PubMed:18363941
Annnotations
PubMed_ArguminSci
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 46-75 | DRI_Background | denotes | Kufs' disease (adult neuronal |
T2 | 97-205 | DRI_Background | denotes | ) is a rare form of neurodegenerative lysosomal storage disease, the genetic basis of which remains obscure. |
T3 | 206-428 | DRI_Challenge | denotes | We present a case of a 53-year-old man with a long history of adult onset epilepsy who presented with confusion and amnesia, and subsequently underwent rapidly progressive cognitive decline associated with myoclonic jerks. |
T4 | 429-482 | DRI_Background | denotes | The clinical diagnosis was Creutzfeldt Jakob disease. |
T5 | 483-573 | DRI_Background | denotes | However, autopsy brain examination revealed changes of Kufs' disease (Adult onset neuronal |
T6 | 595-626 | DRI_Background | denotes | , or ANCL, also known as CLN4). |
T7 | 627-825 | DRI_Outcome | denotes | No specific gross abnormalities were found but light microscopic examination revealed widespread neuronal ballooning and histochemical staining showed neuronal accumulation of PAS-positive material. |
T8 | 826-931 | DRI_Outcome | denotes | Ultrastructural examination demonstrated excessive and abnormal lipopigment lysosomes typical of neuronal |
T9 | 953-954 | DRI_Outcome | denotes | . |
T10 | 955-1069 | DRI_Outcome | denotes | The typical clinical and pathologic features of the Kufs' disease are discussed and the classification of neuronal |
T11 | 1092-1104 | DRI_Outcome | denotes | is reviewed. |
PMID_GLOBAL
Id | Subject | Object | Predicate | Lexical cue | mondo_id |
---|---|---|---|---|---|
T1 | 46-59 | DiseaseOrPhenotypicFeature | denotes | Kufs' disease | 0019260 |
T2 | 61-97 | DiseaseOrPhenotypicFeature | denotes | adult neuronal ceroid lipofuscinosis | 0019260 |
T3 | 135-160 | DiseaseOrPhenotypicFeature | denotes | lysosomal storage disease | 0002561 |
T4 | 280-288 | DiseaseOrPhenotypicFeature | denotes | epilepsy | 0005027 |
T5 | 322-329 | DiseaseOrPhenotypicFeature | denotes | amnesia | 0001152 |
T6 | 456-481 | DiseaseOrPhenotypicFeature | denotes | Creutzfeldt Jakob disease | 0005357 |
T7 | 538-551 | DiseaseOrPhenotypicFeature | denotes | Kufs' disease | 0019260 |
T8 | 565-595 | DiseaseOrPhenotypicFeature | denotes | neuronal ceroid lipofuscinosis | 0016295 |
T9 | 600-604 | DiseaseOrPhenotypicFeature | denotes | ANCL | 0019260 |
T10 | 803-806 | DiseaseOrPhenotypicFeature | denotes | PAS | 0004277 |
T11 | 923-953 | DiseaseOrPhenotypicFeature | denotes | neuronal ceroid lipofuscinosis | 0016295 |
T12 | 1007-1020 | DiseaseOrPhenotypicFeature | denotes | Kufs' disease | 0019260 |
T13 | 1061-1091 | DiseaseOrPhenotypicFeature | denotes | neuronal ceroid lipofuscinosis | 0016295 |
sentences
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
TextSentencer_T1 | 0-45 | Sentence | denotes | 53-year-old man with rapid cognitive decline. |
TextSentencer_T2 | 46-205 | Sentence | denotes | Kufs' disease (adult neuronal ceroid lipofuscinosis) is a rare form of neurodegenerative lysosomal storage disease, the genetic basis of which remains obscure. |
TextSentencer_T3 | 206-428 | Sentence | denotes | We present a case of a 53-year-old man with a long history of adult onset epilepsy who presented with confusion and amnesia, and subsequently underwent rapidly progressive cognitive decline associated with myoclonic jerks. |
TextSentencer_T4 | 429-482 | Sentence | denotes | The clinical diagnosis was Creutzfeldt Jakob disease. |
TextSentencer_T5 | 483-626 | Sentence | denotes | However, autopsy brain examination revealed changes of Kufs' disease (Adult onset neuronal ceroid lipofuscinosis, or ANCL, also known as CLN4). |
TextSentencer_T6 | 627-825 | Sentence | denotes | No specific gross abnormalities were found but light microscopic examination revealed widespread neuronal ballooning and histochemical staining showed neuronal accumulation of PAS-positive material. |
TextSentencer_T7 | 826-954 | Sentence | denotes | Ultrastructural examination demonstrated excessive and abnormal lipopigment lysosomes typical of neuronal ceroid lipofuscinosis. |
TextSentencer_T8 | 955-1104 | Sentence | denotes | The typical clinical and pathologic features of the Kufs' disease are discussed and the classification of neuronal ceroid lipofuscinosis is reviewed. |
T1 | 0-45 | Sentence | denotes | 53-year-old man with rapid cognitive decline. |
T2 | 46-205 | Sentence | denotes | Kufs' disease (adult neuronal ceroid lipofuscinosis) is a rare form of neurodegenerative lysosomal storage disease, the genetic basis of which remains obscure. |
T3 | 206-428 | Sentence | denotes | We present a case of a 53-year-old man with a long history of adult onset epilepsy who presented with confusion and amnesia, and subsequently underwent rapidly progressive cognitive decline associated with myoclonic jerks. |
T4 | 429-482 | Sentence | denotes | The clinical diagnosis was Creutzfeldt Jakob disease. |
T5 | 483-626 | Sentence | denotes | However, autopsy brain examination revealed changes of Kufs' disease (Adult onset neuronal ceroid lipofuscinosis, or ANCL, also known as CLN4). |
T6 | 627-825 | Sentence | denotes | No specific gross abnormalities were found but light microscopic examination revealed widespread neuronal ballooning and histochemical staining showed neuronal accumulation of PAS-positive material. |
T7 | 826-954 | Sentence | denotes | Ultrastructural examination demonstrated excessive and abnormal lipopigment lysosomes typical of neuronal ceroid lipofuscinosis. |
T8 | 955-1104 | Sentence | denotes | The typical clinical and pathologic features of the Kufs' disease are discussed and the classification of neuronal ceroid lipofuscinosis is reviewed. |
PubCasesHPO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
AB1 | 308-317 | HP:0001289 | denotes | confusion |
performance-test
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
PD-UBERON-AE-B_T1 | 67-75 | http://purl.obolibrary.org/obo/UBERON_2000602 | denotes | neuronal |
PD-UBERON-AE-B_T2 | 565-573 | http://purl.obolibrary.org/obo/UBERON_2000602 | denotes | neuronal |
PD-UBERON-AE-B_T3 | 724-732 | http://purl.obolibrary.org/obo/UBERON_2000602 | denotes | neuronal |
PD-UBERON-AE-B_T4 | 778-786 | http://purl.obolibrary.org/obo/UBERON_2000602 | denotes | neuronal |
PD-UBERON-AE-B_T5 | 923-931 | http://purl.obolibrary.org/obo/UBERON_2000602 | denotes | neuronal |
PD-UBERON-AE-B_T6 | 1061-1069 | http://purl.obolibrary.org/obo/UBERON_2000602 | denotes | neuronal |
PD-UBERON-AE-B_T7 | 500-505 | http://purl.obolibrary.org/obo/UBERON_0000955 | denotes | brain |
PubCasesORDO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
AB1 | 46-59 | ORDO:79262 | denotes | Kufs' disease |
AB2 | 61-97 | ORDO:79262 | denotes | adult neuronal ceroid lipofuscinosis |
AB3 | 538-551 | ORDO:79262 | denotes | Kufs' disease |
AB4 | 600-604 | ORDO:79262 | denotes | ANCL |
AB5 | 1007-1020 | ORDO:79262 | denotes | Kufs' disease |
UBERON-AE
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
PD-UBERON-AE-B_T1 | 500-505 | http://purl.obolibrary.org/obo/UBERON_0000955 | denotes | brain |