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PubMed:16412238
Annnotations
LitCoin-entities-OrganismTaxon-PD
Id | Subject | Object | Predicate | Lexical cue | db_id |
---|---|---|---|---|---|
T1 | 1222-1227 | OrganismTaxon | denotes | human | NCBItxid:9606 |
LitCoin-sentences
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 0-134 | Sentence | denotes | Peroxisomal proliferator activated receptor-gamma deficiency in a Canadian kindred with familial partial lipodystrophy type 3 (FPLD3). |
T2 | 135-146 | Sentence | denotes | BACKGROUND: |
T3 | 147-351 | Sentence | denotes | Familial partial lipodystrophy (Dunnigan) type 3 (FPLD3, Mendelian Inheritance in Man [MIM] 604367) results from heterozygous mutations in PPARG encoding peroxisomal proliferator-activated receptor-gamma. |
T4 | 352-448 | Sentence | denotes | Both dominant-negative and haploinsufficiency mechanisms have been suggested for this condition. |
T5 | 449-457 | Sentence | denotes | METHODS: |
T6 | 458-620 | Sentence | denotes | We present a Canadian FPLD3 kindred with an affected mother who had loss of fat on arms and legs, but no increase in facial, neck, suprascapular or abdominal fat. |
T7 | 621-884 | Sentence | denotes | She had profound insulin resistance, diabetes, severe hypertriglyceridemia and relapsing pancreatitis, while her pre-pubescent daughter had normal fat distribution but elevated plasma triglycerides and C-peptide and depressed high-density lipoprotein cholesterol. |
T8 | 885-893 | Sentence | denotes | RESULTS: |
T9 | 894-1104 | Sentence | denotes | The mother and daughter were each heterozygous for PPARG nonsense mutation Y355X, whose protein product in vitro was transcriptionally inactive with no dominant-negative activity against the wild-type receptor. |
T10 | 1105-1169 | Sentence | denotes | In addition the mutant protein appeared to be markedly unstable. |
T11 | 1170-1181 | Sentence | denotes | CONCLUSION: |
T12 | 1182-1481 | Sentence | denotes | Taken together with previous studies of human PPARG mutations, these findings suggest that PPAR-gamma deficiency due either to haploinsufficiency or to substantial activity loss due to dominant negative interference of the normal allele product's function can each contribute to the FPLD3 phenotype. |
LitCoin-entities
Id | Subject | Object | Predicate | Lexical cue | db_id |
---|---|---|---|---|---|
2735 | 0-49 | GeneOrGeneProduct | denotes | Peroxisomal proliferator activated receptor-gamma | NCBIGene:5468 |
2736 | 88-125 | DiseaseOrPhenotypicFeature | denotes | familial partial lipodystrophy type 3 | MESH:D052496 |
2737 | 127-132 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | MESH:D052496 |
2738 | 147-195 | DiseaseOrPhenotypicFeature | denotes | Familial partial lipodystrophy (Dunnigan) type 3 | MESH:D052496 |
2739 | 197-202 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | MESH:D052496 |
2740 | 204-245 | DiseaseOrPhenotypicFeature | denotes | Mendelian Inheritance in Man [MIM] 604367 | MESH:D052496 |
2741 | 286-291 | GeneOrGeneProduct | denotes | PPARG | NCBIGene:5468 |
2742 | 301-350 | GeneOrGeneProduct | denotes | peroxisomal proliferator-activated receptor-gamma | NCBIGene:5468 |
2743 | 480-485 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | MESH:D052496 |
2744 | 638-656 | DiseaseOrPhenotypicFeature | denotes | insulin resistance | MESH:D007333 |
2745 | 658-666 | DiseaseOrPhenotypicFeature | denotes | diabetes | MESH:D003920 |
2746 | 675-695 | DiseaseOrPhenotypicFeature | denotes | hypertriglyceridemia | MESH:D015228 |
2747 | 710-722 | DiseaseOrPhenotypicFeature | denotes | pancreatitis | MESH:D010195 |
2748 | 805-818 | ChemicalEntity | denotes | triglycerides | MESH:D014280 |
2749 | 823-832 | ChemicalEntity | denotes | C-peptide | MESH:D002096 |
2750 | 847-883 | ChemicalEntity | denotes | high-density lipoprotein cholesterol | MESH:D008076 |
2751 | 945-950 | GeneOrGeneProduct | denotes | PPARG | NCBIGene:5468 |
2752 | 969-974 | SequenceVariant | denotes | Y355X | p|SUB|Y|355|X |
2753 | 1222-1227 | OrganismTaxon | denotes | human | NCBITaxon:9606 |
2754 | 1228-1233 | GeneOrGeneProduct | denotes | PPARG | NCBIGene:5468 |
2755 | 1273-1283 | GeneOrGeneProduct | denotes | PPAR-gamma | NCBIGene:5468 |
2756 | 1465-1470 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | MESH:D052496 |
LitCoin_Mondo
Id | Subject | Object | Predicate | Lexical cue | mondo_id |
---|---|---|---|---|---|
T1 | 88-118 | DiseaseOrPhenotypicFeature | denotes | familial partial lipodystrophy | 0020088 |
T2 | 97-118 | DiseaseOrPhenotypicFeature | denotes | partial lipodystrophy | 0027767 |
T3 | 105-118 | DiseaseOrPhenotypicFeature | denotes | lipodystrophy | 0006573 |
T4 | 147-193 | DiseaseOrPhenotypicFeature | denotes | Familial partial lipodystrophy (Dunnigan) type | 0007906 |
T5 | 147-177 | DiseaseOrPhenotypicFeature | denotes | Familial partial lipodystrophy | 0020088 |
T6 | 156-177 | DiseaseOrPhenotypicFeature | denotes | partial lipodystrophy | 0027767 |
T7 | 164-177 | DiseaseOrPhenotypicFeature | denotes | lipodystrophy | 0006573 |
T8 | 214-225 | DiseaseOrPhenotypicFeature | denotes | Inheritance | 0021152 |
T9 | 675-695 | DiseaseOrPhenotypicFeature | denotes | hypertriglyceridemia | 0005347 |
T10 | 710-722 | DiseaseOrPhenotypicFeature | denotes | pancreatitis | 0004982 |
LitCoin-SeqVar
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 969-974 | SequenceVariant | denotes | Y355X |
LitCoin-GeneOrGeneProduct-v2
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 35-43 | GeneOrGeneProduct | denotes | receptor |
T2 | 44-49 | GeneOrGeneProduct | denotes | gamma |
T3 | 286-291 | GeneOrGeneProduct | denotes | PPARG |
T4 | 301-344 | GeneOrGeneProduct | denotes | peroxisomal proliferator-activated receptor |
T5 | 345-350 | GeneOrGeneProduct | denotes | gamma |
T6 | 606-615 | GeneOrGeneProduct | denotes | abdominal |
T7 | 638-645 | GeneOrGeneProduct | denotes | insulin |
T8 | 658-666 | GeneOrGeneProduct | denotes | diabetes |
T9 | 738-747 | GeneOrGeneProduct | denotes | pubescent |
T10 | 768-784 | GeneOrGeneProduct | denotes | fat distribution |
T11 | 805-818 | GeneOrGeneProduct | denotes | triglycerides |
T12 | 823-832 | GeneOrGeneProduct | denotes | C-peptide |
T13 | 837-846 | GeneOrGeneProduct | denotes | depressed |
T14 | 847-851 | GeneOrGeneProduct | denotes | high |
T15 | 860-871 | GeneOrGeneProduct | denotes | lipoprotein |
T16 | 945-950 | GeneOrGeneProduct | denotes | PPARG |
T17 | 982-989 | GeneOrGeneProduct | denotes | protein |
T18 | 990-997 | GeneOrGeneProduct | denotes | product |
T19 | 1011-1028 | GeneOrGeneProduct | denotes | transcriptionally |
T20 | 1029-1037 | GeneOrGeneProduct | denotes | inactive |
T21 | 1095-1103 | GeneOrGeneProduct | denotes | receptor |
T22 | 1121-1127 | GeneOrGeneProduct | denotes | mutant |
T23 | 1128-1135 | GeneOrGeneProduct | denotes | protein |
T24 | 1228-1233 | GeneOrGeneProduct | denotes | PPARG |
T25 | 1273-1283 | GeneOrGeneProduct | denotes | PPAR-gamma |
LitCoin-GeneOrGeneProduct-v0
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 35-43 | GeneOrGeneProduct | denotes | receptor |
T2 | 44-49 | GeneOrGeneProduct | denotes | gamma |
T3 | 61-65 | GeneOrGeneProduct | denotes | in a |
T4 | 273-282 | GeneOrGeneProduct | denotes | mutations |
T5 | 286-291 | GeneOrGeneProduct | denotes | PPARG |
T6 | 301-344 | GeneOrGeneProduct | denotes | peroxisomal proliferator-activated receptor |
T7 | 345-350 | GeneOrGeneProduct | denotes | gamma |
T8 | 379-397 | GeneOrGeneProduct | denotes | haploinsufficiency |
T9 | 449-456 | GeneOrGeneProduct | denotes | METHODS |
T10 | 541-545 | GeneOrGeneProduct | denotes | arms |
T11 | 606-615 | GeneOrGeneProduct | denotes | abdominal |
T12 | 638-645 | GeneOrGeneProduct | denotes | insulin |
T13 | 658-666 | GeneOrGeneProduct | denotes | diabetes |
T14 | 738-747 | GeneOrGeneProduct | denotes | pubescent |
T15 | 768-784 | GeneOrGeneProduct | denotes | fat distribution |
T16 | 805-818 | GeneOrGeneProduct | denotes | triglycerides |
T17 | 823-832 | GeneOrGeneProduct | denotes | C-peptide |
T18 | 837-846 | GeneOrGeneProduct | denotes | depressed |
T19 | 847-851 | GeneOrGeneProduct | denotes | high |
T20 | 860-871 | GeneOrGeneProduct | denotes | lipoprotein |
T21 | 945-950 | GeneOrGeneProduct | denotes | PPARG |
T22 | 960-968 | GeneOrGeneProduct | denotes | mutation |
T23 | 982-989 | GeneOrGeneProduct | denotes | protein |
T24 | 990-997 | GeneOrGeneProduct | denotes | product |
T25 | 1011-1028 | GeneOrGeneProduct | denotes | transcriptionally |
T26 | 1029-1037 | GeneOrGeneProduct | denotes | inactive |
T27 | 1064-1072 | GeneOrGeneProduct | denotes | activity |
T28 | 1095-1103 | GeneOrGeneProduct | denotes | receptor |
T29 | 1121-1127 | GeneOrGeneProduct | denotes | mutant |
T30 | 1128-1135 | GeneOrGeneProduct | denotes | protein |
T31 | 1151-1159 | GeneOrGeneProduct | denotes | markedly |
T32 | 1228-1233 | GeneOrGeneProduct | denotes | PPARG |
T33 | 1234-1243 | GeneOrGeneProduct | denotes | mutations |
T34 | 1251-1259 | GeneOrGeneProduct | denotes | findings |
T35 | 1273-1283 | GeneOrGeneProduct | denotes | PPAR-gamma |
T36 | 1309-1327 | GeneOrGeneProduct | denotes | haploinsufficiency |
T37 | 1346-1354 | GeneOrGeneProduct | denotes | activity |
T38 | 1419-1428 | GeneOrGeneProduct | denotes | product's |
LitCoin-Disease-MeSH
Id | Subject | Object | Predicate | Lexical cue | originalLabel |
---|---|---|---|---|---|
T1 | 88-118 | DiseaseOrPhenotypicFeature | denotes | familial partial lipodystrophy | D052496 |
T2 | 147-177 | DiseaseOrPhenotypicFeature | denotes | Familial partial lipodystrophy | D052496 |
T3 | 638-656 | DiseaseOrPhenotypicFeature | denotes | insulin resistance | D007333 |
T4 | 658-666 | DiseaseOrPhenotypicFeature | denotes | diabetes | DISEASE |
T5 | 675-695 | DiseaseOrPhenotypicFeature | denotes | hypertriglyceridemia | D015228 |
T6 | 710-722 | DiseaseOrPhenotypicFeature | denotes | pancreatitis | D010195 |
T7 | 837-846 | DiseaseOrPhenotypicFeature | denotes | depressed | DISEASE |
LitCoin-GeneOrGeneProduct-v3
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 12-49 | GeneOrGeneProduct | denotes | proliferator activated receptor-gamma |
T2 | 286-291 | GeneOrGeneProduct | denotes | PPARG |
T3 | 301-344 | GeneOrGeneProduct | denotes | peroxisomal proliferator-activated receptor |
T4 | 738-747 | GeneOrGeneProduct | denotes | pubescent |
T5 | 768-784 | GeneOrGeneProduct | denotes | fat distribution |
T6 | 847-871 | GeneOrGeneProduct | denotes | high-density lipoprotein |
T7 | 945-950 | GeneOrGeneProduct | denotes | PPARG |
T8 | 1228-1233 | GeneOrGeneProduct | denotes | PPARG |
T9 | 1273-1283 | GeneOrGeneProduct | denotes | PPAR-gamma |
LitCoin_Mondo_095
Id | Subject | Object | Predicate | Lexical cue | mondo_id |
---|---|---|---|---|---|
T1 | 88-125 | DiseaseOrPhenotypicFeature | denotes | familial partial lipodystrophy type 3 | 0011448 |
T2 | 127-132 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | 0011448 |
T3 | 147-193 | DiseaseOrPhenotypicFeature | denotes | Familial partial lipodystrophy (Dunnigan) type | 0007906 |
T4 | 197-202 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | 0011448 |
T5 | 480-485 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | 0011448 |
T6 | 541-545 | DiseaseOrPhenotypicFeature | denotes | arms | 0009994 |
T7 | 658-666 | DiseaseOrPhenotypicFeature | denotes | diabetes | 0005015 |
T8 | 675-695 | DiseaseOrPhenotypicFeature | denotes | hypertriglyceridemia | 0005347 |
T9 | 710-722 | DiseaseOrPhenotypicFeature | denotes | pancreatitis | 0004982 |
T10 | 1438-1441 | DiseaseOrPhenotypicFeature | denotes | can | 0012833 |
T11 | 1465-1470 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | 0011448 |
LitCoin-MeSH-Disease-2
Id | Subject | Object | Predicate | Lexical cue | ID: |
---|---|---|---|---|---|
T1 | 88-118 | DiseaseOrPhenotypicFeature | denotes | familial partial lipodystrophy | D052496 |
T2 | 127-132 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE |
T3 | 147-195 | DiseaseOrPhenotypicFeature | denotes | Familial partial lipodystrophy (Dunnigan) type 3 | DISEASE |
T4 | 197-202 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE |
T5 | 204-245 | DiseaseOrPhenotypicFeature | denotes | Mendelian Inheritance in Man [MIM] 604367 | DISEASE |
T6 | 480-485 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE |
T7 | 638-656 | DiseaseOrPhenotypicFeature | denotes | insulin resistance | D007333 |
T8 | 658-666 | DiseaseOrPhenotypicFeature | denotes | diabetes | DISEASE |
T9 | 675-695 | DiseaseOrPhenotypicFeature | denotes | hypertriglyceridemia | D015228 |
T10 | 710-722 | DiseaseOrPhenotypicFeature | denotes | pancreatitis | D010195 |
T11 | 837-846 | DiseaseOrPhenotypicFeature | denotes | depressed | DISEASE |
T12 | 1465-1470 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE |
LitCoin-MONDO_bioort2019
Id | Subject | Object | Predicate | Lexical cue | #label |
---|---|---|---|---|---|
T1 | 88-118 | DiseaseOrPhenotypicFeature | denotes | familial partial lipodystrophy | D052496 |
T2 | 127-132 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE |
T3 | 147-195 | DiseaseOrPhenotypicFeature | denotes | Familial partial lipodystrophy (Dunnigan) type 3 | DISEASE |
T4 | 197-202 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE |
T5 | 204-245 | DiseaseOrPhenotypicFeature | denotes | Mendelian Inheritance in Man [MIM] 604367 | DISEASE |
T6 | 480-485 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE |
T7 | 638-656 | DiseaseOrPhenotypicFeature | denotes | insulin resistance | D007333 |
T8 | 658-666 | DiseaseOrPhenotypicFeature | denotes | diabetes | DISEASE |
T9 | 675-695 | DiseaseOrPhenotypicFeature | denotes | hypertriglyceridemia | D015228 |
T10 | 710-722 | DiseaseOrPhenotypicFeature | denotes | pancreatitis | D010195 |
T11 | 837-846 | DiseaseOrPhenotypicFeature | denotes | depressed | DISEASE |
T12 | 1465-1470 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE |
LitCoin-Chemical-MeSH-CHEBI
Id | Subject | Object | Predicate | Lexical cue | ID: |
---|---|---|---|---|---|
T1 | 229-232 | ChemicalEntity | denotes | Man | http://purl.obolibrary.org/obo/CHEBI_37684 |
T2 | 805-818 | ChemicalEntity | denotes | triglycerides | D014280|http://purl.obolibrary.org/obo/CHEBI_17855 |
T4 | 823-832 | ChemicalEntity | denotes | C-peptide | http://purl.obolibrary.org/obo/CHEBI_80332 |
T5 | 847-883 | ChemicalEntity | denotes | high-density lipoprotein cholesterol | http://purl.obolibrary.org/obo/CHEBI_47775 |
LitCoin-NCBITaxon-2
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 229-232 | OrganismTaxon | denotes | Man |
T2 | 1222-1227 | OrganismTaxon | denotes | human |
LitCoin-training-merged
Id | Subject | Object | Predicate | Lexical cue | #label | ID: |
---|---|---|---|---|---|---|
T5 | 847-883 | ChemicalEntity | denotes | high-density lipoprotein cholesterol | http://purl.obolibrary.org/obo/CHEBI_47775 | |
T4 | 823-832 | ChemicalEntity | denotes | C-peptide | http://purl.obolibrary.org/obo/CHEBI_80332 | |
T2 | 805-818 | ChemicalEntity | denotes | triglycerides | http://purl.obolibrary.org/obo/CHEBI_17855|D014280 | |
T1 | 229-232 | ChemicalEntity | denotes | Man | http://purl.obolibrary.org/obo/CHEBI_37684 | |
T9 | 1273-1283 | GeneOrGeneProduct | denotes | PPAR-gamma | ||
T8 | 1228-1233 | GeneOrGeneProduct | denotes | PPARG | ||
T7 | 945-950 | GeneOrGeneProduct | denotes | PPARG | ||
T6 | 847-871 | GeneOrGeneProduct | denotes | high-density lipoprotein | ||
T90017 | 768-784 | GeneOrGeneProduct | denotes | fat distribution | ||
T36090 | 738-747 | GeneOrGeneProduct | denotes | pubescent | ||
T3 | 301-344 | GeneOrGeneProduct | denotes | peroxisomal proliferator-activated receptor | ||
T52161 | 286-291 | GeneOrGeneProduct | denotes | PPARG | ||
T80883 | 12-49 | GeneOrGeneProduct | denotes | proliferator activated receptor-gamma | ||
T12 | 1465-1470 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE | |
T11 | 837-846 | DiseaseOrPhenotypicFeature | denotes | depressed | DISEASE | |
T10 | 710-722 | DiseaseOrPhenotypicFeature | denotes | pancreatitis | D010195 | |
T42321 | 675-695 | DiseaseOrPhenotypicFeature | denotes | hypertriglyceridemia | D015228 | |
T17898 | 658-666 | DiseaseOrPhenotypicFeature | denotes | diabetes | DISEASE | |
T81558 | 638-656 | DiseaseOrPhenotypicFeature | denotes | insulin resistance | D007333 | |
T54232 | 480-485 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE | |
T88457 | 204-245 | DiseaseOrPhenotypicFeature | denotes | Mendelian Inheritance in Man [MIM] 604367 | DISEASE | |
T49623 | 197-202 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE | |
T48326 | 147-195 | DiseaseOrPhenotypicFeature | denotes | Familial partial lipodystrophy (Dunnigan) type 3 | DISEASE | |
T91128 | 127-132 | DiseaseOrPhenotypicFeature | denotes | FPLD3 | DISEASE | |
T52704 | 88-118 | DiseaseOrPhenotypicFeature | denotes | familial partial lipodystrophy | D052496 | |
T94298 | 1222-1227 | OrganismTaxon | denotes | human | ||
T36434 | 229-232 | OrganismTaxon | denotes | Man | ||
T5420 | 969-974 | SequenceVariant | denotes | Y355X |
sentences
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
TextSentencer_T1 | 0-134 | Sentence | denotes | Peroxisomal proliferator activated receptor-gamma deficiency in a Canadian kindred with familial partial lipodystrophy type 3 (FPLD3). |
TextSentencer_T2 | 135-146 | Sentence | denotes | BACKGROUND: |
TextSentencer_T3 | 147-351 | Sentence | denotes | Familial partial lipodystrophy (Dunnigan) type 3 (FPLD3, Mendelian Inheritance in Man [MIM] 604367) results from heterozygous mutations in PPARG encoding peroxisomal proliferator-activated receptor-gamma. |
TextSentencer_T4 | 352-448 | Sentence | denotes | Both dominant-negative and haploinsufficiency mechanisms have been suggested for this condition. |
TextSentencer_T5 | 449-457 | Sentence | denotes | METHODS: |
TextSentencer_T6 | 458-620 | Sentence | denotes | We present a Canadian FPLD3 kindred with an affected mother who had loss of fat on arms and legs, but no increase in facial, neck, suprascapular or abdominal fat. |
TextSentencer_T7 | 621-884 | Sentence | denotes | She had profound insulin resistance, diabetes, severe hypertriglyceridemia and relapsing pancreatitis, while her pre-pubescent daughter had normal fat distribution but elevated plasma triglycerides and C-peptide and depressed high-density lipoprotein cholesterol. |
TextSentencer_T8 | 885-893 | Sentence | denotes | RESULTS: |
TextSentencer_T9 | 894-1104 | Sentence | denotes | The mother and daughter were each heterozygous for PPARG nonsense mutation Y355X, whose protein product in vitro was transcriptionally inactive with no dominant-negative activity against the wild-type receptor. |
TextSentencer_T10 | 1105-1169 | Sentence | denotes | In addition the mutant protein appeared to be markedly unstable. |
TextSentencer_T11 | 1170-1181 | Sentence | denotes | CONCLUSION: |
TextSentencer_T12 | 1182-1481 | Sentence | denotes | Taken together with previous studies of human PPARG mutations, these findings suggest that PPAR-gamma deficiency due either to haploinsufficiency or to substantial activity loss due to dominant negative interference of the normal allele product's function can each contribute to the FPLD3 phenotype. |
T1 | 0-134 | Sentence | denotes | Peroxisomal proliferator activated receptor-gamma deficiency in a Canadian kindred with familial partial lipodystrophy type 3 (FPLD3). |
T2 | 135-146 | Sentence | denotes | BACKGROUND: |
T3 | 147-351 | Sentence | denotes | Familial partial lipodystrophy (Dunnigan) type 3 (FPLD3, Mendelian Inheritance in Man [MIM] 604367) results from heterozygous mutations in PPARG encoding peroxisomal proliferator-activated receptor-gamma. |
T4 | 352-448 | Sentence | denotes | Both dominant-negative and haploinsufficiency mechanisms have been suggested for this condition. |
T5 | 449-457 | Sentence | denotes | METHODS: |
T6 | 458-620 | Sentence | denotes | We present a Canadian FPLD3 kindred with an affected mother who had loss of fat on arms and legs, but no increase in facial, neck, suprascapular or abdominal fat. |
T7 | 621-884 | Sentence | denotes | She had profound insulin resistance, diabetes, severe hypertriglyceridemia and relapsing pancreatitis, while her pre-pubescent daughter had normal fat distribution but elevated plasma triglycerides and C-peptide and depressed high-density lipoprotein cholesterol. |
T8 | 885-893 | Sentence | denotes | RESULTS: |
T9 | 894-1104 | Sentence | denotes | The mother and daughter were each heterozygous for PPARG nonsense mutation Y355X, whose protein product in vitro was transcriptionally inactive with no dominant-negative activity against the wild-type receptor. |
T10 | 1105-1169 | Sentence | denotes | In addition the mutant protein appeared to be markedly unstable. |
T11 | 1170-1181 | Sentence | denotes | CONCLUSION: |
T12 | 1182-1481 | Sentence | denotes | Taken together with previous studies of human PPARG mutations, these findings suggest that PPAR-gamma deficiency due either to haploinsufficiency or to substantial activity loss due to dominant negative interference of the normal allele product's function can each contribute to the FPLD3 phenotype. |
PubmedHPO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T1 | 164-177 | HP_0009125 | denotes | lipodystrophy |
DisGeNET5_gene_disease
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
16412238-7#46#51#gene5468 | 1228-1233 | gene5468 | denotes | PPARG |
16412238-7#283#288#diseaseC1720861 | 1465-1470 | diseaseC1720861 | denotes | FPLD3 |
46#51#gene5468283#288#diseaseC1720861 | 16412238-7#46#51#gene5468 | 16412238-7#283#288#diseaseC1720861 | associated_with | PPARG,FPLD3 |
PubCasesHPO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
AB1 | 164-177 | HP:0009125 | denotes | lipodystrophy |
TI1 | 105-118 | HP:0009125 | denotes | lipodystrophy |
AB2 | 638-656 | HP:0000855 | denotes | insulin resistance |
AB3 | 675-695 | HP:0002155 | denotes | hypertriglyceridemia |
AB4 | 710-722 | HP:0001733 | denotes | pancreatitis |
PubCasesORDO
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
AB1 | 147-193 | ORDO:2348 | denotes | Familial partial lipodystrophy (Dunnigan) type |
AB2 | 197-202 | ORDO:79083 | denotes | FPLD3 |
TI1 | 88-125 | ORDO:79083 | denotes | familial partial lipodystrophy type 3 |
TI2 | 127-132 | ORDO:79083 | denotes | FPLD3 |
AB3 | 480-485 | ORDO:79083 | denotes | FPLD3 |
AB4 | 1465-1470 | ORDO:79083 | denotes | FPLD3 |
performance-test
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
PD-UBERON-AE-B_T1 | 541-545 | http://purl.obolibrary.org/obo/UBERON_0001460 | denotes | arms |
PD-UBERON-AE-B_T2 | 550-554 | http://purl.obolibrary.org/obo/UBERON_0000978 | denotes | legs |
PD-UBERON-AE-B_T3 | 583-587 | http://purl.obolibrary.org/obo/UBERON_0000974 | denotes | neck |
PD-UBERON-AE-B_T4 | 589-602 | http://purl.obolibrary.org/obo/UBERON_3000748 | denotes | suprascapular |
DisGeNET
Id | Subject | Object | Predicate | Lexical cue |
---|---|---|---|---|
T0 | 286-291 | gene:5468 | denotes | PPARG |
T1 | 147-177 | disease:C0271694 | denotes | Familial partial lipodystrophy |
R1 | T0 | T1 | associated_with | PPARG,Familial partial lipodystrophy |