PubMed:21910226
Annnotations
sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TextSentencer_T1 | 0-156 | Sentence | denotes | Implantable cardioverter defibrillator for progressive hypertrophic cardiomyopathy in a patient with LEOPARD syndrome and a novel PTPN11 mutation Gln510His. |
| TextSentencer_T2 | 157-368 | Sentence | denotes | LEOPARD syndrome (LS), generally caused by heterozygous mutations in the PTPN11 gene, is a rare autosomal-dominant multiple congenital anomaly condition, characterized by skin, facial, and cardiac abnormalities. |
| TextSentencer_T3 | 369-521 | Sentence | denotes | Prognosis appears to be related to the type of structural, myocardial, and arrhythmogenic cardiac disease, especially hypertrophic cardiomyopathy (HCM). |
| TextSentencer_T4 | 522-760 | Sentence | denotes | We report on a woman with LS and a novel Gln510His mutation in PTPN11, who had progressive HCM with congestive heart failure and nonsustained ventricular tachycardia, successfully treated with implantable cardioverter defibrillator (ICD). |
| TextSentencer_T5 | 761-950 | Sentence | denotes | Comparing our patient to the literature suggests that specific mutations at codon 510 in PTPN11 (Gln510Glu, Gln510His, but not Gln510Pro) might be a predictor of fatal cardiac events in LS. |
| TextSentencer_T6 | 951-1108 | Sentence | denotes | Molecular risk stratification and careful evaluations for an indication of ICD implantation are likely to be beneficial in managing patients with LS and HCM. |
| T1 | 0-156 | Sentence | denotes | Implantable cardioverter defibrillator for progressive hypertrophic cardiomyopathy in a patient with LEOPARD syndrome and a novel PTPN11 mutation Gln510His. |
| T2 | 157-368 | Sentence | denotes | LEOPARD syndrome (LS), generally caused by heterozygous mutations in the PTPN11 gene, is a rare autosomal-dominant multiple congenital anomaly condition, characterized by skin, facial, and cardiac abnormalities. |
| T3 | 369-521 | Sentence | denotes | Prognosis appears to be related to the type of structural, myocardial, and arrhythmogenic cardiac disease, especially hypertrophic cardiomyopathy (HCM). |
| T4 | 522-760 | Sentence | denotes | We report on a woman with LS and a novel Gln510His mutation in PTPN11, who had progressive HCM with congestive heart failure and nonsustained ventricular tachycardia, successfully treated with implantable cardioverter defibrillator (ICD). |
| T5 | 761-950 | Sentence | denotes | Comparing our patient to the literature suggests that specific mutations at codon 510 in PTPN11 (Gln510Glu, Gln510His, but not Gln510Pro) might be a predictor of fatal cardiac events in LS. |
| T6 | 951-1108 | Sentence | denotes | Molecular risk stratification and careful evaluations for an indication of ICD implantation are likely to be beneficial in managing patients with LS and HCM. |
DisGeNET
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T0 | 130-136 | gene:5781 | denotes | PTPN11 |
| T1 | 55-82 | disease:C0007194 | denotes | hypertrophic cardiomyopathy |
| T2 | 130-136 | gene:5781 | denotes | PTPN11 |
| T3 | 101-117 | disease:C0175704 | denotes | LEOPARD syndrome |
| T4 | 230-236 | gene:5781 | denotes | PTPN11 |
| T5 | 157-173 | disease:C0175704 | denotes | LEOPARD syndrome |
| T6 | 230-236 | gene:5781 | denotes | PTPN11 |
| T7 | 346-367 | disease:C0018798 | denotes | cardiac abnormalities |
| T8 | 585-591 | gene:5781 | denotes | PTPN11 |
| T9 | 548-550 | disease:C0175704 | denotes | LS |
| T10 | 850-856 | gene:5781 | denotes | PTPN11 |
| T11 | 947-949 | disease:C0175704 | denotes | LS |
| T12 | 850-856 | gene:5781 | denotes | PTPN11 |
| T13 | 929-943 | disease:C0741923 | denotes | cardiac events |
| R1 | T0 | T1 | associated_with | PTPN11,hypertrophic cardiomyopathy |
| R2 | T2 | T3 | associated_with | PTPN11,LEOPARD syndrome |
| R3 | T4 | T5 | associated_with | PTPN11,LEOPARD syndrome |
| R4 | T6 | T7 | associated_with | PTPN11,cardiac abnormalities |
| R5 | T8 | T9 | associated_with | PTPN11,LS |
| R6 | T10 | T11 | associated_with | PTPN11,LS |
| R7 | T12 | T13 | associated_with | PTPN11,cardiac events |
PubmedHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 253-271 | HP_0000006 | denotes | autosomal-dominant |
| T2 | 346-367 | HP_0001627 | denotes | cardiac abnormalities |
| T3 | 487-514 | HP_0001639 | denotes | hypertrophic cardiomyopathy |
| T4 | 500-514 | HP_0001638 | denotes | cardiomyopathy |
| T5 | 622-646 | HP_0001635 | denotes | congestive heart failure |
| T6 | 633-646 | HP_0001635 | denotes | heart failure |
| T7 | 664-687 | HP_0004756 | denotes | ventricular tachycardia |
| T8 | 676-687 | HP_0001649 | denotes | tachycardia |
Allie
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| SS1_21910226_1_0 | 157-173 | expanded | denotes | LEOPARD syndrome |
| SS2_21910226_1_0 | 175-177 | abbr | denotes | LS |
| SS1_21910226_2_0 | 487-514 | expanded | denotes | hypertrophic cardiomyopathy |
| SS2_21910226_2_0 | 516-519 | abbr | denotes | HCM |
| SS1_21910226_3_0 | 715-753 | expanded | denotes | implantable cardioverter defibrillator |
| SS2_21910226_3_0 | 755-758 | abbr | denotes | ICD |
| AE1_21910226_1_0 | SS1_21910226_1_0 | SS2_21910226_1_0 | abbreviatedTo | LEOPARD syndrome,LS |
| AE1_21910226_2_0 | SS1_21910226_2_0 | SS2_21910226_2_0 | abbreviatedTo | hypertrophic cardiomyopathy,HCM |
| AE1_21910226_3_0 | SS1_21910226_3_0 | SS2_21910226_3_0 | abbreviatedTo | implantable cardioverter defibrillator,ICD |
DisGeNET5_variant_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 21910226-0#146#155#geners397507550 | 146-155 | geners397507550 | denotes | Gln510His |
| 21910226-0#101#117#diseaseC0175704 | 101-117 | diseaseC0175704 | denotes | LEOPARD syndrome |
| 21910226-4#127#136#geners121918470 | 888-897 | geners121918470 | denotes | Gln510Pro |
| 21910226-4#186#188#diseaseC0175704 | 947-949 | diseaseC0175704 | denotes | LS |
| 146#155#geners397507550101#117#diseaseC0175704 | 21910226-0#146#155#geners397507550 | 21910226-0#101#117#diseaseC0175704 | associated_with | Gln510His,LEOPARD syndrome |
| 127#136#geners121918470186#188#diseaseC0175704 | 21910226-4#127#136#geners121918470 | 21910226-4#186#188#diseaseC0175704 | associated_with | Gln510Pro,LS |
DisGeNET5_gene_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 21910226-0#130#136#gene5781 | 130-136 | gene5781 | denotes | PTPN11 |
| 21910226-0#55#82#diseaseC0007194 | 55-82 | diseaseC0007194 | denotes | hypertrophic cardiomyopathy |
| 21910226-0#101#117#diseaseC0175704 | 101-117 | diseaseC0175704 | denotes | LEOPARD syndrome |
| 130#136#gene578155#82#diseaseC0007194 | 21910226-0#130#136#gene5781 | 21910226-0#55#82#diseaseC0007194 | associated_with | PTPN11,hypertrophic cardiomyopathy |
| 130#136#gene5781101#117#diseaseC0175704 | 21910226-0#130#136#gene5781 | 21910226-0#101#117#diseaseC0175704 | associated_with | PTPN11,LEOPARD syndrome |
UBERON-AE
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| PD-UBERON-AE-B_T1 | 633-638 | http://purl.obolibrary.org/obo/UBERON_0000948 | denotes | heart |
PubCasesHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TI1 | 55-82 | HP:0001639 | denotes | hypertrophic cardiomyopathy |
| AB1 | 487-514 | HP:0001639 | denotes | hypertrophic cardiomyopathy |
| AB2 | 622-646 | HP:0001635 | denotes | congestive heart failure |
| AB3 | 664-687 | HP:0004756 | denotes | ventricular tachycardia |
PubCasesORDO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| AB1 | 157-173 | ORDO:500 | denotes | LEOPARD syndrome |
| TI1 | 101-117 | ORDO:500 | denotes | LEOPARD syndrome |
performance-test
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| PD-UBERON-AE-B_T1 | 633-638 | http://purl.obolibrary.org/obo/UBERON_0000948 | denotes | heart |