpecificDisease:D003645 | denotes | sudden death |
NCBI-Disease-Train
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T4301 | 39-88 | SpecificDisease | denotes | very-long-chain acyl-CoA dehydrogenase deficiency | C536353 |
| T4302 | 97-111 | SpecificDisease | denotes | cardiomyopathy | D009202 |
| T4303 | 116-128 | SpecificDisease | denotes | sudden death | D003645 |
| T4304 | 289-314 | SpecificDisease | denotes | sudden, unexplained death | D003645 |
| T4305 | 335-357 | SpecificDisease | denotes | hepatic encephalopathy | D006501 |
| T4306 | 361-374 | SpecificDisease | denotes | liver failure | D017093 |
| T4307 | 376-393 | SpecificDisease | denotes | skeletal myopathy | D009135 |
| T4308 | 399-413 | SpecificDisease | denotes | cardiomyopathy | D009202 |
| T4309 | 796-812 | SpecificDisease | denotes | VLCAD deficiency | C536353 |
| T4310 | 844-858 | SpecificDisease | denotes | cardiac arrest | D006323 |
| T4311 | 863-877 | SpecificDisease | denotes | cardiomyopathy | D009202 |
| T4312 | 1340-1356 | SpecificDisease | denotes | VLCAD deficiency | C536353 |
| T4313 | 1447-1461 | SpecificDisease | denotes | cardiomyopathy | D009202 |
| T4314 | 1466-1478 | SpecificDisease | denotes | sudden death | D003645 |
NCBI-Disease-Corpus-All
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T4301 | 39-88 | SpecificDisease | denotes | very-long-chain acyl-CoA dehydrogenase deficiency | C536353 |
| T4302 | 97-111 | SpecificDisease | denotes | cardiomyopathy | D009202 |
| T4303 | 116-128 | SpecificDisease | denotes | sudden death | D003645 |
| T4304 | 289-314 | SpecificDisease | denotes | sudden, unexplained death | D003645 |
| T4305 | 335-357 | SpecificDisease | denotes | hepatic encephalopathy | D006501 |
| T4306 | 361-374 | SpecificDisease | denotes | liver failure | D017093 |
| T4307 | 376-393 | SpecificDisease | denotes | skeletal myopathy | D009135 |
| T4308 | 399-413 | SpecificDisease | denotes | cardiomyopathy | D009202 |
| T4309 | 796-812 | SpecificDisease | denotes | VLCAD deficiency | C536353 |
| T4310 | 844-858 | SpecificDisease | denotes | cardiac arrest | D006323 |
| T4311 | 863-877 | SpecificDisease | denotes | cardiomyopathy | D009202 |
| T4312 | 1340-1356 | SpecificDisease | denotes | VLCAD deficiency | C536353 |
| T4313 | 1447-1461 | SpecificDisease | denotes | cardiomyopathy | D009202 |
| T4314 | 1466-1478 | SpecificDisease | denotes | sudden death | D003645 |
NCBI-Disease-Corpus-2stage-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 97-111 | CompositeMention | denotes | cardiomyopathy |
| T2 | 116-141 | CompositeMention | denotes | sudden death in childhood |
| T3 | 289-327 | CompositeMention | denotes | sudden, unexplained death in childhood |
| T4 | 329-357 | SpecificDisease | denotes | acute hepatic encephalopathy |
| T5 | 361-374 | SpecificDisease | denotes | liver failure |
| T6 | 376-393 | SpecificDisease | denotes | skeletal myopathy |
| T7 | 399-413 | CompositeMention | denotes | cardiomyopathy |
| T8 | 796-812 | SpecificDisease | denotes | VLCAD deficiency |
| T9 | 863-877 | CompositeMention | denotes | cardiomyopathy |
| T10 | 1340-1356 | SpecificDisease | denotes | VLCAD deficiency |
| T11 | 1447-1461 | CompositeMention | denotes | cardiomyopathy |
| T12 | 1466-1491 | CompositeMention | denotes | sudden death in childhood |
NCBI-Disease-Corpus-rezarta-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 39-88 | SpecificDisease | denotes | very-long-chain acyl-CoA dehydrogenase deficiency |
| T2 | 97-128 | CompositeMention | denotes | cardiomyopathy and sudden death |
| T3 | 289-314 | SpecificDisease | denotes | sudden, unexplained death |
| T4 | 335-374 | CompositeMention | denotes | hepatic encephalopathy or liver failure |
| T5 | 385-393 | SpecificDisease | denotes | myopathy |
| T6 | 399-413 | SpecificDisease | denotes | cardiomyopathy |
| T7 | 796-812 | SpecificDisease | denotes | VLCAD deficiency |
| T8 | 844-877 | CompositeMention | denotes | cardiac arrest and cardiomyopathy |
| T9 | 1340-1356 | SpecificDisease | denotes | VLCAD deficiency |
| T10 | 1447-1478 | CompositeMention | denotes | cardiomyopathy and sudden death |
NCBI-Disease-Corpus-4oGuideline-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 39-88 | SpecificDisease | denotes | very-long-chain acyl-CoA dehydrogenase deficiency |
| T2 | 97-111 | SpecificDisease | denotes | cardiomyopathy |
| T3 | 116-141 | SpecificDisease | denotes | sudden death in childhood |
| T4 | 289-327 | SpecificDisease | denotes | sudden, unexplained death in childhood |
| T5 | 329-357 | SpecificDisease | denotes | acute hepatic encephalopathy |
| T6 | 361-374 | SpecificDisease | denotes | liver failure |
| T7 | 376-393 | SpecificDisease | denotes | skeletal myopathy |
| T8 | 399-413 | SpecificDisease | denotes | cardiomyopathy |
| T9 | 796-812 | SpecificDisease | denotes | VLCAD deficiency |
| T10 | 832-858 | SpecificDisease | denotes | unexplained cardiac arrest |
| T11 | 863-877 | SpecificDisease | denotes | cardiomyopathy |
| T12 | 1340-1356 | SpecificDisease | denotes | VLCAD deficiency |
| T13 | 1447-1461 | SpecificDisease | denotes | cardiomyopathy |
| T14 | 1466-1491 | SpecificDisease | denotes | sudden death in childhood |
NCBI-Disease-Corpus-Simple-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 39-88 | SpecificDisease | denotes | very-long-chain acyl-CoA dehydrogenase deficiency |
| T2 | 97-111 | SpecificDisease | denotes | cardiomyopathy |
| T3 | 116-141 | CompositeMention | denotes | sudden death in childhood |
| T4 | 289-327 | CompositeMention | denotes | sudden, unexplained death in childhood |
| T5 | 329-357 | SpecificDisease | denotes | acute hepatic encephalopathy |
| T6 | 361-374 | SpecificDisease | denotes | liver failure |
| T7 | 376-393 | SpecificDisease | denotes | skeletal myopathy |
| T8 | 399-413 | SpecificDisease | denotes | cardiomyopathy |
| T9 | 796-812 | SpecificDisease | denotes | VLCAD deficiency |
| T10 | 832-877 | CompositeMention | denotes | unexplained cardiac arrest and cardiomyopathy |
| T11 | 1340-1356 | SpecificDisease | denotes | VLCAD deficiency |
| T12 | 1447-1491 | CompositeMention | denotes | cardiomyopathy and sudden death in childhood |