PubMed:2852474
Annnotations
sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TextSentencer_T1 | 0-115 | Sentence | denotes | Complex glycerol kinase deficiency: molecular-genetic, cytogenetic, and clinical studies of five Japanese patients. |
| TextSentencer_T2 | 116-279 | Sentence | denotes | Five male Japanese patients with complex glycerol kinase deficiency (CGKD) and their relatives were studied clinically, cytogenetically, and molecular-genetically. |
| TextSentencer_T3 | 280-418 | Sentence | denotes | All patients had muscular dystrophy or muscle weakness, mental retardation, congenital adrenal hypoplasia, and glycerol kinase deficiency. |
| TextSentencer_T4 | 419-554 | Sentence | denotes | High-resolution GTG-banded chromosomes showed a microdeletion in the Xp21 region in all four patients examined and in all five mothers. |
| TextSentencer_T5 | 555-872 | Sentence | denotes | Southern hybridizations, after digestions by restriction endonucleases, with various cloned DNAs (D2, 99-6, B24, C7, L1-4, cDMD13-14, J66-HI, P20, J-Bir, ERT87-30, ERT87-15, ERT87-8, ERT87-1, XJ-1.1, 754, cx5.7, and OTC-1) that are located around Xp21 also showed a deletion in the genome of all patients and mothers. |
| TextSentencer_T6 | 873-1032 | Sentence | denotes | Although the deletion differed in size among patients, a segment commonly absent was located between the genomic sequences corresponding to L1-4 and cDMD13-14. |
| TextSentencer_T7 | 1033-1133 | Sentence | denotes | This finding indicated that the gene coding for glycerol kinase (GK) is located within this segment. |
| TextSentencer_T8 | 1134-1376 | Sentence | denotes | A comparison of the clinical manifestations of the present five patients and reported CGKD or Duchenne muscular dystrophy (DMD) patients with DNA deletion suggests the existence of a certain gene responsible for gonadotropin deficiency (GTD). |
| TextSentencer_T9 | 1377-1667 | Sentence | denotes | The result of the present study and results of previous studies suggest that genes for ornithine transcarbamylase (OTC), DMD, and GK and putative genes responsible for congenital adrenal hypoplasia (AHC) and GTD are arranged from telomere to centromere as pter--GTD--AHC--GK--DMD--OTC--cen. |
| T1 | 0-115 | Sentence | denotes | Complex glycerol kinase deficiency: molecular-genetic, cytogenetic, and clinical studies of five Japanese patients. |
| T2 | 116-279 | Sentence | denotes | Five male Japanese patients with complex glycerol kinase deficiency (CGKD) and their relatives were studied clinically, cytogenetically, and molecular-genetically. |
| T3 | 280-418 | Sentence | denotes | All patients had muscular dystrophy or muscle weakness, mental retardation, congenital adrenal hypoplasia, and glycerol kinase deficiency. |
| T4 | 419-554 | Sentence | denotes | High-resolution GTG-banded chromosomes showed a microdeletion in the Xp21 region in all four patients examined and in all five mothers. |
| T5 | 555-872 | Sentence | denotes | Southern hybridizations, after digestions by restriction endonucleases, with various cloned DNAs (D2, 99-6, B24, C7, L1-4, cDMD13-14, J66-HI, P20, J-Bir, ERT87-30, ERT87-15, ERT87-8, ERT87-1, XJ-1.1, 754, cx5.7, and OTC-1) that are located around Xp21 also showed a deletion in the genome of all patients and mothers. |
| T6 | 873-1032 | Sentence | denotes | Although the deletion differed in size among patients, a segment commonly absent was located between the genomic sequences corresponding to L1-4 and cDMD13-14. |
| T7 | 1033-1133 | Sentence | denotes | This finding indicated that the gene coding for glycerol kinase (GK) is located within this segment. |
| T8 | 1134-1376 | Sentence | denotes | A comparison of the clinical manifestations of the present five patients and reported CGKD or Duchenne muscular dystrophy (DMD) patients with DNA deletion suggests the existence of a certain gene responsible for gonadotropin deficiency (GTD). |
| T9 | 1377-1667 | Sentence | denotes | The result of the present study and results of previous studies suggest that genes for ornithine transcarbamylase (OTC), DMD, and GK and putative genes responsible for congenital adrenal hypoplasia (AHC) and GTD are arranged from telomere to centromere as pter--GTD--AHC--GK--DMD--OTC--cen. |
DisGeNET
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T0 | 1464-1490 | gene:5009 | denotes | ornithine transcarbamylase |
| T1 | 1545-1574 | disease:C0220766 | denotes | congenital adrenal hypoplasia |
| T2 | 1464-1490 | gene:5009 | denotes | ornithine transcarbamylase |
| T3 | 1585-1588 | disease:C0271623 | denotes | GTD |
| T4 | 1492-1495 | gene:5009 | denotes | OTC |
| T5 | 1545-1574 | disease:C0220766 | denotes | congenital adrenal hypoplasia |
| T6 | 1492-1495 | gene:5009 | denotes | OTC |
| T7 | 1585-1588 | disease:C0271623 | denotes | GTD |
| T8 | 1492-1495 | gene:5009 | denotes | OTC |
| T9 | 1639-1642 | disease:C0271623 | denotes | GTD |
| T10 | 1492-1495 | gene:5009 | denotes | OTC |
| T11 | 1644-1647 | disease:C0220766 | denotes | AHC |
| T12 | 1492-1495 | gene:5009 | denotes | OTC |
| T13 | 1653-1656 | disease:C0026850 | denotes | DMD |
| T14 | 1507-1509 | gene:2710 | denotes | GK |
| T15 | 1545-1574 | disease:C0220766 | denotes | congenital adrenal hypoplasia |
| T16 | 1507-1509 | gene:2710 | denotes | GK |
| T17 | 1576-1579 | disease:C0220766 | denotes | AHC |
| T18 | 1507-1509 | gene:2710 | denotes | GK |
| T19 | 1585-1588 | disease:C0271623 | denotes | GTD |
| T20 | 1507-1509 | gene:2710 | denotes | GK |
| T21 | 1639-1642 | disease:C0271623 | denotes | GTD |
| T22 | 1507-1509 | gene:2710 | denotes | GK |
| T23 | 1644-1647 | disease:C0220766 | denotes | AHC |
| T24 | 1507-1509 | gene:2710 | denotes | GK |
| T25 | 1653-1656 | disease:C0026850 | denotes | DMD |
| T26 | 1649-1651 | gene:2710 | denotes | GK |
| T27 | 1545-1574 | disease:C0220766 | denotes | congenital adrenal hypoplasia |
| T28 | 1649-1651 | gene:2710 | denotes | GK |
| T29 | 1576-1579 | disease:C0220766 | denotes | AHC |
| T30 | 1649-1651 | gene:2710 | denotes | GK |
| T31 | 1585-1588 | disease:C0271623 | denotes | GTD |
| T32 | 1658-1661 | gene:5009 | denotes | OTC |
| T33 | 1545-1574 | disease:C0220766 | denotes | congenital adrenal hypoplasia |
| T34 | 1658-1661 | gene:5009 | denotes | OTC |
| T35 | 1576-1579 | disease:C0220766 | denotes | AHC |
| T36 | 1658-1661 | gene:5009 | denotes | OTC |
| T37 | 1585-1588 | disease:C0271623 | denotes | GTD |
| R1 | T0 | T1 | associated_with | ornithine transcarbamylase,congenital adrenal hypoplasia |
| R2 | T2 | T3 | associated_with | ornithine transcarbamylase,GTD |
| R3 | T4 | T5 | associated_with | OTC,congenital adrenal hypoplasia |
| R4 | T6 | T7 | associated_with | OTC,GTD |
| R5 | T8 | T9 | associated_with | OTC,GTD |
| R6 | T10 | T11 | associated_with | OTC,AHC |
| R7 | T12 | T13 | associated_with | OTC,DMD |
| R8 | T14 | T15 | associated_with | GK,congenital adrenal hypoplasia |
| R9 | T16 | T17 | associated_with | GK,AHC |
| R10 | T18 | T19 | associated_with | GK,GTD |
| R11 | T20 | T21 | associated_with | GK,GTD |
| R12 | T22 | T23 | associated_with | GK,AHC |
| R13 | T24 | T25 | associated_with | GK,DMD |
| R14 | T26 | T27 | associated_with | GK,congenital adrenal hypoplasia |
| R15 | T28 | T29 | associated_with | GK,AHC |
| R16 | T30 | T31 | associated_with | GK,GTD |
| R17 | T32 | T33 | associated_with | OTC,congenital adrenal hypoplasia |
| R18 | T34 | T35 | associated_with | OTC,AHC |
| R19 | T36 | T37 | associated_with | OTC,GTD |
PubmedHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 297-315 | HP_0003560 | denotes | muscular dystrophy |
| T2 | 319-334 | HP_0001324 | denotes | muscle weakness |
| T3 | 336-354 | HP_0001249 | denotes | mental retardation |
| T4 | 356-385 | HP_0008244 | denotes | congenital adrenal hypoplasia |
| T5 | 367-385 | HP_0000835 | denotes | adrenal hypoplasia |
| T6 | 1237-1255 | HP_0003560 | denotes | muscular dystrophy |
| T7 | 1346-1369 | HP_0008213 | denotes | gonadotropin deficiency |
| T8 | 1545-1574 | HP_0008244 | denotes | congenital adrenal hypoplasia |
| T9 | 1556-1574 | HP_0000835 | denotes | adrenal hypoplasia |
PubCasesORDO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| AB1 | 1228-1255 | ORDO:98896 | denotes | Duchenne muscular dystrophy |
| AB2 | 1257-1260 | ORDO:98896 | denotes | DMD |
| AB3 | 1498-1501 | ORDO:98896 | denotes | DMD |
| AB4 | 1653-1656 | ORDO:98896 | denotes | DMD |
PubCasesHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| AB1 | 297-315 | HP:0003560 | denotes | muscular dystrophy |
| AB2 | 319-334 | HP:0001324 | denotes | muscle weakness |
| AB3 | 356-385 | HP:0008244 | denotes | congenital adrenal hypoplasia |
| AB4 | 1237-1255 | HP:0003560 | denotes | muscular dystrophy |
| AB5 | 1346-1369 | HP:0008213 | denotes | gonadotropin deficiency |
| AB6 | 1545-1574 | HP:0008244 | denotes | congenital adrenal hypoplasia |
NCBIDiseaseCorpus
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 0-34 | SpecificDisease:C538138 | denotes | Complex glycerol kinase deficiency |
| T2 | 149-183 | SpecificDisease:C538138 | denotes | complex glycerol kinase deficiency |
| T3 | 185-189 | SpecificDisease:C538138 | denotes | CGKD |
| T4 | 297-315 | DiseaseClass:D009136 | denotes | muscular dystrophy |
| T5 | 319-334 | DiseaseClass:D018908 | denotes | muscle weakness |
| T6 | 336-354 | DiseaseClass:D008607 | denotes | mental retardation |
| T7 | 356-385 | SpecificDisease:D000312 | denotes | congenital adrenal hypoplasia |
| T8 | 391-417 | DiseaseClass:C538138 | denotes | glycerol kinase deficiency |
| T9 | 1220-1224 | Modifier:C538138 | denotes | CGKD |
| T10 | 1228-1255 | Modifier:D020388 | denotes | Duchenne muscular dystrophy |
| T11 | 1257-1260 | Modifier:D020388 | denotes | DMD |
| T12 | 1346-1369 | SpecificDisease:C535764 | denotes | gonadotropin deficiency |
| T13 | 1371-1374 | SpecificDisease:C535764 | denotes | GTD |
| T14 | 1498-1501 | SpecificDisease:D020388 | denotes | DMD |
| T15 | 1545-1574 | SpecificDisease:D000312 | denotes | congenital adrenal hypoplasia |
| T16 | 1576-1579 | SpecificDisease:D000312 | denotes | AHC |
| T17 | 1585-1588 | SpecificDisease:C535764 | denotes | GTD |
NCBI-Disease-Train
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T4412 | 0-34 | SpecificDisease | denotes | Complex glycerol kinase deficiency | C538138 |
| T4413 | 149-183 | SpecificDisease | denotes | complex glycerol kinase deficiency | C538138 |
| T4414 | 185-189 | SpecificDisease | denotes | CGKD | C538138 |
| T4415 | 297-315 | DiseaseClass | denotes | muscular dystrophy | D009136 |
| T4416 | 319-334 | DiseaseClass | denotes | muscle weakness | D018908 |
| T4417 | 336-354 | DiseaseClass | denotes | mental retardation | D008607 |
| T4418 | 356-385 | SpecificDisease | denotes | congenital adrenal hypoplasia | D000312 |
| T4419 | 391-417 | DiseaseClass | denotes | glycerol kinase deficiency | C538138 |
| T4420 | 1220-1224 | Modifier | denotes | CGKD | C538138 |
| T4421 | 1228-1255 | Modifier | denotes | Duchenne muscular dystrophy | D020388 |
| T4422 | 1257-1260 | Modifier | denotes | DMD | D020388 |
| T4423 | 1346-1369 | SpecificDisease | denotes | gonadotropin deficiency | C535764 |
| T4424 | 1371-1374 | SpecificDisease | denotes | GTD | C535764 |
| T4425 | 1498-1501 | SpecificDisease | denotes | DMD | D020388 |
| T4426 | 1545-1574 | SpecificDisease | denotes | congenital adrenal hypoplasia | D000312 |
| T4427 | 1576-1579 | SpecificDisease | denotes | AHC | D000312 |
| T4428 | 1585-1588 | SpecificDisease | denotes | GTD | C535764 |
NCBI-Disease-Corpus-All
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T4412 | 0-34 | SpecificDisease | denotes | Complex glycerol kinase deficiency | C538138 |
| T4413 | 149-183 | SpecificDisease | denotes | complex glycerol kinase deficiency | C538138 |
| T4414 | 185-189 | SpecificDisease | denotes | CGKD | C538138 |
| T4415 | 297-315 | DiseaseClass | denotes | muscular dystrophy | D009136 |
| T4416 | 319-334 | DiseaseClass | denotes | muscle weakness | D018908 |
| T4417 | 336-354 | DiseaseClass | denotes | mental retardation | D008607 |
| T4418 | 356-385 | SpecificDisease | denotes | congenital adrenal hypoplasia | D000312 |
| T4419 | 391-417 | DiseaseClass | denotes | glycerol kinase deficiency | C538138 |
| T4420 | 1220-1224 | Modifier | denotes | CGKD | C538138 |
| T4421 | 1228-1255 | Modifier | denotes | Duchenne muscular dystrophy | D020388 |
| T4422 | 1257-1260 | Modifier | denotes | DMD | D020388 |
| T4423 | 1346-1369 | SpecificDisease | denotes | gonadotropin deficiency | C535764 |
| T4424 | 1371-1374 | SpecificDisease | denotes | GTD | C535764 |
| T4425 | 1498-1501 | SpecificDisease | denotes | DMD | D020388 |
| T4426 | 1545-1574 | SpecificDisease | denotes | congenital adrenal hypoplasia | D000312 |
| T4427 | 1576-1579 | SpecificDisease | denotes | AHC | D000312 |
| T4428 | 1585-1588 | SpecificDisease | denotes | GTD | C535764 |
NCBI-Disease-Corpus-2stage-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 8-34 | CompositeMention | denotes | glycerol kinase deficiency |
| T2 | 157-183 | CompositeMention | denotes | glycerol kinase deficiency |
| T3 | 185-189 | SpecificDisease | denotes | CGKD |
| T4 | 297-315 | CompositeMention | denotes | muscular dystrophy |
| T5 | 336-354 | SpecificDisease | denotes | mental retardation |
| T6 | 356-385 | SpecificDisease | denotes | congenital adrenal hypoplasia |
| T7 | 391-417 | SpecificDisease | denotes | glycerol kinase deficiency |
| T8 | 1081-1096 | Modifier | denotes | glycerol kinase |
| T9 | 1098-1100 | Modifier | denotes | GK |
| T10 | 1220-1224 | SpecificDisease | denotes | CGKD |
| T11 | 1228-1255 | CompositeMention | denotes | Duchenne muscular dystrophy |
| T12 | 1257-1260 | SpecificDisease | denotes | DMD |
| T13 | 1346-1369 | SpecificDisease | denotes | gonadotropin deficiency |
| T14 | 1371-1374 | SpecificDisease | denotes | GTD |
| T15 | 1464-1490 | Modifier | denotes | ornithine transcarbamylase |
| T16 | 1492-1495 | Modifier | denotes | OTC |
| T17 | 1498-1501 | SpecificDisease | denotes | DMD |
| T18 | 1507-1509 | Modifier | denotes | GK |
| T19 | 1545-1574 | SpecificDisease | denotes | congenital adrenal hypoplasia |
| T20 | 1576-1579 | SpecificDisease | denotes | AHC |
| T21 | 1585-1588 | SpecificDisease | denotes | GTD |
| T22 | 1639-1642 | SpecificDisease | denotes | GTD |
| T23 | 1644-1647 | SpecificDisease | denotes | AHC |
| T24 | 1649-1651 | Modifier | denotes | GK |
| T25 | 1653-1656 | SpecificDisease | denotes | DMD |
| T26 | 1658-1661 | Modifier | denotes | OTC |
NCBI-Disease-Corpus-rezarta-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 8-34 | DiseaseClass | denotes | glycerol kinase deficiency |
| T2 | 157-183 | DiseaseClass | denotes | glycerol kinase deficiency |
| T3 | 297-315 | SpecificDisease | denotes | muscular dystrophy |
| T4 | 356-385 | SpecificDisease | denotes | congenital adrenal hypoplasia |
| T5 | 391-417 | SpecificDisease | denotes | glycerol kinase deficiency |
| T6 | 1081-1096 | Modifier | denotes | glycerol kinase |
| T7 | 1228-1255 | SpecificDisease | denotes | Duchenne muscular dystrophy |
| T8 | 1257-1260 | SpecificDisease | denotes | DMD |
| T9 | 1346-1369 | DiseaseClass | denotes | gonadotropin deficiency |
| T10 | 1464-1490 | SpecificDisease | denotes | ornithine transcarbamylase |
| T11 | 1498-1501 | SpecificDisease | denotes | DMD |
| T12 | 1507-1509 | SpecificDisease | denotes | GK |
| T13 | 1545-1574 | SpecificDisease | denotes | congenital adrenal hypoplasia |
| T14 | 1576-1579 | SpecificDisease | denotes | AHC |
| T15 | 1585-1588 | DiseaseClass | denotes | GTD |
| T16 | 1639-1642 | DiseaseClass | denotes | GTD |
| T17 | 1644-1647 | SpecificDisease | denotes | AHC |
| T18 | 1649-1651 | SpecificDisease | denotes | GK |
| T19 | 1653-1656 | SpecificDisease | denotes | DMD |
| T20 | 1658-1661 | SpecificDisease | denotes | OTC |
NCBI-Disease-Corpus-4oGuideline-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 8-34 | SpecificDisease | denotes | glycerol kinase deficiency |
| T2 | 157-183 | SpecificDisease | denotes | glycerol kinase deficiency |
| T3 | 297-315 | DiseaseClass | denotes | muscular dystrophy |
| T4 | 319-334 | DiseaseClass | denotes | muscle weakness |
| T5 | 336-354 | DiseaseClass | denotes | mental retardation |
| T6 | 356-385 | SpecificDisease | denotes | congenital adrenal hypoplasia |
| T7 | 391-417 | SpecificDisease | denotes | glycerol kinase deficiency |
| T8 | 1081-1096 | SpecificDisease | denotes | glycerol kinase |
| T9 | 1228-1255 | SpecificDisease | denotes | Duchenne muscular dystrophy |
| T10 | 1346-1369 | DiseaseClass | denotes | gonadotropin deficiency |
| T11 | 1464-1490 | SpecificDisease | denotes | ornithine transcarbamylase |
| T12 | 1545-1574 | SpecificDisease | denotes | congenital adrenal hypoplasia |
NCBI-Disease-Corpus-Simple-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 24-34 | SpecificDisease | denotes | deficiency |
| T2 | 173-183 | SpecificDisease | denotes | deficiency |
| T3 | 185-189 | SpecificDisease | denotes | CGKD |
| T4 | 297-315 | DiseaseClass | denotes | muscular dystrophy |
| T5 | 319-334 | CompositeMention | denotes | muscle weakness |
| T6 | 336-354 | CompositeMention | denotes | mental retardation |
| T7 | 356-385 | SpecificDisease | denotes | congenital adrenal hypoplasia |
| T8 | 391-417 | SpecificDisease | denotes | glycerol kinase deficiency |
| T9 | 1220-1224 | SpecificDisease | denotes | CGKD |
| T10 | 1228-1255 | SpecificDisease | denotes | Duchenne muscular dystrophy |
| T11 | 1257-1260 | SpecificDisease | denotes | DMD |
| T12 | 1346-1369 | SpecificDisease | denotes | gonadotropin deficiency |
| T13 | 1371-1374 | SpecificDisease | denotes | GTD |
| T14 | 1492-1495 | SpecificDisease | denotes | OTC |
| T15 | 1498-1501 | SpecificDisease | denotes | DMD |
| T16 | 1507-1509 | SpecificDisease | denotes | GK |
| T17 | 1545-1574 | SpecificDisease | denotes | congenital adrenal hypoplasia |
| T18 | 1576-1579 | SpecificDisease | denotes | AHC |
| T19 | 1585-1588 | SpecificDisease | denotes | GTD |
| T20 | 1639-1642 | SpecificDisease | denotes | GTD |
| T21 | 1644-1647 | SpecificDisease | denotes | AHC |
| T22 | 1649-1651 | SpecificDisease | denotes | GK |
| T23 | 1653-1656 | SpecificDisease | denotes | DMD |
| T24 | 1658-1661 | SpecificDisease | denotes | OTC |