PubMed:23824322
Annnotations
sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TextSentencer_T1 | 0-93 | Sentence | denotes | Six cases with severe insulin resistance (SIR) associated with mutations of insulin receptor: |
| TextSentencer_T2 | 94-149 | Sentence | denotes | Is a Bartter-like syndrome a feature of congenital SIR? |
| TextSentencer_T3 | 150-329 | Sentence | denotes | Biallelic insulin receptor (INSR) gene mutations cause congenital syndromes of severe insulin resistance (SIR) known as Donohue syndrome (DS) and Rabson-Mendenhall syndrome (RMS). |
| TextSentencer_T4 | 330-548 | Sentence | denotes | At presentation, DS and RMS are difficult to differentiate since they share many clinical features; however, while patients with DS usually die within 1 year of birth, individuals classified as RMS can reach adult age. |
| TextSentencer_T5 | 549-680 | Sentence | denotes | INSR mutations can be also found in pubertal females with hyperinsulinism, hyperandrogenism, and acanthosis nigricans (type A SIR). |
| TextSentencer_T6 | 681-776 | Sentence | denotes | We studied the INSR gene in five subjects with congenital SIR and in a patient with type A SIR. |
| TextSentencer_T7 | 777-1017 | Sentence | denotes | Nine biallelic INSR gene mutations (eight novels, including an in-frame deletion of INSR signal peptide) were identified in patients with congenital SIR; a heterozygous, spontaneous INSR mutation was detected in the patient with type A SIR. |
| TextSentencer_T8 | 1018-1212 | Sentence | denotes | Two probands, presenting severe hirsutism at birth, died at the age of 3 months and were classified as DS, while other 2, currently 2 and 3 years old, were diagnosed with RMS (patients 3 and 4). |
| TextSentencer_T9 | 1213-1275 | Sentence | denotes | The fifth patient with congenital SIR died when 14 months old. |
| TextSentencer_T10 | 1276-1454 | Sentence | denotes | Nephrocalcinosis, hyperaldosteronism, hyperreninemia, and hypokalemia, in the absence of hypertension, were discovered in patients 3 and 5 when 24 and 4 months old, respectively. |
| TextSentencer_T11 | 1455-1574 | Sentence | denotes | Patient 3, now 3 years/3 months old, still shows hyperreninemic hyperaldosteronism requiring potassium supplementation. |
| TextSentencer_T12 | 1575-1751 | Sentence | denotes | We conclude that renal abnormalities resembling antenatal Bartter's syndrome type II, recently reported also by others, is a common observation in patients with congenital SIR. |
| T1 | 0-93 | Sentence | denotes | Six cases with severe insulin resistance (SIR) associated with mutations of insulin receptor: |
| T2 | 94-149 | Sentence | denotes | Is a Bartter-like syndrome a feature of congenital SIR? |
| T3 | 150-329 | Sentence | denotes | Biallelic insulin receptor (INSR) gene mutations cause congenital syndromes of severe insulin resistance (SIR) known as Donohue syndrome (DS) and Rabson-Mendenhall syndrome (RMS). |
| T4 | 330-548 | Sentence | denotes | At presentation, DS and RMS are difficult to differentiate since they share many clinical features; however, while patients with DS usually die within 1 year of birth, individuals classified as RMS can reach adult age. |
| T5 | 549-680 | Sentence | denotes | INSR mutations can be also found in pubertal females with hyperinsulinism, hyperandrogenism, and acanthosis nigricans (type A SIR). |
| T6 | 681-776 | Sentence | denotes | We studied the INSR gene in five subjects with congenital SIR and in a patient with type A SIR. |
| T7 | 777-1017 | Sentence | denotes | Nine biallelic INSR gene mutations (eight novels, including an in-frame deletion of INSR signal peptide) were identified in patients with congenital SIR; a heterozygous, spontaneous INSR mutation was detected in the patient with type A SIR. |
| T8 | 1018-1212 | Sentence | denotes | Two probands, presenting severe hirsutism at birth, died at the age of 3 months and were classified as DS, while other 2, currently 2 and 3 years old, were diagnosed with RMS (patients 3 and 4). |
| T9 | 1213-1275 | Sentence | denotes | The fifth patient with congenital SIR died when 14 months old. |
| T10 | 1276-1454 | Sentence | denotes | Nephrocalcinosis, hyperaldosteronism, hyperreninemia, and hypokalemia, in the absence of hypertension, were discovered in patients 3 and 5 when 24 and 4 months old, respectively. |
| T11 | 1455-1574 | Sentence | denotes | Patient 3, now 3 years/3 months old, still shows hyperreninemic hyperaldosteronism requiring potassium supplementation. |
| T12 | 1575-1751 | Sentence | denotes | We conclude that renal abnormalities resembling antenatal Bartter's syndrome type II, recently reported also by others, is a common observation in patients with congenital SIR. |
DisGeNET
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T0 | 549-553 | gene:3643 | denotes | INSR |
| T1 | 607-622 | disease:C0020459 | denotes | hyperinsulinism |
| T2 | 549-553 | gene:3643 | denotes | INSR |
| T3 | 646-666 | disease:C0000889 | denotes | acanthosis nigricans |
| R1 | T0 | T1 | associated_with | INSR,hyperinsulinism |
| R2 | T2 | T3 | associated_with | INSR,acanthosis nigricans |
Allie
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| SS1_23824322_0_0 | 15-40 | expanded | denotes | severe insulin resistance |
| SS2_23824322_0_0 | 42-45 | abbr | denotes | SIR |
| SS1_23824322_1_0 | 160-176 | expanded | denotes | insulin receptor |
| SS2_23824322_1_0 | 178-182 | abbr | denotes | INSR |
| SS1_23824322_1_1 | 229-254 | expanded | denotes | severe insulin resistance |
| SS2_23824322_1_1 | 256-259 | abbr | denotes | SIR |
| SS1_23824322_1_2 | 270-286 | expanded | denotes | Donohue syndrome |
| SS2_23824322_1_2 | 288-290 | abbr | denotes | DS |
| SS1_23824322_1_3 | 296-322 | expanded | denotes | Rabson-Mendenhall syndrome |
| SS2_23824322_1_3 | 324-327 | abbr | denotes | RMS |
| AE1_23824322_0_0 | SS1_23824322_0_0 | SS2_23824322_0_0 | abbreviatedTo | severe insulin resistance,SIR |
| AE1_23824322_1_0 | SS1_23824322_1_0 | SS2_23824322_1_0 | abbreviatedTo | insulin receptor,INSR |
| AE1_23824322_1_1 | SS1_23824322_1_1 | SS2_23824322_1_1 | abbreviatedTo | severe insulin resistance,SIR |
| AE1_23824322_1_2 | SS1_23824322_1_2 | SS2_23824322_1_2 | abbreviatedTo | Donohue syndrome,DS |
| AE1_23824322_1_3 | SS1_23824322_1_3 | SS2_23824322_1_3 | abbreviatedTo | Rabson-Mendenhall syndrome,RMS |
PubmedHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 236-254 | HP_0000855 | denotes | insulin resistance |
| T2 | 646-666 | HP_0000956 | denotes | acanthosis nigricans |
| T3 | 1050-1059 | HP_0001007 | denotes | hirsutism |
| T4 | 1276-1292 | HP_0000121 | denotes | Nephrocalcinosis |
| T5 | 1294-1312 | HP_0000859 | denotes | hyperaldosteronism |
| T6 | 1314-1328 | HP_0000848 | denotes | hyperreninemia |
| T7 | 1334-1345 | HP_0002900 | denotes | hypokalemia |
| T8 | 1365-1377 | HP_0000822 | denotes | hypertension |
| T9 | 1504-1537 | HP_0011741 | denotes | hyperreninemic hyperaldosteronism |
| T10 | 1519-1537 | HP_0000859 | denotes | hyperaldosteronism |
| T11 | 1592-1611 | HP_0012210 | denotes | renal abnormalities |
| T12 | 1592-1611 | HP_0000077 | denotes | renal abnormalities |
DisGeNET5_gene_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 23824322-1#10#26#gene3643 | 160-176 | gene3643 | denotes | insulin receptor |
| 23824322-1#28#32#gene3643 | 178-182 | gene3643 | denotes | INSR |
| 23824322-1#120#136#diseaseC0265344 | 270-286 | diseaseC0265344 | denotes | Donohue syndrome |
| 23824322-1#146#172#diseaseC0271695 | 296-322 | diseaseC0271695 | denotes | Rabson-Mendenhall syndrome |
| 23824322-1#174#177#diseaseC0271695 | 324-327 | diseaseC0271695 | denotes | RMS |
| 23824322-1#120#136#diseaseC0265344 | 270-286 | diseaseC0265344 | denotes | Donohue syndrome |
| 23824322-1#138#140#diseaseC0265344 | 288-290 | diseaseC0265344 | denotes | DS |
| 23824322-1#146#172#diseaseC0271695 | 296-322 | diseaseC0271695 | denotes | Rabson-Mendenhall syndrome |
| 23824322-1#174#177#diseaseC0271695 | 324-327 | diseaseC0271695 | denotes | RMS |
| 23824322-3#0#4#gene3643 | 549-553 | gene3643 | denotes | INSR |
| 23824322-3#58#73#diseaseC0020459 | 607-622 | diseaseC0020459 | denotes | hyperinsulinism |
| 23824322-3#97#117#diseaseC0000889 | 646-666 | diseaseC0000889 | denotes | acanthosis nigricans |
| 10#26#gene3643120#136#diseaseC0265344 | 23824322-1#10#26#gene3643 | 23824322-1#120#136#diseaseC0265344 | associated_with | insulin receptor,Donohue syndrome |
| 10#26#gene3643146#172#diseaseC0271695 | 23824322-1#10#26#gene3643 | 23824322-1#146#172#diseaseC0271695 | associated_with | insulin receptor,Rabson-Mendenhall syndrome |
| 10#26#gene3643174#177#diseaseC0271695 | 23824322-1#10#26#gene3643 | 23824322-1#174#177#diseaseC0271695 | associated_with | insulin receptor,RMS |
| 10#26#gene3643120#136#diseaseC0265344 | 23824322-1#10#26#gene3643 | 23824322-1#120#136#diseaseC0265344 | associated_with | insulin receptor,Donohue syndrome |
| 10#26#gene3643138#140#diseaseC0265344 | 23824322-1#10#26#gene3643 | 23824322-1#138#140#diseaseC0265344 | associated_with | insulin receptor,DS |
| 10#26#gene3643146#172#diseaseC0271695 | 23824322-1#10#26#gene3643 | 23824322-1#146#172#diseaseC0271695 | associated_with | insulin receptor,Rabson-Mendenhall syndrome |
| 10#26#gene3643174#177#diseaseC0271695 | 23824322-1#10#26#gene3643 | 23824322-1#174#177#diseaseC0271695 | associated_with | insulin receptor,RMS |
| 28#32#gene3643120#136#diseaseC0265344 | 23824322-1#28#32#gene3643 | 23824322-1#120#136#diseaseC0265344 | associated_with | INSR,Donohue syndrome |
| 28#32#gene3643146#172#diseaseC0271695 | 23824322-1#28#32#gene3643 | 23824322-1#146#172#diseaseC0271695 | associated_with | INSR,Rabson-Mendenhall syndrome |
| 28#32#gene3643174#177#diseaseC0271695 | 23824322-1#28#32#gene3643 | 23824322-1#174#177#diseaseC0271695 | associated_with | INSR,RMS |
| 28#32#gene3643120#136#diseaseC0265344 | 23824322-1#28#32#gene3643 | 23824322-1#120#136#diseaseC0265344 | associated_with | INSR,Donohue syndrome |
| 28#32#gene3643138#140#diseaseC0265344 | 23824322-1#28#32#gene3643 | 23824322-1#138#140#diseaseC0265344 | associated_with | INSR,DS |
| 28#32#gene3643146#172#diseaseC0271695 | 23824322-1#28#32#gene3643 | 23824322-1#146#172#diseaseC0271695 | associated_with | INSR,Rabson-Mendenhall syndrome |
| 28#32#gene3643174#177#diseaseC0271695 | 23824322-1#28#32#gene3643 | 23824322-1#174#177#diseaseC0271695 | associated_with | INSR,RMS |
| 0#4#gene364358#73#diseaseC0020459 | 23824322-3#0#4#gene3643 | 23824322-3#58#73#diseaseC0020459 | associated_with | INSR,hyperinsulinism |
| 0#4#gene364397#117#diseaseC0000889 | 23824322-3#0#4#gene3643 | 23824322-3#97#117#diseaseC0000889 | associated_with | INSR,acanthosis nigricans |
PubCasesHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TI1 | 22-40 | HP:0000855 | denotes | insulin resistance |
| AB1 | 236-254 | HP:0000855 | denotes | insulin resistance |
| AB2 | 646-666 | HP:0000956 | denotes | acanthosis nigricans |
| AB3 | 1050-1059 | HP:0001007 | denotes | hirsutism |
| AB4 | 1276-1292 | HP:0000121 | denotes | Nephrocalcinosis |
| AB5 | 1294-1312 | HP:0000859 | denotes | hyperaldosteronism |
| AB6 | 1334-1345 | HP:0002900 | denotes | hypokalemia |
| AB7 | 1365-1377 | HP:0000822 | denotes | hypertension |
| AB8 | 1519-1537 | HP:0000859 | denotes | hyperaldosteronism |
PubCasesORDO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| AB1 | 270-286 | ORDO:508 | denotes | Donohue syndrome |
| AB2 | 296-322 | ORDO:769 | denotes | Rabson-Mendenhall syndrome |
| AB3 | 324-327 | ORDO:93307 | denotes | RMS |
| AB4 | 354-357 | ORDO:93307 | denotes | RMS |
| AB5 | 524-527 | ORDO:93307 | denotes | RMS |
| AB6 | 1189-1192 | ORDO:93307 | denotes | RMS |