| Id |
Subject |
Object |
Predicate |
Lexical cue |
| T1 |
0-82 |
Sentence |
denotes |
Molecular genetics and transgenic model of Gertsmann-Sträussler-Scheinker disease. |
| T2 |
83-313 |
Sentence |
denotes |
Gerstmann-Sträussler-Scheinker disease (GSS) is a rare, dominantly inherited neurodegenerative disease that can sometimes be transmitted to experimental animals through intracerebral inoculation of brain homogenates from patients. |
| T3 |
314-485 |
Sentence |
denotes |
Substitution of leucine for proline at codon 102 of the prion protein gene has been found in several families with the disease; this mutation is genetically linked to GSS. |
| T4 |
486-689 |
Sentence |
denotes |
Mice containing murine prion protein transgenes with this mutation spontaneously develop neurologic symptoms of ataxia, lethargy, and rigidity accompanied by spongiform degeneration throughout the brain. |
| T5 |
690-970 |
Sentence |
denotes |
Thus, many of the clinical and pathological features of the GSS have been reproduced in this transgenic mouse paradigm; to our knowledge, this study illustrates, for the first time, that a neurodegenerative process similar to a human disease can be genetically modeled in animals. |
| T6 |
971-1144 |
Sentence |
denotes |
Whether or not this transgenic mouse model of GSS may facilitate the understanding of common neurodegenerative disorders such as Alzheimer disease remains to be established. |