PubMed:16781314
Annnotations
LitCoin-sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 0-136 | Sentence | denotes | Ectodermal dysplasia-skin fragility syndrome resulting from a new homozygous mutation, 888delC, in the desmosomal protein plakophilin 1. |
| T2 | 137-287 | Sentence | denotes | We report an unusual case of an inherited disorder of the desmosomal protein plakophilin 1, resulting in ectodermal dysplasia-skin fragility syndrome. |
| T3 | 288-443 | Sentence | denotes | The affected 6-year-old boy had red skin at birth and subsequently developed skin fragility, progressive plantar keratoderma, nail dystrophy, and alopecia. |
| T4 | 444-571 | Sentence | denotes | Skin biopsy revealed widening of intercellular spaces in the epidermis and a reduced number of small, poorly formed desmosomes. |
| T5 | 572-689 | Sentence | denotes | Mutation analysis of the plakophilin 1 gene PKP1 revealed a homozygous deletion of C at nucleotide 888 within exon 5. |
| T6 | 690-818 | Sentence | denotes | This mutation differs from the PKP1 gene pathology reported in 8 previously published individuals with this rare genodermatosis. |
| T7 | 819-1043 | Sentence | denotes | However, all cases show similar clinical features, highlighting the importance of functional plakophilin 1 in maintaining desmosomal adhesion in skin, as well as the role of this protein in aspects of ectodermal development. |
LitCoin-entities
| Id | Subject | Object | Predicate | Lexical cue | db_id |
|---|---|---|---|---|---|
| 3016 | 0-44 | DiseaseOrPhenotypicFeature | denotes | Ectodermal dysplasia-skin fragility syndrome | MESH:C536183 |
| 3017 | 87-94 | SequenceVariant | denotes | 888delC | c|DEL888|C |
| 3018 | 122-135 | GeneOrGeneProduct | denotes | plakophilin 1 | NCBIGene:5317 |
| 3019 | 169-187 | DiseaseOrPhenotypicFeature | denotes | inherited disorder | MESH:D030342 |
| 3020 | 214-227 | GeneOrGeneProduct | denotes | plakophilin 1 | NCBIGene:5317 |
| 3021 | 242-286 | DiseaseOrPhenotypicFeature | denotes | ectodermal dysplasia-skin fragility syndrome | MESH:C536183 |
| 3022 | 365-379 | DiseaseOrPhenotypicFeature | denotes | skin fragility | MESH:C536183 |
| 3023 | 393-412 | DiseaseOrPhenotypicFeature | denotes | plantar keratoderma | MESH:D017499 |
| 3024 | 414-428 | DiseaseOrPhenotypicFeature | denotes | nail dystrophy | MESH:D009260 |
| 3025 | 434-442 | DiseaseOrPhenotypicFeature | denotes | alopecia | MESH:D000505 |
| 3026 | 597-610 | GeneOrGeneProduct | denotes | plakophilin 1 | NCBIGene:5317 |
| 3027 | 616-620 | GeneOrGeneProduct | denotes | PKP1 | NCBIGene:5317 |
| 3028 | 643-674 | SequenceVariant | denotes | deletion of C at nucleotide 888 | c|DEL888|C |
| 3029 | 721-725 | GeneOrGeneProduct | denotes | PKP1 | NCBIGene:5317 |
| 3030 | 803-817 | DiseaseOrPhenotypicFeature | denotes | genodermatosis | MESH:D012873 |
| 3031 | 912-925 | GeneOrGeneProduct | denotes | plakophilin 1 | NCBIGene:5317 |
LitCoin_Mondo
| Id | Subject | Object | Predicate | Lexical cue | mondo_id |
|---|---|---|---|---|---|
| T1 | 169-178 | DiseaseOrPhenotypicFeature | denotes | inherited | 0021152 |
| T2 | 434-442 | DiseaseOrPhenotypicFeature | denotes | alopecia | 0004907 |
| T3 | 798-802 | DiseaseOrPhenotypicFeature | denotes | rare | 0021136 |
LitCoin-SeqVar
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 87-94 | SequenceVariant | denotes | 888delC |
| T2 | 643-656 | SequenceVariant | denotes | deletion of C |
LitCoin-GeneOrGeneProduct-v0
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 0-10 | GeneOrGeneProduct | denotes | Ectodermal |
| T2 | 21-25 | GeneOrGeneProduct | denotes | skin |
| T3 | 36-44 | GeneOrGeneProduct | denotes | syndrome |
| T4 | 77-85 | GeneOrGeneProduct | denotes | mutation |
| T5 | 114-121 | GeneOrGeneProduct | denotes | protein |
| T6 | 122-135 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T7 | 158-162 | GeneOrGeneProduct | denotes | case |
| T8 | 206-213 | GeneOrGeneProduct | denotes | protein |
| T9 | 214-227 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T10 | 242-252 | GeneOrGeneProduct | denotes | ectodermal |
| T11 | 263-267 | GeneOrGeneProduct | denotes | skin |
| T12 | 278-286 | GeneOrGeneProduct | denotes | syndrome |
| T13 | 303-307 | GeneOrGeneProduct | denotes | year |
| T14 | 320-323 | GeneOrGeneProduct | denotes | red |
| T15 | 324-328 | GeneOrGeneProduct | denotes | skin |
| T16 | 365-369 | GeneOrGeneProduct | denotes | skin |
| T17 | 414-418 | GeneOrGeneProduct | denotes | nail |
| T18 | 434-442 | GeneOrGeneProduct | denotes | alopecia |
| T19 | 444-448 | GeneOrGeneProduct | denotes | Skin |
| T20 | 521-528 | GeneOrGeneProduct | denotes | reduced |
| T21 | 539-544 | GeneOrGeneProduct | denotes | small |
| T22 | 572-580 | GeneOrGeneProduct | denotes | Mutation |
| T23 | 597-610 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T24 | 616-620 | GeneOrGeneProduct | denotes | PKP1 |
| T25 | 695-703 | GeneOrGeneProduct | denotes | mutation |
| T26 | 721-725 | GeneOrGeneProduct | denotes | PKP1 |
| T27 | 750-754 | GeneOrGeneProduct | denotes | in 8 |
| T28 | 798-802 | GeneOrGeneProduct | denotes | rare |
| T29 | 828-831 | GeneOrGeneProduct | denotes | all |
| T30 | 832-837 | GeneOrGeneProduct | denotes | cases |
| T31 | 843-850 | GeneOrGeneProduct | denotes | similar |
| T32 | 912-925 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T33 | 952-960 | GeneOrGeneProduct | denotes | adhesion |
| T34 | 964-968 | GeneOrGeneProduct | denotes | skin |
| T35 | 998-1005 | GeneOrGeneProduct | denotes | protein |
| T36 | 1020-1030 | GeneOrGeneProduct | denotes | ectodermal |
LitCoin-GeneOrGeneProduct-v2
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 0-10 | GeneOrGeneProduct | denotes | Ectodermal |
| T2 | 36-44 | GeneOrGeneProduct | denotes | syndrome |
| T3 | 114-121 | GeneOrGeneProduct | denotes | protein |
| T4 | 122-135 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T5 | 206-213 | GeneOrGeneProduct | denotes | protein |
| T6 | 214-227 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T7 | 242-252 | GeneOrGeneProduct | denotes | ectodermal |
| T8 | 278-286 | GeneOrGeneProduct | denotes | syndrome |
| T9 | 434-442 | GeneOrGeneProduct | denotes | alopecia |
| T10 | 444-448 | GeneOrGeneProduct | denotes | Skin |
| T11 | 521-528 | GeneOrGeneProduct | denotes | reduced |
| T12 | 539-544 | GeneOrGeneProduct | denotes | small |
| T13 | 597-610 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T14 | 616-620 | GeneOrGeneProduct | denotes | PKP1 |
| T15 | 721-725 | GeneOrGeneProduct | denotes | PKP1 |
| T16 | 798-802 | GeneOrGeneProduct | denotes | rare |
| T17 | 843-850 | GeneOrGeneProduct | denotes | similar |
| T18 | 912-925 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T19 | 952-960 | GeneOrGeneProduct | denotes | adhesion |
| T20 | 998-1005 | GeneOrGeneProduct | denotes | protein |
| T21 | 1020-1030 | GeneOrGeneProduct | denotes | ectodermal |
LitCoin-Disease-MeSH
| Id | Subject | Object | Predicate | Lexical cue | originalLabel |
|---|---|---|---|---|---|
| T1 | 0-44 | DiseaseOrPhenotypicFeature | denotes | Ectodermal dysplasia-skin fragility syndrome | C536183 |
| T2 | 169-187 | DiseaseOrPhenotypicFeature | denotes | inherited disorder | DISEASE |
| T3 | 242-286 | DiseaseOrPhenotypicFeature | denotes | ectodermal dysplasia-skin fragility syndrome | C536183 |
| T4 | 434-442 | DiseaseOrPhenotypicFeature | denotes | alopecia | D000505 |
LitCoin-GeneOrGeneProduct-v3
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 122-135 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T2 | 214-227 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T3 | 444-448 | GeneOrGeneProduct | denotes | Skin |
| T4 | 597-610 | GeneOrGeneProduct | denotes | plakophilin 1 |
| T5 | 616-620 | GeneOrGeneProduct | denotes | PKP1 |
| T6 | 721-725 | GeneOrGeneProduct | denotes | PKP1 |
| T7 | 912-925 | GeneOrGeneProduct | denotes | plakophilin 1 |
LitCoin_Mondo_095
| Id | Subject | Object | Predicate | Lexical cue | mondo_id |
|---|---|---|---|---|---|
| T1 | 0-44 | DiseaseOrPhenotypicFeature | denotes | Ectodermal dysplasia-skin fragility syndrome | 0011472 |
| T2 | 242-286 | DiseaseOrPhenotypicFeature | denotes | ectodermal dysplasia-skin fragility syndrome | 0011472 |
| T3 | 324-328 | DiseaseOrPhenotypicFeature | denotes | skin | 0002531 |
| T4 | 365-369 | DiseaseOrPhenotypicFeature | denotes | skin | 0002531 |
| T5 | 401-412 | DiseaseOrPhenotypicFeature | denotes | keratoderma | 0006566 |
| T6 | 434-442 | DiseaseOrPhenotypicFeature | denotes | alopecia | 0004907 |
| T7 | 803-817 | DiseaseOrPhenotypicFeature | denotes | genodermatosis | 0024255 |
| T8 | 964-968 | DiseaseOrPhenotypicFeature | denotes | skin | 0002531 |
LitCoin-MeSH-Disease-2
| Id | Subject | Object | Predicate | Lexical cue | ID: |
|---|---|---|---|---|---|
| T1 | 0-44 | DiseaseOrPhenotypicFeature | denotes | Ectodermal dysplasia-skin fragility syndrome | C536183 |
| T2 | 169-187 | DiseaseOrPhenotypicFeature | denotes | inherited disorder | DISEASE |
| T3 | 242-286 | DiseaseOrPhenotypicFeature | denotes | ectodermal dysplasia-skin fragility syndrome | C536183 |
| T4 | 365-379 | DiseaseOrPhenotypicFeature | denotes | skin fragility | DISEASE |
| T5 | 393-412 | DiseaseOrPhenotypicFeature | denotes | plantar keratoderma | DISEASE |
| T6 | 414-428 | DiseaseOrPhenotypicFeature | denotes | nail dystrophy | DISEASE |
| T7 | 434-442 | DiseaseOrPhenotypicFeature | denotes | alopecia | D000505 |
| T8 | 803-817 | DiseaseOrPhenotypicFeature | denotes | genodermatosis | DISEASE |
LitCoin-MONDO_bioort2019
| Id | Subject | Object | Predicate | Lexical cue | #label |
|---|---|---|---|---|---|
| T1 | 0-44 | DiseaseOrPhenotypicFeature | denotes | Ectodermal dysplasia-skin fragility syndrome | C536183 |
| T2 | 169-187 | DiseaseOrPhenotypicFeature | denotes | inherited disorder | DISEASE |
| T3 | 242-286 | DiseaseOrPhenotypicFeature | denotes | ectodermal dysplasia-skin fragility syndrome | C536183 |
| T4 | 365-379 | DiseaseOrPhenotypicFeature | denotes | skin fragility | DISEASE |
| T5 | 393-412 | DiseaseOrPhenotypicFeature | denotes | plantar keratoderma | DISEASE |
| T6 | 414-428 | DiseaseOrPhenotypicFeature | denotes | nail dystrophy | DISEASE |
| T7 | 434-442 | DiseaseOrPhenotypicFeature | denotes | alopecia | D000505 |
| T8 | 803-817 | DiseaseOrPhenotypicFeature | denotes | genodermatosis | DISEASE |
LitCoin-training-merged
| Id | Subject | Object | Predicate | Lexical cue | #label |
|---|---|---|---|---|---|
| T7 | 912-925 | GeneOrGeneProduct | denotes | plakophilin 1 | |
| T6 | 721-725 | GeneOrGeneProduct | denotes | PKP1 | |
| T5 | 616-620 | GeneOrGeneProduct | denotes | PKP1 | |
| T4 | 597-610 | GeneOrGeneProduct | denotes | plakophilin 1 | |
| T3 | 444-448 | GeneOrGeneProduct | denotes | Skin | |
| T2 | 214-227 | GeneOrGeneProduct | denotes | plakophilin 1 | |
| T1 | 122-135 | GeneOrGeneProduct | denotes | plakophilin 1 | |
| T8 | 803-817 | DiseaseOrPhenotypicFeature | denotes | genodermatosis | DISEASE |
| T98095 | 434-442 | DiseaseOrPhenotypicFeature | denotes | alopecia | D000505 |
| T11431 | 414-428 | DiseaseOrPhenotypicFeature | denotes | nail dystrophy | DISEASE |
| T73192 | 393-412 | DiseaseOrPhenotypicFeature | denotes | plantar keratoderma | DISEASE |
| T95371 | 365-379 | DiseaseOrPhenotypicFeature | denotes | skin fragility | DISEASE |
| T32858 | 242-286 | DiseaseOrPhenotypicFeature | denotes | ectodermal dysplasia-skin fragility syndrome | C536183 |
| T3596 | 169-187 | DiseaseOrPhenotypicFeature | denotes | inherited disorder | DISEASE |
| T73070 | 0-44 | DiseaseOrPhenotypicFeature | denotes | Ectodermal dysplasia-skin fragility syndrome | C536183 |
| T20656 | 643-656 | SequenceVariant | denotes | deletion of C | |
| T254 | 87-94 | SequenceVariant | denotes | 888delC |
sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TextSentencer_T1 | 0-136 | Sentence | denotes | Ectodermal dysplasia-skin fragility syndrome resulting from a new homozygous mutation, 888delC, in the desmosomal protein plakophilin 1. |
| TextSentencer_T2 | 137-287 | Sentence | denotes | We report an unusual case of an inherited disorder of the desmosomal protein plakophilin 1, resulting in ectodermal dysplasia-skin fragility syndrome. |
| TextSentencer_T3 | 288-443 | Sentence | denotes | The affected 6-year-old boy had red skin at birth and subsequently developed skin fragility, progressive plantar keratoderma, nail dystrophy, and alopecia. |
| TextSentencer_T4 | 444-571 | Sentence | denotes | Skin biopsy revealed widening of intercellular spaces in the epidermis and a reduced number of small, poorly formed desmosomes. |
| TextSentencer_T5 | 572-689 | Sentence | denotes | Mutation analysis of the plakophilin 1 gene PKP1 revealed a homozygous deletion of C at nucleotide 888 within exon 5. |
| TextSentencer_T6 | 690-818 | Sentence | denotes | This mutation differs from the PKP1 gene pathology reported in 8 previously published individuals with this rare genodermatosis. |
| TextSentencer_T7 | 819-1043 | Sentence | denotes | However, all cases show similar clinical features, highlighting the importance of functional plakophilin 1 in maintaining desmosomal adhesion in skin, as well as the role of this protein in aspects of ectodermal development. |
| T1 | 0-136 | Sentence | denotes | Ectodermal dysplasia-skin fragility syndrome resulting from a new homozygous mutation, 888delC, in the desmosomal protein plakophilin 1. |
| T2 | 137-287 | Sentence | denotes | We report an unusual case of an inherited disorder of the desmosomal protein plakophilin 1, resulting in ectodermal dysplasia-skin fragility syndrome. |
| T3 | 288-443 | Sentence | denotes | The affected 6-year-old boy had red skin at birth and subsequently developed skin fragility, progressive plantar keratoderma, nail dystrophy, and alopecia. |
| T4 | 444-571 | Sentence | denotes | Skin biopsy revealed widening of intercellular spaces in the epidermis and a reduced number of small, poorly formed desmosomes. |
| T5 | 572-689 | Sentence | denotes | Mutation analysis of the plakophilin 1 gene PKP1 revealed a homozygous deletion of C at nucleotide 888 within exon 5. |
| T6 | 690-818 | Sentence | denotes | This mutation differs from the PKP1 gene pathology reported in 8 previously published individuals with this rare genodermatosis. |
| T7 | 819-1043 | Sentence | denotes | However, all cases show similar clinical features, highlighting the importance of functional plakophilin 1 in maintaining desmosomal adhesion in skin, as well as the role of this protein in aspects of ectodermal development. |
PubmedHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 242-262 | HP_0000968 | denotes | ectodermal dysplasia |
| T2 | 263-277 | HP_0001030 | denotes | skin fragility |
| T3 | 365-379 | HP_0001030 | denotes | skin fragility |
| T4 | 414-428 | HP_0008404 | denotes | nail dystrophy |
| T5 | 434-442 | HP_0001596 | denotes | alopecia |
DisGeNET5_gene_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 16781314-1#77#90#gene5317 | 214-227 | gene5317 | denotes | plakophilin 1 |
| 16781314-1#105#149#diseaseC1858302 | 242-286 | diseaseC1858302 | denotes | ectodermal dysplasia-skin fragility syndrome |
| 16781314-5#31#35#gene5317 | 721-725 | gene5317 | denotes | PKP1 |
| 16781314-5#113#127#diseaseC0037277 | 803-817 | diseaseC0037277 | denotes | genodermatosis |
| 77#90#gene5317105#149#diseaseC1858302 | 16781314-1#77#90#gene5317 | 16781314-1#105#149#diseaseC1858302 | associated_with | plakophilin 1,ectodermal dysplasia-skin fragility syndrome |
| 31#35#gene5317113#127#diseaseC0037277 | 16781314-5#31#35#gene5317 | 16781314-5#113#127#diseaseC0037277 | associated_with | PKP1,genodermatosis |
PubCasesHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TI1 | 0-20 | HP:0000968 | denotes | Ectodermal dysplasia |
| AB1 | 242-262 | HP:0000968 | denotes | ectodermal dysplasia |
| AB2 | 414-428 | HP:0008404 | denotes | nail dystrophy |
| AB3 | 434-442 | HP:0001596 | denotes | alopecia |
PubCasesORDO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TI1 | 0-44 | ORDO:158668 | denotes | Ectodermal dysplasia-skin fragility syndrome |
| AB1 | 242-286 | ORDO:158668 | denotes | ectodermal dysplasia-skin fragility syndrome |
performance-test
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| PD-UBERON-AE-B_T1 | 414-418 | http://purl.obolibrary.org/obo/UBERON_0001705 | denotes | nail |
| PD-UBERON-AE-B_T2 | 0-10 | http://purl.obolibrary.org/obo/UBERON_0000924 | denotes | Ectodermal |
| PD-UBERON-AE-B_T3 | 242-252 | http://purl.obolibrary.org/obo/UBERON_0000924 | denotes | ectodermal |
| PD-UBERON-AE-B_T4 | 1020-1030 | http://purl.obolibrary.org/obo/UBERON_0000924 | denotes | ectodermal |
tmVarCorpus
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 87-94 | DNAMutation:|DEL|888|C | denotes | 888delC |
DisGeNET
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T0 | 214-227 | gene:5317 | denotes | plakophilin 1 |
| T1 | 242-286 | disease:C1858302 | denotes | ectodermal dysplasia-skin fragility syndrome |
| T2 | 721-725 | gene:5317 | denotes | PKP1 |
| T3 | 803-817 | disease:C0037277 | denotes | genodermatosis |
| R1 | T0 | T1 | associated_with | plakophilin 1,ectodermal dysplasia-skin fragility syndrome |
| R2 | T2 | T3 | associated_with | PKP1,genodermatosis |