PubMed:10519880
Annnotations
PMID_GLOBAL
| Id | Subject | Object | Predicate | Lexical cue | mondo_id |
|---|---|---|---|---|---|
| T1 | 131-161 | DiseaseOrPhenotypicFeature | denotes | cerebrotendinous xanthomatosis | 0008948 |
| T2 | 198-228 | DiseaseOrPhenotypicFeature | denotes | cerebrotendinous xanthomatosis | 0008948 |
| T3 | 230-233 | DiseaseOrPhenotypicFeature | denotes | CTX | 0008948 |
| T4 | 1386-1389 | DiseaseOrPhenotypicFeature | denotes | can | 0012833 |
sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TextSentencer_T1 | 0-162 | Sentence | denotes | Mutation of the sterol 27-hydroxylase gene (CYP27) results in truncation of mRNA expressed in leucocytes in a Japanese family with cerebrotendinous xanthomatosis. |
| TextSentencer_T2 | 163-174 | Sentence | denotes | OBJECTIVES: |
| TextSentencer_T3 | 175-320 | Sentence | denotes | A Japanese family with cerebrotendinous xanthomatosis (CTX) was investigated for a sequence alteration in the sterol 27-hydroxylase gene (CYP27). |
| TextSentencer_T4 | 321-497 | Sentence | denotes | The expression of CYP27 has been mostly explored using cultured fibroblasts, prompting the examination of the transcripts from blood leucocytes as a simple and rapid technique. |
| TextSentencer_T5 | 498-506 | Sentence | denotes | METHODS: |
| TextSentencer_T6 | 507-677 | Sentence | denotes | An alteration in CYP27 of the proband was searched for by polymerase chain reaction-single strand conformation polymorphism (PCR-SSCP) analysis and subsequent sequencing. |
| TextSentencer_T7 | 678-825 | Sentence | denotes | Samples of RNA were subjected to reverse transcription PCR (RT-PCR) and the product of the proband was amplified with nested primers and sequenced. |
| TextSentencer_T8 | 826-834 | Sentence | denotes | RESULTS: |
| TextSentencer_T9 | 835-920 | Sentence | denotes | A homozygous G to A transition at the 5' end of intron 7 was detected in the patient. |
| TextSentencer_T10 | 921-1074 | Sentence | denotes | In RT-PCR analysis, only a truncated transcript was detected in the patient, whereas both normal and truncated transcripts were detected in the siblings. |
| TextSentencer_T11 | 1075-1172 | Sentence | denotes | The sequencing of the patient's cDNA fragment disclosed a direct conjuction of exon 6 and exon 8. |
| TextSentencer_T12 | 1173-1184 | Sentence | denotes | CONCLUSION: |
| TextSentencer_T13 | 1185-1349 | Sentence | denotes | The mutation at splice donor site and the truncation of mRNA were identical with those of a recently reported Italian patient, although different in symptomatology. |
| TextSentencer_T14 | 1350-1466 | Sentence | denotes | The application of blood leucocytes can be a simple technique on analysing a constructive abnormality of CYP27 mRNA. |
| T1 | 0-162 | Sentence | denotes | Mutation of the sterol 27-hydroxylase gene (CYP27) results in truncation of mRNA expressed in leucocytes in a Japanese family with cerebrotendinous xanthomatosis. |
| T2 | 163-174 | Sentence | denotes | OBJECTIVES: |
| T3 | 175-320 | Sentence | denotes | A Japanese family with cerebrotendinous xanthomatosis (CTX) was investigated for a sequence alteration in the sterol 27-hydroxylase gene (CYP27). |
| T4 | 321-497 | Sentence | denotes | The expression of CYP27 has been mostly explored using cultured fibroblasts, prompting the examination of the transcripts from blood leucocytes as a simple and rapid technique. |
| T5 | 498-506 | Sentence | denotes | METHODS: |
| T6 | 507-677 | Sentence | denotes | An alteration in CYP27 of the proband was searched for by polymerase chain reaction-single strand conformation polymorphism (PCR-SSCP) analysis and subsequent sequencing. |
| T7 | 678-825 | Sentence | denotes | Samples of RNA were subjected to reverse transcription PCR (RT-PCR) and the product of the proband was amplified with nested primers and sequenced. |
| T8 | 826-834 | Sentence | denotes | RESULTS: |
| T9 | 835-920 | Sentence | denotes | A homozygous G to A transition at the 5' end of intron 7 was detected in the patient. |
| T10 | 921-1074 | Sentence | denotes | In RT-PCR analysis, only a truncated transcript was detected in the patient, whereas both normal and truncated transcripts were detected in the siblings. |
| T11 | 1075-1172 | Sentence | denotes | The sequencing of the patient's cDNA fragment disclosed a direct conjuction of exon 6 and exon 8. |
| T12 | 1173-1184 | Sentence | denotes | CONCLUSION: |
| T13 | 1185-1349 | Sentence | denotes | The mutation at splice donor site and the truncation of mRNA were identical with those of a recently reported Italian patient, although different in symptomatology. |
| T14 | 1350-1466 | Sentence | denotes | The application of blood leucocytes can be a simple technique on analysing a constructive abnormality of CYP27 mRNA. |
PubmedHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 215-228 | HP_0000991 | denotes | xanthomatosis |
DisGeNET5_gene_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 10519880-0#16#37#gene1593 | 16-37 | gene1593 | denotes | sterol 27-hydroxylase |
| 10519880-0#44#49#gene1593 | 44-49 | gene1593 | denotes | CYP27 |
| 10519880-0#131#161#diseaseC0238052 | 131-161 | diseaseC0238052 | denotes | cerebrotendinous xanthomatosis |
| 16#37#gene1593131#161#diseaseC0238052 | 10519880-0#16#37#gene1593 | 10519880-0#131#161#diseaseC0238052 | associated_with | sterol 27-hydroxylase,cerebrotendinous xanthomatosis |
| 44#49#gene1593131#161#diseaseC0238052 | 10519880-0#44#49#gene1593 | 10519880-0#131#161#diseaseC0238052 | associated_with | CYP27,cerebrotendinous xanthomatosis |
performance-test
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| PD-UBERON-AE-B_T1 | 448-453 | http://purl.obolibrary.org/obo/UBERON_0000178 | denotes | blood |
| PD-UBERON-AE-B_T2 | 1369-1374 | http://purl.obolibrary.org/obo/UBERON_0000178 | denotes | blood |
PubCasesHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| AB1 | 215-228 | HP:0000991 | denotes | xanthomatosis |
| TI1 | 148-161 | HP:0000991 | denotes | xanthomatosis |
PubCasesORDO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| AB1 | 198-228 | ORDO:909 | denotes | cerebrotendinous xanthomatosis |
| AB2 | 230-233 | ORDO:909 | denotes | CTX |
| TI1 | 131-161 | ORDO:909 | denotes | cerebrotendinous xanthomatosis |
UBERON-AE
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| PD-UBERON-AE-B_T1 | 448-453 | http://purl.obolibrary.org/obo/UBERON_0000178 | denotes | blood |
| PD-UBERON-AE-B_T2 | 1369-1374 | http://purl.obolibrary.org/obo/UBERON_0000178 | denotes | blood |
NCBIDiseaseCorpus
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 131-161 | SpecificDisease:D019294 | denotes | cerebrotendinous xanthomatosis |
| T2 | 198-228 | SpecificDisease:D019294 | denotes | cerebrotendinous xanthomatosis |
| T3 | 230-233 | SpecificDisease:D019294 | denotes | CTX |
| T4 | 1440-1460 | SpecificDisease:OMIM:213700 | denotes | abnormality of CYP27 |
DisGeNET
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T0 | 44-49 | gene:1593 | denotes | CYP27 |
| T1 | 131-161 | disease:C0238052 | denotes | cerebrotendinous xanthomatosis |
| T2 | 16-37 | gene:1593 | denotes | sterol 27-hydroxylase |
| T3 | 131-161 | disease:C0238052 | denotes | cerebrotendinous xanthomatosis |
| T4 | 313-318 | gene:1593 | denotes | CYP27 |
| T5 | 230-233 | disease:C0238052 | denotes | CTX |
| T6 | 313-318 | gene:1593 | denotes | CYP27 |
| T7 | 198-228 | disease:C0238052 | denotes | cerebrotendinous xanthomatosis |
| T8 | 285-306 | gene:1593 | denotes | sterol 27-hydroxylase |
| T9 | 230-233 | disease:C0238052 | denotes | CTX |
| T10 | 285-306 | gene:1593 | denotes | sterol 27-hydroxylase |
| T11 | 198-228 | disease:C0238052 | denotes | cerebrotendinous xanthomatosis |
| R1 | T0 | T1 | associated_with | CYP27,cerebrotendinous xanthomatosis |
| R2 | T2 | T3 | associated_with | sterol 27-hydroxylase,cerebrotendinous xanthomatosis |
| R3 | T4 | T5 | associated_with | CYP27,CTX |
| R4 | T6 | T7 | associated_with | CYP27,cerebrotendinous xanthomatosis |
| R5 | T8 | T9 | associated_with | sterol 27-hydroxylase,CTX |
| R6 | T10 | T11 | associated_with | sterol 27-hydroxylase,cerebrotendinous xanthomatosis |
NCBI-Disease-Train
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T4086 | 131-161 | SpecificDisease | denotes | cerebrotendinous xanthomatosis | D019294 |
| T4087 | 198-228 | SpecificDisease | denotes | cerebrotendinous xanthomatosis | D019294 |
| T4088 | 230-233 | SpecificDisease | denotes | CTX | D019294 |
| T4089 | 1440-1460 | SpecificDisease | denotes | abnormality of CYP27 | OMIM:213700 |
NCBI-Disease-Corpus-All
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T4086 | 131-161 | SpecificDisease | denotes | cerebrotendinous xanthomatosis | D019294 |
| T4087 | 198-228 | SpecificDisease | denotes | cerebrotendinous xanthomatosis | D019294 |
| T4088 | 230-233 | SpecificDisease | denotes | CTX | D019294 |
| T4089 | 1440-1460 | SpecificDisease | denotes | abnormality of CYP27 | OMIM:213700 |
NCBI-Disease-Corpus-2stage-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 131-161 | SpecificDisease | denotes | cerebrotendinous xanthomatosis |
| T2 | 198-228 | SpecificDisease | denotes | cerebrotendinous xanthomatosis |
| T3 | 230-233 | SpecificDisease | denotes | CTX |
NCBI-Disease-Corpus-rezarta-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 131-161 | SpecificDisease | denotes | cerebrotendinous xanthomatosis |
| T2 | 198-228 | SpecificDisease | denotes | cerebrotendinous xanthomatosis |
NCBI-Disease-Corpus-4oGuideline-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 131-161 | SpecificDisease | denotes | cerebrotendinous xanthomatosis |
| T2 | 198-234 | SpecificDisease | denotes | cerebrotendinous xanthomatosis (CTX) |
NCBI-Disease-Corpus-Simple-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 131-161 | SpecificDisease | denotes | cerebrotendinous xanthomatosis |
| T2 | 198-234 | SpecificDisease | denotes | cerebrotendinous xanthomatosis (CTX) |