PubMed:29054882
Annnotations
c_corpus
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T5 | 0-19 | D010300 | denotes | Parkinson's Disease |
| T6 | 0-19 | D010300 | denotes | Parkinson's Disease |
| T9 | 31-36 | PR:Q5S006 | denotes | LRRK2 |
| T10 | 31-36 | PR:000003033 | denotes | LRRK2 |
| T11 | 31-36 | PR:Q5S007 | denotes | LRRK2 |
| T12 | 49-55 | D010770 | denotes | Kinase |
| T13 | 72-88 | GO:0008021 | denotes | Synaptic Vesicle |
| T14 | 72-100 | GO:0048489 | denotes | Synaptic Vesicle Trafficking |
| T17 | 112-120 | UBERON:0001891 | denotes | Midbrain |
| T18 | 142-149 | D004194 | denotes | disease |
| T19 | 142-149 | D004194 | denotes | disease |
| T20 | 212-228 | UBERON:0002038 | denotes | substantia nigra |
| T21 | 306-311 | PR:Q5S006 | denotes | LRRK2 |
| T22 | 306-311 | PR:000003033 | denotes | LRRK2 |
| T23 | 306-311 | PR:Q5S007 | denotes | LRRK2 |
| T24 | 368-384 | GO:0008021 | denotes | synaptic vesicle |
| T26 | 434-439 | PR:Q5S006 | denotes | LRRK2 |
| T27 | 434-439 | PR:000003033 | denotes | LRRK2 |
| T28 | 434-439 | PR:Q5S007 | denotes | LRRK2 |
| T29 | 537-545 | SO:0000109 | denotes | mutation |
| T30 | 546-551 | PR:Q5S006 | denotes | LRRK2 |
| T31 | 546-551 | PR:000003033 | denotes | LRRK2 |
| T32 | 546-551 | PR:Q5S007 | denotes | LRRK2 |
| T33 | 570-581 | GO:0006897 | denotes | endocytosis |
| T34 | 593-601 | UBERON:0001891 | denotes | midbrain |
| T35 | 653-664 | GO:0006897 | denotes | endocytosis |
| T36 | 697-702 | PR:Q5S006 | denotes | LRRK2 |
| T37 | 697-702 | PR:000003033 | denotes | LRRK2 |
| T38 | 697-702 | PR:Q5S007 | denotes | LRRK2 |
| T39 | 703-718 | GO:0016301 | denotes | kinase activity |
| T40 | 777-782 | PR:Q5S006 | denotes | LRRK2 |
| T41 | 777-782 | PR:000003033 | denotes | LRRK2 |
| T42 | 777-782 | PR:Q5S007 | denotes | LRRK2 |
| T43 | 807-816 | UBERON:0001950 | denotes | neocortex |
| T44 | 854-865 | UBERON:0002421 | denotes | hippocampus |
| T45 | 854-865 | UBERON:0001954 | denotes | hippocampus |
| T46 | 854-865 | UBERON:0002961 | denotes | hippocampus |
| T47 | 880-885 | UBERON:6110636 | denotes | brain |
| T48 | 880-885 | UBERON:0000955 | denotes | brain |
| T49 | 930-938 | SO:0000109 | denotes | mutation |
| T50 | 992-1003 | GO:0006897 | denotes | endocytosis |
| T51 | 1037-1045 | SO:0000159 | denotes | deletion |
| T52 | 1049-1054 | PR:Q8CHC4 | denotes | SYNJ1 |
| T53 | 1049-1054 | PR:000015882 | denotes | SYNJ1 |
| T54 | 1049-1054 | PR:Q62910 | denotes | SYNJ1 |
| T55 | 1049-1054 | PR:O43426 | denotes | SYNJ1 |
| T57 | 1056-1062 | 615530 | denotes | PARK20 |
| T58 | 1067-1071 | SO:0000704 | denotes | gene |
| T59 | 1106-1118 | D020734 | denotes | Parkinsonism |
| T60 | 1106-1118 | D020734 | denotes | Parkinsonism |
| T61 | 1130-1135 | PR:Q8CHC4 | denotes | SYNJ1 |
| T62 | 1130-1135 | PR:000015882 | denotes | SYNJ1 |
| T63 | 1130-1135 | PR:Q62910 | denotes | SYNJ1 |
| T64 | 1130-1135 | PR:O43426 | denotes | SYNJ1 |
| T65 | 1143-1148 | PR:Q5S006 | denotes | LRRK2 |
| T66 | 1143-1148 | PR:000003033 | denotes | LRRK2 |
| T67 | 1143-1148 | PR:Q5S007 | denotes | LRRK2 |
| T68 | 1179-1190 | GO:0006897 | denotes | endocytosis |
| T69 | 1213-1223 | GO:0006887 | denotes | exocytosis |
| T71 | 1288-1292 | UBERON:0003101 | denotes | male |
| T72 | 1288-1292 | CHEBI:30780 | denotes | male |
| T73 | 1293-1297 | PR:000005054 | denotes | mice |
| T75 | 1293-1297 | O89094 | denotes | mice |
| T74 | 1293-1297 | D051379 | denotes | mice |
| T76 | 1293-1297 | 10095 | denotes | mice |
| T77 | 1327-1332 | PR:Q5S006 | denotes | LRRK2 |
| T78 | 1327-1332 | PR:000003033 | denotes | LRRK2 |
| T79 | 1327-1332 | PR:Q5S007 | denotes | LRRK2 |
| T82 | 1357-1370 | Q62910 | denotes | synaptojanin1 |
| T83 | 1357-1370 | PR:000015882 | denotes | synaptojanin1 |
| T84 | 1357-1370 | O18964 | denotes | synaptojanin1 |
| T85 | 1357-1370 | Q8CHC4 | denotes | synaptojanin1 |
| T87 | 1357-1370 | O43426 | denotes | synaptojanin1 |
| T86 | 1357-1370 | C097702 | denotes | synaptojanin1 |
| T90 | 1423-1436 | Q62910 | denotes | synaptojanin1 |
| T91 | 1423-1436 | PR:000015882 | denotes | synaptojanin1 |
| T92 | 1423-1436 | O18964 | denotes | synaptojanin1 |
| T93 | 1423-1436 | Q8CHC4 | denotes | synaptojanin1 |
| T95 | 1423-1436 | O43426 | denotes | synaptojanin1 |
| T94 | 1423-1436 | C097702 | denotes | synaptojanin1 |
| T96 | 1465-1476 | GO:0006897 | denotes | endocytosis |
| T97 | 1507-1512 | PR:Q5S006 | denotes | LRRK2 |
| T98 | 1507-1512 | PR:000003033 | denotes | LRRK2 |
| T99 | 1507-1512 | PR:Q5S007 | denotes | LRRK2 |
| T100 | 1517-1522 | PR:Q8CHC4 | denotes | SYNJ1 |
| T101 | 1517-1522 | PR:000015882 | denotes | SYNJ1 |
| T102 | 1517-1522 | PR:Q62910 | denotes | SYNJ1 |
| T103 | 1517-1522 | PR:O43426 | denotes | SYNJ1 |
| T104 | 1637-1649 | GO:0009405 | denotes | pathogenesis |
| T105 | 1687-1695 | UBERON:0001891 | denotes | midbrain |
| T106 | 1719-1725 | CL:0000540 | denotes | neuron |
| T107 | 1848-1853 | UBERON:0001021 | denotes | nerve |
| T108 | 1848-1862 | GO:0044306 | denotes | nerve terminal |
| T109 | 1957-1961 | 168600 | denotes | PARK |
| T110 | 1969-1974 | PR:Q5S006 | denotes | LRRK2 |
| T111 | 1969-1974 | PR:000003033 | denotes | LRRK2 |
| T112 | 1969-1974 | PR:Q5S007 | denotes | LRRK2 |
| T115 | 1976-1981 | PR:000003033 | denotes | PARK8 |
| T116 | 1976-1981 | PR:Q5S007 | denotes | PARK8 |
| T114 | 1976-1981 | 607060 | denotes | PARK8 |
| T117 | 1987-1992 | PR:Q8CHC4 | denotes | SYNJ1 |
| T118 | 1987-1992 | PR:000015882 | denotes | SYNJ1 |
| T119 | 1987-1992 | PR:Q62910 | denotes | SYNJ1 |
| T120 | 1987-1992 | PR:O43426 | denotes | SYNJ1 |
| T122 | 1994-2000 | 615530 | denotes | PARK20 |
| T123 | 2036-2051 | GO:0016301 | denotes | kinase activity |
| T124 | 2092-2100 | SO:0000109 | denotes | mutation |
| T125 | 2104-2109 | PR:Q5S006 | denotes | LRRK2 |
| T126 | 2104-2109 | PR:000003033 | denotes | LRRK2 |
| T127 | 2104-2109 | PR:Q5S007 | denotes | LRRK2 |
| T128 | 2177-2182 | PR:Q5S006 | denotes | LRRK2 |
| T129 | 2177-2182 | PR:000003033 | denotes | LRRK2 |
| T130 | 2177-2182 | PR:Q5S007 | denotes | LRRK2 |
| T131 | 2194-2199 | PR:Q8CHC4 | denotes | SYNJ1 |
| T132 | 2194-2199 | PR:000015882 | denotes | SYNJ1 |
| T133 | 2194-2199 | PR:Q62910 | denotes | SYNJ1 |
| T134 | 2194-2199 | PR:O43426 | denotes | SYNJ1 |
| T135 | 2244-2251 | CHEBI:34922 | denotes | pathway |
| T136 | 2276-2282 | CL:0000540 | denotes | neuron |
| T137 | 2286-2297 | GO:0006897 | denotes | endocytosis |
PubMed_ArguminSci
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 130-265 | DRI_Background | denotes | Parkinson's disease (PD) is characterized pathologically by the selective loss of substantia nigra (SN) dopaminergic (DAergic) neurons. |
| T2 | 266-402 | DRI_Background | denotes | Recent evidence has suggested a role of LRRK2, linked to the most frequent familial PD, in regulating synaptic vesicle (SV) trafficking. |
| T3 | 403-499 | DRI_Background | denotes | However, the mechanism whereby LRRK2 mutants contribute to nigral vulnerability remains unclear. |
| T4 | 500-545 | DRI_Outcome | denotes | Here we show that the most common PD mutation |
| T5 | 559-719 | DRI_Outcome | denotes | impairs SV endocytosis in ventral midbrain (MB) neurons, including DA neurons, and the slowed endocytosis can be rescued by inhibition of LRRK2 kinase activity. |
| T6 | 720-939 | DRI_Challenge | denotes | A similar endocytic defect, however, was not observed in LRRK2 mutant neurons from the neocortex (hereafter, cortical neurons) or the hippocampus, suggesting a brain region-specific vulnerability to the G2019S mutation. |
| T7 | 940-1119 | DRI_Approach | denotes | Additionally, we found MB-specific impairment of SV endocytosis in neurons carrying heterozygous deletion of SYNJ1 (PARK20), a gene that is associated with recessive Parkinsonism. |
| T8 | 1120-1142 | DRI_Outcome | denotes | Combining SYNJ1+/- and |
| T9 | 1156-1298 | DRI_Outcome | denotes | does not exacerbate SV endocytosis but impairs sustained exocytosis in MB neurons and alters specific motor functions of 1-year-old male mice. |
| T10 | 1299-1477 | DRI_Outcome | denotes | Interestingly, we show that LRRK2 directly phosphorylates synaptojanin1 in vitro, resulting in the disruption of endophilin-synaptojanin1 interaction required for SV endocytosis. |
| T11 | 1478-1814 | DRI_Challenge | denotes | Our work suggests a merge of LRRK2 and SYNJ1 pathogenic pathways in deregulating SV trafficking in MB neurons as an underlying molecular mechanism of early PD pathogenesis.SIGNIFICANCE STATEMENT Understanding midbrain dopaminergic (DAergic) neuron-selective vulnerability in PD is essential for the development of targeted therapeutics. |
| T12 | 1815-2002 | DRI_Outcome | denotes | We report, for the first time, a nerve terminal impairment in SV trafficking selectively in MB neurons but not cortical neurons caused by two PARK genes: LRRK2 (PARK8) and SYNJ1 (PARK20). |
| T13 | 2003-2140 | DRI_Outcome | denotes | We demonstrate that the enhanced kinase activity resulting from the most frequent G2019S mutation in LRRK2 is the key to this impairment. |
| T14 | 2141-2176 | DRI_Outcome | denotes | We provide evidence suggesting that |
| T15 | 2190-2388 | DRI_Outcome | denotes | and SYNJ1 loss of function share a similar pathogenic pathway in deregulating DAergic neuron SV endocytosis and that they play additive roles in facilitating each other's pathogenic functions in PD. |
kaiyin_test
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 0-19 | Disease | denotes | Parkinson's Disease |
| T2 | 31-36 | Gene | denotes | LRRK2 |
| T3 | 56-62 | Var | denotes | Mutant |
| T4 | 63-71 | NegReg | denotes | Disrupts |
| T5 | 72-128 | MPA | denotes | Synaptic Vesicle Trafficking in Ventral Midbrain Neurons |
| T6 | 434-439 | Gene | denotes | LRRK2 |
| T7 | 440-447 | Var | denotes | mutants |
| T9 | 448-458 | Reg | denotes | contribute |
| T8 | 462-482 | MPA | denotes | nigral vulnerability |
| T11 | 537-545 | Var | denotes | mutation |
| T12 | 546-551 | Gene | denotes | LRRK2 |
| T10 | 559-566 | NegReg | denotes | impairs |
| T13 | 567-636 | MPA | denotes | SV endocytosis in ventral midbrain (MB) neurons, including DA neurons |
| T15 | 975-985 | NegReg | denotes | impairment |
| T16 | 989-1014 | MPA | denotes | SV endocytosis in neurons |
| T17 | 1037-1045 | Var | denotes | deletion |
| T14 | 1049-1054 | Gene | denotes | SYNJ1 |
| T18 | 1130-1138 | Var | denotes | SYNJ1+/- |
| T19 | 1143-1155 | Var | denotes | LRRK2 G2019S |
| T20 | 1195-1202 | NegReg | denotes | impairs |
| T21 | 1203-1237 | MPA | denotes | sustained exocytosis in MB neurons |
| T22 | 1242-1248 | Reg | denotes | alters |
| T23 | 1249-1273 | MPA | denotes | specific motor functions |
| T24 | 1327-1332 | Var | denotes | LRRK2 |
| T25 | 1381-1393 | Reg | denotes | resulting in |
| T26 | 1398-1476 | MPA | denotes | disruption of endophilin-synaptojanin1 interaction required for SV endocytosis |
| T31 | 2027-2035 | PosReg | denotes | enhanced |
| T32 | 2036-2051 | MPA | denotes | kinase activity |
| T28 | 2085-2091 | Var | denotes | G2019S |
| T29 | 2104-2109 | Gene | denotes | LRRK2 |
| T39 | 2177-2182 | Gene | denotes | LRRK2 |
| T33 | 2183-2189 | Var | denotes | G2019S |
| T34 | 2194-2199 | Gene | denotes | SYNJ1 |
| T35 | 2200-2216 | NegReg | denotes | loss of function |
| T36 | 2255-2297 | MPA | denotes | deregulating DAergic neuron SV endocytosis |
| T37 | 2312-2331 | Reg | denotes | play additive roles |
| T38 | 2385-2387 | Disease | denotes | PD |
| R1 | T2 | T3 | ThemeOf | LRRK2,Mutant |
| R10 | T13 | T10 | ThemeOf | "SV endocytosis in ventral midbrain (MB) neurons, including DA neurons",impairs |
| R11 | T14 | T17 | ThemeOf | SYNJ1,deletion |
| R12 | T17 | T15 | CauseOf | deletion,impairment |
| R13 | T16 | T15 | ThemeOf | SV endocytosis in neurons,impairment |
| R14 | T18 | T20 | CauseOf | SYNJ1+/-,impairs |
| R15 | T21 | T20 | ThemeOf | sustained exocytosis in MB neurons,impairs |
| R16 | T19 | T20 | CauseOf | LRRK2 G2019S,impairs |
| R17 | T18 | T22 | CauseOf | SYNJ1+/-,alters |
| R18 | T19 | T22 | CauseOf | LRRK2 G2019S,alters |
| R19 | T23 | T22 | ThemeOf | specific motor functions,alters |
| R2 | T3 | T4 | CauseOf | Mutant,Disrupts |
| R20 | T28 | T31 | CauseOf | G2019S,enhanced |
| R21 | T32 | T31 | ThemeOf | kinase activity,enhanced |
| R22 | T29 | T28 | ThemeOf | LRRK2,G2019S |
| R23 | T33 | T35 | CauseOf | G2019S,loss of function |
| R24 | T34 | T35 | CauseOf | SYNJ1,loss of function |
| R25 | T36 | T35 | ThemeOf | deregulating DAergic neuron SV endocytosis,loss of function |
| R26 | T34 | T37 | CauseOf | SYNJ1,play additive roles |
| R27 | T33 | T37 | CauseOf | G2019S,play additive roles |
| R28 | T38 | T37 | ThemeOf | PD,play additive roles |
| R29 | T24 | T25 | CauseOf | LRRK2,resulting in |
| R3 | T5 | T4 | ThemeOf | Synaptic Vesicle Trafficking in Ventral Midbrain Neurons,Disrupts |
| R30 | T26 | T25 | ThemeOf | disruption of endophilin-synaptojanin1 interaction required for SV endocytosis,resulting in |
| R31 | T39 | T33 | ThemeOf | LRRK2,G2019S |
| R4 | T3 | T1 | CauseOf | Mutant,Parkinson's Disease |
| R5 | T6 | T7 | ThemeOf | LRRK2,mutants |
| R6 | T7 | T9 | CauseOf | mutants,contribute |
| R7 | T8 | T9 | ThemeOf | nigral vulnerability,contribute |
| R8 | T12 | T11 | ThemeOf | LRRK2,mutation |
| R9 | T11 | T10 | CauseOf | mutation,impairs |
name_no
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 0-19 | Disease | denotes | Parkinson's Disease |
| T2 | 31-36 | Gene | denotes | LRRK2 |
| T3 | 56-62 | Var | denotes | Mutant |
| T4 | 63-71 | NegReg | denotes | Disrupts |
| T5 | 72-128 | MPA | denotes | Synaptic Vesicle Trafficking in Ventral Midbrain Neurons |
| T6 | 434-439 | Gene | denotes | LRRK2 |
| T7 | 440-447 | Var | denotes | mutants |
| T9 | 448-458 | Reg | denotes | contribute |
| T8 | 462-482 | MPA | denotes | nigral vulnerability |
| T11 | 537-545 | Var | denotes | mutation |
| T12 | 546-551 | Gene | denotes | LRRK2 |
| T10 | 559-566 | NegReg | denotes | impairs |
| T13 | 567-636 | MPA | denotes | SV endocytosis in ventral midbrain (MB) neurons, including DA neurons |
| T15 | 975-985 | NegReg | denotes | impairment |
| T16 | 989-1014 | MPA | denotes | SV endocytosis in neurons |
| T17 | 1037-1045 | Var | denotes | deletion |
| T14 | 1049-1054 | Gene | denotes | SYNJ1 |
| T18 | 1130-1138 | Var | denotes | SYNJ1+/- |
| T19 | 1143-1155 | Var | denotes | LRRK2 G2019S |
| T20 | 1195-1202 | NegReg | denotes | impairs |
| T21 | 1203-1237 | MPA | denotes | sustained exocytosis in MB neurons |
| T22 | 1242-1248 | Reg | denotes | alters |
| T23 | 1249-1273 | MPA | denotes | specific motor functions |
| T24 | 1327-1332 | Var | denotes | LRRK2 |
| T25 | 1381-1393 | Reg | denotes | resulting in |
| T26 | 1398-1476 | MPA | denotes | disruption of endophilin-synaptojanin1 interaction required for SV endocytosis |
| T31 | 2027-2035 | PosReg | denotes | enhanced |
| T32 | 2036-2051 | MPA | denotes | kinase activity |
| T28 | 2085-2091 | Var | denotes | G2019S |
| T29 | 2104-2109 | Gene | denotes | LRRK2 |
| T39 | 2177-2182 | Gene | denotes | LRRK2 |
| T33 | 2183-2189 | Var | denotes | G2019S |
| T34 | 2194-2199 | Gene | denotes | SYNJ1 |
| T35 | 2200-2216 | NegReg | denotes | loss of function |
| T36 | 2255-2297 | MPA | denotes | deregulating DAergic neuron SV endocytosis |
| T37 | 2312-2331 | Reg | denotes | play additive roles |
| T38 | 2385-2387 | Disease | denotes | PD |
| R1 | T2 | T3 | ThemeOf | LRRK2,Mutant |
| R10 | T13 | T10 | ThemeOf | "SV endocytosis in ventral midbrain (MB) neurons, including DA neurons",impairs |
| R11 | T14 | T17 | ThemeOf | SYNJ1,deletion |
| R12 | T17 | T15 | CauseOf | deletion,impairment |
| R13 | T16 | T15 | ThemeOf | SV endocytosis in neurons,impairment |
| R14 | T18 | T20 | CauseOf | SYNJ1+/-,impairs |
| R15 | T21 | T20 | ThemeOf | sustained exocytosis in MB neurons,impairs |
| R16 | T19 | T20 | CauseOf | LRRK2 G2019S,impairs |
| R17 | T18 | T22 | CauseOf | SYNJ1+/-,alters |
| R18 | T19 | T22 | CauseOf | LRRK2 G2019S,alters |
| R19 | T23 | T22 | ThemeOf | specific motor functions,alters |
| R2 | T3 | T4 | CauseOf | Mutant,Disrupts |
| R20 | T28 | T31 | CauseOf | G2019S,enhanced |
| R21 | T32 | T31 | ThemeOf | kinase activity,enhanced |
| R22 | T29 | T28 | ThemeOf | LRRK2,G2019S |
| R23 | T33 | T35 | CauseOf | G2019S,loss of function |
| R24 | T34 | T35 | CauseOf | SYNJ1,loss of function |
| R25 | T36 | T35 | ThemeOf | deregulating DAergic neuron SV endocytosis,loss of function |
| R26 | T34 | T37 | CauseOf | SYNJ1,play additive roles |
| R27 | T33 | T37 | CauseOf | G2019S,play additive roles |
| R28 | T38 | T37 | ThemeOf | PD,play additive roles |
| R29 | T24 | T25 | CauseOf | LRRK2,resulting in |
| R3 | T5 | T4 | ThemeOf | Synaptic Vesicle Trafficking in Ventral Midbrain Neurons,Disrupts |
| R30 | T26 | T25 | ThemeOf | disruption of endophilin-synaptojanin1 interaction required for SV endocytosis,resulting in |
| R31 | T39 | T33 | ThemeOf | LRRK2,G2019S |
| R4 | T3 | T1 | CauseOf | Mutant,Parkinson's Disease |
| R5 | T6 | T7 | ThemeOf | LRRK2,mutants |
| R6 | T7 | T9 | CauseOf | mutants,contribute |
| R7 | T8 | T9 | ThemeOf | nigral vulnerability,contribute |
| R8 | T12 | T11 | ThemeOf | LRRK2,mutation |
| R9 | T11 | T10 | CauseOf | mutation,impairs |