PubMed:20534762
Annnotations
LitCoin-entities
Id | Subject | Object | Predicate | Lexical cue | db_id |
---|---|---|---|---|---|
7520 | 27-35 | GeneOrGeneProduct | denotes | TSH-beta | NCBIGene:7252 |
7521 | 60-93 | DiseaseOrPhenotypicFeature | denotes | congenital central hypothyroidism | MESH:D003409 |
7522 | 119-122 | GeneOrGeneProduct | denotes | TSH | NCBIGene:7252 |
7523 | 143-151 | OrganismTaxon | denotes | Patients | NCBITaxon:9606 |
7524 | 157-165 | GeneOrGeneProduct | denotes | TSH-beta | NCBIGene:7252 |
7525 | 186-211 | DiseaseOrPhenotypicFeature | denotes | congenital hypothyroidism | MESH:D003409 |
7526 | 226-229 | GeneOrGeneProduct | denotes | TSH | NCBIGene:7252 |
7527 | 395-403 | GeneOrGeneProduct | denotes | TSH-beta | NCBIGene:7252 |
7528 | 430-438 | OrganismTaxon | denotes | patients | NCBITaxon:9606 |
7529 | 444-477 | DiseaseOrPhenotypicFeature | denotes | congenital central hypothyroidism | MESH:D003409 |
7530 | 515-521 | DiseaseOrPhenotypicFeature | denotes | anemia | MESH:D000740 |
7531 | 532-539 | OrganismTaxon | denotes | Patient | NCBITaxon:9606 |
7532 | 559-565 | SequenceVariant | denotes | G to A | c|SUB|G||A |
7533 | 978-985 | OrganismTaxon | denotes | patient | NCBITaxon:9606 |
7534 | 1066-1073 | SequenceVariant | denotes | 313delT | c|DEL|313|T |
7535 | 1075-1086 | SequenceVariant | denotes | C105Vfs114X | p|FS|C|105|V|114 |
7536 | 1153-1192 | SequenceVariant | denotes | G for A at cDNA nucleotide position 323 | c|SUB|G|323|A |
7537 | 1209-1213 | SequenceVariant | denotes | C88Y | p|SUB|C|88|Y |
7538 | 1299-1333 | GeneOrGeneProduct | denotes | glycoprotein hormone-beta subunits | NCBIGene:122876 |
7539 | 1383-1387 | SequenceVariant | denotes | C88Y | p|SUB|C|88|Y |
7540 | 1519-1523 | SequenceVariant | denotes | C88Y | p|SUB|C|88|Y |
7541 | 1580-1594 | DiseaseOrPhenotypicFeature | denotes | TSH deficiency | MESH:D007037 |
7542 | 1656-1685 | DiseaseOrPhenotypicFeature | denotes | isolated pituitary deficiency | MESH:C566321 |
7543 | 1760-1782 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | MESH:D007037 |
7544 | 1833-1839 | DiseaseOrPhenotypicFeature | denotes | anemia | MESH:D000740 |
LitCoin-sentences
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 0-133 | Sentence | denotes | Two novel mutations of the TSH-beta subunit gene underlying congenital central hypothyroidism undetectable in neonatal TSH screening. |
T2 | 134-142 | Sentence | denotes | CONTEXT: |
T3 | 143-255 | Sentence | denotes | Patients with TSH-beta subunit defects and congenital hypothyroidism are missed by TSH-based neonatal screening. |
T4 | 256-266 | Sentence | denotes | OBJECTIVE: |
T5 | 267-522 | Sentence | denotes | Our objective was to report the molecular consequences of a novel splice-junction mutation and a novel missense mutation in the TSH-beta subunit gene found in two patients with congenital central hypothyroidism and conventional treatment-resistant anemia. |
T6 | 523-531 | Sentence | denotes | RESULTS: |
T7 | 532-629 | Sentence | denotes | Patient 1 had a homozygous G to A nucleotide change at the 5' donor splice site of exon/intron 2. |
T8 | 630-697 | Sentence | denotes | This resulted in a silent change at codon 34 of the mature protein. |
T9 | 698-838 | Sentence | denotes | In vitro splicing assays showed that the mutant minigene dramatically affected pre-mRNA processing, causing exon 2 to be completely skipped. |
T10 | 839-974 | Sentence | denotes | The putative product from a new out-of-frame translational start point in exon 3 is expected to yield a nonsense 25-amino-acid peptide. |
T11 | 975-1221 | Sentence | denotes | In patient 2, sequence analysis revealed a compound heterozygosis for the already reported 313delT (C105Vfs114X) mutation and for a second novel mutation in exon 3, substituting G for A at cDNA nucleotide position 323, resulting in a C88Y change. |
T12 | 1222-1334 | Sentence | denotes | This cysteine residue is conserved among all dimeric pituitary and placental glycoprotein hormone-beta subunits. |
T13 | 1335-1431 | Sentence | denotes | Data from in silico analysis confirmed that the C88Y mutation would affect subunit conformation. |
T14 | 1432-1554 | Sentence | denotes | Indeed, two different bioinformatics approaches, PolyPhen and SIFT analysis, predicted C88Y to be a damaging substitution. |
T15 | 1555-1567 | Sentence | denotes | CONCLUSIONS: |
T16 | 1568-1736 | Sentence | denotes | In isolated TSH deficiency, the exact molecular diagnosis is mandatory for diagnosis of isolated pituitary deficiency, delineation of prognosis, and genetic counseling. |
T17 | 1737-1862 | Sentence | denotes | Moreover, diagnosis of central hypothyroidism should be considered in the face of severe infant anemia of uncertain etiology. |
LitCoin-entities-OrganismTaxon-PD
Id | Subject | Object | Predicate | Lexical cue | db_id |
---|---|---|---|---|---|
T1 | 515-521 | OrganismTaxon | denotes | anemia | NCBItxid:12939 |
T2 | 666-671 | OrganismTaxon | denotes | codon | NCBItxid:79338 |
T3 | 1289-1298 | OrganismTaxon | denotes | placental | NCBItxid:9347 |
T4 | 1833-1839 | OrganismTaxon | denotes | anemia | NCBItxid:12939 |
LitCoin_Mondo
Id | Subject | Object | Predicate | Lexical cue | mondo_id |
---|---|---|---|---|---|
T1 | 60-70 | DiseaseOrPhenotypicFeature | denotes | congenital | 0021140 |
T2 | 79-93 | DiseaseOrPhenotypicFeature | denotes | hypothyroidism | 0005420 |
T3 | 186-211 | DiseaseOrPhenotypicFeature | denotes | congenital hypothyroidism | 0018612 |
T4 | 186-196 | DiseaseOrPhenotypicFeature | denotes | congenital | 0021140 |
T5 | 197-211 | DiseaseOrPhenotypicFeature | denotes | hypothyroidism | 0005420 |
T6 | 444-454 | DiseaseOrPhenotypicFeature | denotes | congenital | 0021140 |
T7 | 463-477 | DiseaseOrPhenotypicFeature | denotes | hypothyroidism | 0005420 |
T8 | 515-521 | DiseaseOrPhenotypicFeature | denotes | anemia | 0002280 |
T9 | 819-829 | DiseaseOrPhenotypicFeature | denotes | completely | 0700063 |
T10 | 1665-1685 | DiseaseOrPhenotypicFeature | denotes | pituitary deficiency | 0015127 |
T11 | 1768-1782 | DiseaseOrPhenotypicFeature | denotes | hypothyroidism | 0005420 |
T12 | 1833-1839 | DiseaseOrPhenotypicFeature | denotes | anemia | 0002280 |
LitCoin-SeqVar
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 1066-1073 | SequenceVariant | denotes | 313delT |
T2 | 1209-1213 | SequenceVariant | denotes | C88Y |
T3 | 1383-1387 | SequenceVariant | denotes | C88Y |
T4 | 1519-1523 | SequenceVariant | denotes | C88Y |
LitCoin-GeneOrGeneProduct-v0
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 4-9 | GeneOrGeneProduct | denotes | novel |
T2 | 10-19 | GeneOrGeneProduct | denotes | mutations |
T3 | 27-35 | GeneOrGeneProduct | denotes | TSH-beta |
T4 | 157-165 | GeneOrGeneProduct | denotes | TSH-beta |
T5 | 174-181 | GeneOrGeneProduct | denotes | defects |
T6 | 216-222 | GeneOrGeneProduct | denotes | missed |
T7 | 230-235 | GeneOrGeneProduct | denotes | based |
T8 | 327-332 | GeneOrGeneProduct | denotes | novel |
T9 | 333-339 | GeneOrGeneProduct | denotes | splice |
T10 | 349-357 | GeneOrGeneProduct | denotes | mutation |
T11 | 364-369 | GeneOrGeneProduct | denotes | novel |
T12 | 370-378 | GeneOrGeneProduct | denotes | missense |
T13 | 379-387 | GeneOrGeneProduct | denotes | mutation |
T14 | 395-403 | GeneOrGeneProduct | denotes | TSH-beta |
T15 | 542-547 | GeneOrGeneProduct | denotes | had a |
T16 | 600-606 | GeneOrGeneProduct | denotes | splice |
T17 | 644-648 | GeneOrGeneProduct | denotes | in a |
T18 | 689-696 | GeneOrGeneProduct | denotes | protein |
T19 | 707-715 | GeneOrGeneProduct | denotes | splicing |
T20 | 739-745 | GeneOrGeneProduct | denotes | mutant |
T21 | 777-796 | GeneOrGeneProduct | denotes | pre-mRNA processing |
T22 | 830-837 | GeneOrGeneProduct | denotes | skipped |
T23 | 843-859 | GeneOrGeneProduct | denotes | putative product |
T24 | 871-874 | GeneOrGeneProduct | denotes | out |
T25 | 898-903 | GeneOrGeneProduct | denotes | start |
T26 | 904-909 | GeneOrGeneProduct | denotes | point |
T27 | 935-940 | GeneOrGeneProduct | denotes | yield |
T28 | 961-965 | GeneOrGeneProduct | denotes | acid |
T29 | 1088-1096 | GeneOrGeneProduct | denotes | mutation |
T30 | 1114-1119 | GeneOrGeneProduct | denotes | novel |
T31 | 1120-1128 | GeneOrGeneProduct | denotes | mutation |
T32 | 1164-1168 | GeneOrGeneProduct | denotes | cDNA |
T33 | 1204-1208 | GeneOrGeneProduct | denotes | in a |
T34 | 1247-1256 | GeneOrGeneProduct | denotes | conserved |
T35 | 1263-1266 | GeneOrGeneProduct | denotes | all |
T36 | 1299-1311 | GeneOrGeneProduct | denotes | glycoprotein |
T37 | 1312-1319 | GeneOrGeneProduct | denotes | hormone |
T38 | 1320-1324 | GeneOrGeneProduct | denotes | beta |
T39 | 1388-1396 | GeneOrGeneProduct | denotes | mutation |
T40 | 1481-1489 | GeneOrGeneProduct | denotes | PolyPhen |
T41 | 1509-1518 | GeneOrGeneProduct | denotes | predicted |
T42 | 1532-1540 | GeneOrGeneProduct | denotes | damaging |
T43 | 1811-1815 | GeneOrGeneProduct | denotes | face |
LitCoin-GeneOrGeneProduct-v2
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 4-9 | GeneOrGeneProduct | denotes | novel |
T2 | 27-35 | GeneOrGeneProduct | denotes | TSH-beta |
T3 | 157-165 | GeneOrGeneProduct | denotes | TSH-beta |
T4 | 327-332 | GeneOrGeneProduct | denotes | novel |
T5 | 364-369 | GeneOrGeneProduct | denotes | novel |
T6 | 395-403 | GeneOrGeneProduct | denotes | TSH-beta |
T7 | 689-696 | GeneOrGeneProduct | denotes | protein |
T8 | 739-745 | GeneOrGeneProduct | denotes | mutant |
T9 | 777-796 | GeneOrGeneProduct | denotes | pre-mRNA processing |
T10 | 843-859 | GeneOrGeneProduct | denotes | putative product |
T11 | 898-903 | GeneOrGeneProduct | denotes | start |
T12 | 961-965 | GeneOrGeneProduct | denotes | acid |
T13 | 1114-1119 | GeneOrGeneProduct | denotes | novel |
T14 | 1164-1168 | GeneOrGeneProduct | denotes | cDNA |
T15 | 1247-1256 | GeneOrGeneProduct | denotes | conserved |
T16 | 1299-1311 | GeneOrGeneProduct | denotes | glycoprotein |
T17 | 1312-1319 | GeneOrGeneProduct | denotes | hormone |
T18 | 1320-1324 | GeneOrGeneProduct | denotes | beta |
T19 | 1811-1815 | GeneOrGeneProduct | denotes | face |
LitCoin-Disease-MeSH
Id | Subject | Object | Predicate | Lexical cue | originalLabel |
---|---|---|---|---|---|
T1 | 71-93 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 |
T2 | 186-211 | DiseaseOrPhenotypicFeature | denotes | congenital hypothyroidism | D003409 |
T3 | 455-477 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 |
T4 | 515-521 | DiseaseOrPhenotypicFeature | denotes | anemia | D000740 |
T5 | 1580-1594 | DiseaseOrPhenotypicFeature | denotes | TSH deficiency | D007037 |
T6 | 1760-1782 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 |
T7 | 1833-1839 | DiseaseOrPhenotypicFeature | denotes | anemia | D000740 |
LitCoin-GeneOrGeneProduct-v3
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 27-35 | GeneOrGeneProduct | denotes | TSH-beta |
T2 | 157-165 | GeneOrGeneProduct | denotes | TSH-beta |
T3 | 395-403 | GeneOrGeneProduct | denotes | TSH-beta |
T4 | 843-859 | GeneOrGeneProduct | denotes | putative product |
T5 | 1299-1311 | GeneOrGeneProduct | denotes | glycoprotein |
T6 | 1320-1333 | GeneOrGeneProduct | denotes | beta subunits |
LitCoin_Mondo_095
Id | Subject | Object | Predicate | Lexical cue | mondo_id |
---|---|---|---|---|---|
T1 | 71-93 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | 0016410 |
T2 | 186-211 | DiseaseOrPhenotypicFeature | denotes | congenital hypothyroidism | 0018612 |
T3 | 455-477 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | 0016410 |
T4 | 515-521 | DiseaseOrPhenotypicFeature | denotes | anemia | 0002280 |
T5 | 1275-1284 | DiseaseOrPhenotypicFeature | denotes | pituitary | 0021156 |
T6 | 1571-1594 | DiseaseOrPhenotypicFeature | denotes | isolated TSH deficiency | 0010139 |
T7 | 1665-1685 | DiseaseOrPhenotypicFeature | denotes | pituitary deficiency | 0015127 |
T8 | 1760-1782 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | 0016410 |
T9 | 1811-1815 | DiseaseOrPhenotypicFeature | denotes | face | 0010953 |
T10 | 1833-1839 | DiseaseOrPhenotypicFeature | denotes | anemia | 0002280 |
LitCoin-MeSH-Disease-2
Id | Subject | Object | Predicate | Lexical cue | ID: |
---|---|---|---|---|---|
T1 | 71-93 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 |
T2 | 186-211 | DiseaseOrPhenotypicFeature | denotes | congenital hypothyroidism | D003409 |
T3 | 455-477 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 |
T4 | 515-521 | DiseaseOrPhenotypicFeature | denotes | anemia | D000740 |
T5 | 1580-1594 | DiseaseOrPhenotypicFeature | denotes | TSH deficiency | D007037 |
T6 | 1656-1685 | DiseaseOrPhenotypicFeature | denotes | isolated pituitary deficiency | DISEASE |
T7 | 1760-1782 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 |
T8 | 1833-1839 | DiseaseOrPhenotypicFeature | denotes | anemia | D000740 |
LitCoin-MONDO_bioort2019
Id | Subject | Object | Predicate | Lexical cue | #label |
---|---|---|---|---|---|
T1 | 71-93 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 |
T2 | 186-211 | DiseaseOrPhenotypicFeature | denotes | congenital hypothyroidism | D003409 |
T3 | 455-477 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 |
T4 | 515-521 | DiseaseOrPhenotypicFeature | denotes | anemia | D000740 |
T5 | 1580-1594 | DiseaseOrPhenotypicFeature | denotes | TSH deficiency | D007037 |
T6 | 1656-1685 | DiseaseOrPhenotypicFeature | denotes | isolated pituitary deficiency | DISEASE |
T7 | 1760-1782 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 |
T8 | 1833-1839 | DiseaseOrPhenotypicFeature | denotes | anemia | D000740 |
LitCoin-Chemical-MeSH-CHEBI
Id | Subject | Object | Predicate | Lexical cue | ID: |
---|---|---|---|---|---|
T1 | 27-30 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_17842|http://purl.obolibrary.org/obo/CHEBI_137741 |
T3 | 119-122 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_17842|http://purl.obolibrary.org/obo/CHEBI_137741 |
T5 | 157-160 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_17842|http://purl.obolibrary.org/obo/CHEBI_137741 |
T7 | 226-229 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_17842|http://purl.obolibrary.org/obo/CHEBI_137741 |
T9 | 395-398 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_17842|http://purl.obolibrary.org/obo/CHEBI_137741 |
T11 | 1227-1243 | ChemicalEntity | denotes | cysteine residue | http://purl.obolibrary.org/obo/CHEBI_32460 |
T12 | 1580-1583 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_17842|http://purl.obolibrary.org/obo/CHEBI_137741 |
LitCoin-NCBITaxon-2
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 430-438 | OrganismTaxon | denotes | patients |
T2 | 532-539 | OrganismTaxon | denotes | Patient |
T3 | 978-985 | OrganismTaxon | denotes | patient |
T4 | 1289-1298 | OrganismTaxon | denotes | placental |
LitCoin-training-merged
Id | Subject | Object | Predicate | Lexical cue | #label | ID: |
---|---|---|---|---|---|---|
T12 | 1580-1583 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_137741|http://purl.obolibrary.org/obo/CHEBI_17842 | |
T11 | 1227-1243 | ChemicalEntity | denotes | cysteine residue | http://purl.obolibrary.org/obo/CHEBI_32460 | |
T9 | 395-398 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_137741|http://purl.obolibrary.org/obo/CHEBI_17842 | |
T7 | 226-229 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_137741|http://purl.obolibrary.org/obo/CHEBI_17842 | |
T5 | 157-160 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_137741|http://purl.obolibrary.org/obo/CHEBI_17842 | |
T3 | 119-122 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_137741|http://purl.obolibrary.org/obo/CHEBI_17842 | |
T1 | 27-30 | ChemicalEntity | denotes | TSH | http://purl.obolibrary.org/obo/CHEBI_137741|http://purl.obolibrary.org/obo/CHEBI_17842 | |
T6 | 1320-1333 | GeneOrGeneProduct | denotes | beta subunits | ||
T8897 | 1299-1311 | GeneOrGeneProduct | denotes | glycoprotein | ||
T4 | 843-859 | GeneOrGeneProduct | denotes | putative product | ||
T5945 | 395-403 | GeneOrGeneProduct | denotes | TSH-beta | ||
T2 | 157-165 | GeneOrGeneProduct | denotes | TSH-beta | ||
T89104 | 27-35 | GeneOrGeneProduct | denotes | TSH-beta | ||
T8 | 1833-1839 | DiseaseOrPhenotypicFeature | denotes | anemia | D000740 | |
T31863 | 1760-1782 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 | |
T95573 | 1656-1685 | DiseaseOrPhenotypicFeature | denotes | isolated pituitary deficiency | DISEASE | |
T65195 | 1580-1594 | DiseaseOrPhenotypicFeature | denotes | TSH deficiency | D007037 | |
T54252 | 515-521 | DiseaseOrPhenotypicFeature | denotes | anemia | D000740 | |
T62466 | 455-477 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 | |
T3451 | 186-211 | DiseaseOrPhenotypicFeature | denotes | congenital hypothyroidism | D003409 | |
T69120 | 71-93 | DiseaseOrPhenotypicFeature | denotes | central hypothyroidism | D007037 | |
T48940 | 1289-1298 | OrganismTaxon | denotes | placental | ||
T88293 | 978-985 | OrganismTaxon | denotes | patient | ||
T87381 | 532-539 | OrganismTaxon | denotes | Patient | ||
T90879 | 430-438 | OrganismTaxon | denotes | patients | ||
T12790 | 1519-1523 | SequenceVariant | denotes | C88Y | ||
T21214 | 1383-1387 | SequenceVariant | denotes | C88Y | ||
T76614 | 1209-1213 | SequenceVariant | denotes | C88Y | ||
T33335 | 1066-1073 | SequenceVariant | denotes | 313delT |
PubmedHPO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 186-211 | HP_0000851 | denotes | congenital hypothyroidism |
T2 | 197-211 | HP_0000821 | denotes | hypothyroidism |
UBERON-AE
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
PD-UBERON-AE-B_T1 | 71-78 | http://purl.obolibrary.org/obo/UBERON_0012131 | denotes | central |
PD-UBERON-AE-B_T2 | 455-462 | http://purl.obolibrary.org/obo/UBERON_0012131 | denotes | central |
PD-UBERON-AE-B_T3 | 1760-1767 | http://purl.obolibrary.org/obo/UBERON_0012131 | denotes | central |
PD-UBERON-AE-B_T4 | 1811-1815 | http://purl.obolibrary.org/obo/UBERON_0001456 | denotes | face |
PubCasesHPO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
AB1 | 186-211 | HP:0000851 | denotes | congenital hypothyroidism |
TI1 | 71-93 | HP:0011787 | denotes | central hypothyroidism |
AB2 | 455-477 | HP:0011787 | denotes | central hypothyroidism |
AB3 | 515-521 | HP:0001903 | denotes | anemia |
AB4 | 1760-1782 | HP:0011787 | denotes | central hypothyroidism |
AB5 | 1833-1839 | HP:0001903 | denotes | anemia |
PubCasesORDO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
AB1 | 1571-1594 | ORDO:90674 | denotes | isolated TSH deficiency |
sentences
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
TextSentencer_T1 | 0-133 | Sentence | denotes | Two novel mutations of the TSH-beta subunit gene underlying congenital central hypothyroidism undetectable in neonatal TSH screening. |
TextSentencer_T2 | 134-142 | Sentence | denotes | CONTEXT: |
TextSentencer_T3 | 143-255 | Sentence | denotes | Patients with TSH-beta subunit defects and congenital hypothyroidism are missed by TSH-based neonatal screening. |
TextSentencer_T4 | 256-266 | Sentence | denotes | OBJECTIVE: |
TextSentencer_T5 | 267-522 | Sentence | denotes | Our objective was to report the molecular consequences of a novel splice-junction mutation and a novel missense mutation in the TSH-beta subunit gene found in two patients with congenital central hypothyroidism and conventional treatment-resistant anemia. |
TextSentencer_T6 | 523-531 | Sentence | denotes | RESULTS: |
TextSentencer_T7 | 532-629 | Sentence | denotes | Patient 1 had a homozygous G to A nucleotide change at the 5' donor splice site of exon/intron 2. |
TextSentencer_T8 | 630-697 | Sentence | denotes | This resulted in a silent change at codon 34 of the mature protein. |
TextSentencer_T9 | 698-838 | Sentence | denotes | In vitro splicing assays showed that the mutant minigene dramatically affected pre-mRNA processing, causing exon 2 to be completely skipped. |
TextSentencer_T10 | 839-974 | Sentence | denotes | The putative product from a new out-of-frame translational start point in exon 3 is expected to yield a nonsense 25-amino-acid peptide. |
TextSentencer_T11 | 975-1221 | Sentence | denotes | In patient 2, sequence analysis revealed a compound heterozygosis for the already reported 313delT (C105Vfs114X) mutation and for a second novel mutation in exon 3, substituting G for A at cDNA nucleotide position 323, resulting in a C88Y change. |
TextSentencer_T12 | 1222-1334 | Sentence | denotes | This cysteine residue is conserved among all dimeric pituitary and placental glycoprotein hormone-beta subunits. |
TextSentencer_T13 | 1335-1431 | Sentence | denotes | Data from in silico analysis confirmed that the C88Y mutation would affect subunit conformation. |
TextSentencer_T14 | 1432-1554 | Sentence | denotes | Indeed, two different bioinformatics approaches, PolyPhen and SIFT analysis, predicted C88Y to be a damaging substitution. |
TextSentencer_T15 | 1555-1567 | Sentence | denotes | CONCLUSIONS: |
TextSentencer_T16 | 1568-1736 | Sentence | denotes | In isolated TSH deficiency, the exact molecular diagnosis is mandatory for diagnosis of isolated pituitary deficiency, delineation of prognosis, and genetic counseling. |
TextSentencer_T17 | 1737-1862 | Sentence | denotes | Moreover, diagnosis of central hypothyroidism should be considered in the face of severe infant anemia of uncertain etiology. |
T1 | 0-133 | Sentence | denotes | Two novel mutations of the TSH-beta subunit gene underlying congenital central hypothyroidism undetectable in neonatal TSH screening. |
T2 | 134-142 | Sentence | denotes | CONTEXT: |
T3 | 143-255 | Sentence | denotes | Patients with TSH-beta subunit defects and congenital hypothyroidism are missed by TSH-based neonatal screening. |
T4 | 256-266 | Sentence | denotes | OBJECTIVE: |
T5 | 267-522 | Sentence | denotes | Our objective was to report the molecular consequences of a novel splice-junction mutation and a novel missense mutation in the TSH-beta subunit gene found in two patients with congenital central hypothyroidism and conventional treatment-resistant anemia. |
T6 | 523-531 | Sentence | denotes | RESULTS: |
T7 | 532-629 | Sentence | denotes | Patient 1 had a homozygous G to A nucleotide change at the 5' donor splice site of exon/intron 2. |
T8 | 630-697 | Sentence | denotes | This resulted in a silent change at codon 34 of the mature protein. |
T9 | 698-838 | Sentence | denotes | In vitro splicing assays showed that the mutant minigene dramatically affected pre-mRNA processing, causing exon 2 to be completely skipped. |
T10 | 839-974 | Sentence | denotes | The putative product from a new out-of-frame translational start point in exon 3 is expected to yield a nonsense 25-amino-acid peptide. |
T11 | 975-1221 | Sentence | denotes | In patient 2, sequence analysis revealed a compound heterozygosis for the already reported 313delT (C105Vfs114X) mutation and for a second novel mutation in exon 3, substituting G for A at cDNA nucleotide position 323, resulting in a C88Y change. |
T12 | 1222-1334 | Sentence | denotes | This cysteine residue is conserved among all dimeric pituitary and placental glycoprotein hormone-beta subunits. |
T13 | 1335-1431 | Sentence | denotes | Data from in silico analysis confirmed that the C88Y mutation would affect subunit conformation. |
T14 | 1432-1554 | Sentence | denotes | Indeed, two different bioinformatics approaches, PolyPhen and SIFT analysis, predicted C88Y to be a damaging substitution. |
T15 | 1555-1567 | Sentence | denotes | CONCLUSIONS: |
T16 | 1568-1736 | Sentence | denotes | In isolated TSH deficiency, the exact molecular diagnosis is mandatory for diagnosis of isolated pituitary deficiency, delineation of prognosis, and genetic counseling. |
T17 | 1737-1862 | Sentence | denotes | Moreover, diagnosis of central hypothyroidism should be considered in the face of severe infant anemia of uncertain etiology. |
performance-test
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
PD-UBERON-AE-B_T1 | 71-78 | http://purl.obolibrary.org/obo/UBERON_0012131 | denotes | central |
PD-UBERON-AE-B_T2 | 455-462 | http://purl.obolibrary.org/obo/UBERON_0012131 | denotes | central |
PD-UBERON-AE-B_T3 | 1760-1767 | http://purl.obolibrary.org/obo/UBERON_0012131 | denotes | central |
PD-UBERON-AE-B_T4 | 1289-1298 | http://purl.obolibrary.org/obo/UBERON_0001987 | denotes | placental |
PD-UBERON-AE-B_T5 | 1811-1815 | http://purl.obolibrary.org/obo/UBERON_0001456 | denotes | face |
tmVarCorpus
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 1066-1073 | DNAMutation:c|DEL|313|T | denotes | 313delT |
T2 | 1075-1086 | ProteinMutation:p|FS|C|105|V|114 | denotes | C105Vfs114X |
T3 | 1209-1213 | ProteinMutation:p|SUB|C|88|Y | denotes | C88Y |
T4 | 1383-1387 | ProteinMutation:p|SUB|C|88|Y | denotes | C88Y |
T5 | 1519-1523 | ProteinMutation:p|SUB|C|88|Y | denotes | C88Y |