PubMed:10482951
Annnotations
PubmedHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 227-252 | HP_0010864 | denotes | severe mental retardation |
| T2 | 234-252 | HP_0001249 | denotes | mental retardation |
| T3 | 254-276 | HP_0005484 | denotes | postnatal microcephaly |
| T4 | 264-276 | HP_0000252 | denotes | microcephaly |
| T5 | 278-289 | HP_0000154 | denotes | macrostomia |
| T6 | 294-304 | HP_0000303 | denotes | prognathia |
| T7 | 306-323 | HP_0001344 | denotes | absence of speech |
| T8 | 325-331 | HP_0001251 | denotes | ataxia |
| T9 | 339-356 | HP_0040082 | denotes | happy disposition |
| T10 | 438-445 | HP_0001513 | denotes | obesity |
| T11 | 447-465 | HP_0001252 | denotes | muscular hypotonia |
| T12 | 456-465 | HP_0001252 | denotes | hypotonia |
| T13 | 470-493 | HP_0001256 | denotes | mild mental retardation |
| T14 | 475-493 | HP_0001249 | denotes | mental retardation |
DisGeNET5_gene_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 10482951-4#28#33#gene6638 | 624-629 | gene6638 | denotes | SNRPN |
| 10482951-4#67#69#diseaseC0162635 | 663-665 | diseaseC0162635 | denotes | AS |
| 28#33#gene663867#69#diseaseC0162635 | 10482951-4#28#33#gene6638 | 10482951-4#67#69#diseaseC0162635 | associated_with | SNRPN,AS |
BioLarkPubmedHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| HP:0002187 | 227-252 | HP:0002187 | denotes | severe mental retardation |
| HP:0005484 | 254-276 | HP:0005484 | denotes | postnatal microcephaly |
| HP:0000181 | 278-289 | HP:0000181 | denotes | macrostomia |
| HP:0000303 | 294-304 | HP:0000303 | denotes | prognathia |
| HP:0001617 | 306-323 | HP:0001617 | denotes | absence of speech |
| HP:0001251 | 325-331 | HP:0001251 | denotes | ataxia |
| HP:0100024 | 339-356 | HP:0100024 | denotes | happy disposition |
| HP:0001513 | 438-445 | HP:0001513 | denotes | obesity |
| HP:0001252 | 447-465 | HP:0001252 | denotes | muscular hypotonia |
| HP:0001256 | 470-493 | HP:0001256 | denotes | mild mental retardation |
| T1 | 227-252 | HP:0002187 | denotes | severe mental retardation |
| T2 | 254-276 | HP:0005484 | denotes | postnatal microcephaly |
| T3 | 278-289 | HP:0000181 | denotes | macrostomia |
| T4 | 294-304 | HP:0000303 | denotes | prognathia |
| T5 | 306-323 | HP:0001617 | denotes | absence of speech |
| T6 | 325-331 | HP:0001251 | denotes | ataxia |
| T7 | 339-356 | HP:0100024 | denotes | happy disposition |
| T8 | 438-445 | HP:0001513 | denotes | obesity |
| T9 | 447-465 | HP:0001252 | denotes | muscular hypotonia |
| T10 | 470-493 | HP:0001256 | denotes | mild mental retardation |
| T1 | 227-252 | HP:0002187 | denotes | severe mental retardation |
| T2 | 254-276 | HP:0005484 | denotes | postnatal microcephaly |
| T3 | 278-289 | HP:0000181 | denotes | macrostomia |
| T4 | 294-304 | HP:0000303 | denotes | prognathia |
| T5 | 306-323 | HP:0001617 | denotes | absence of speech |
| T6 | 325-331 | HP:0001251 | denotes | ataxia |
| T7 | 339-356 | HP:0100024 | denotes | happy disposition |
| T8 | 438-445 | HP:0001513 | denotes | obesity |
| T9 | 447-465 | HP:0001252 | denotes | muscular hypotonia |
| T10 | 470-493 | HP:0001256 | denotes | mild mental retardation |
| T1 | 227-252 | HP:0002187 | denotes | severe mental retardation |
| T2 | 254-276 | HP:0005484 | denotes | postnatal microcephaly |
| T3 | 278-289 | HP:0000181 | denotes | macrostomia |
| T4 | 294-304 | HP:0000303 | denotes | prognathia |
| T5 | 306-323 | HP:0001617 | denotes | absence of speech |
| T6 | 325-331 | HP:0001251 | denotes | ataxia |
| T7 | 339-356 | HP:0100024 | denotes | happy disposition |
| T8 | 438-445 | HP:0001513 | denotes | obesity |
| T9 | 447-465 | HP:0001252 | denotes | muscular hypotonia |
| T10 | 470-493 | HP:0001256 | denotes | mild mental retardation |
PubCasesHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TI1 | 53-60 | HP:0001513 | denotes | obesity |
| TI2 | 62-80 | HP:0001252 | denotes | muscular hypotonia |
| AB1 | 254-276 | HP:0005484 | denotes | postnatal microcephaly |
| AB2 | 325-331 | HP:0001251 | denotes | ataxia |
| AB3 | 438-445 | HP:0001513 | denotes | obesity |
| AB4 | 447-465 | HP:0001252 | denotes | muscular hypotonia |
sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TextSentencer_T1 | 0-169 | Sentence | denotes | A previously unrecognised phenotype characterised by obesity, muscular hypotonia, and ability to speak in patients with Angelman syndrome caused by an imprinting defect. |
| TextSentencer_T2 | 170-357 | Sentence | denotes | The clinical features of Angelman syndrome (AS) comprise severe mental retardation, postnatal microcephaly, macrostomia and prognathia, absence of speech, ataxia, and a happy disposition. |
| TextSentencer_T3 | 358-494 | Sentence | denotes | We report on seven patients who lack most of these features, but presented with obesity, muscular hypotonia and mild mental retardation. |
| TextSentencer_T4 | 495-595 | Sentence | denotes | Based on the latter findings, the patients were initially suspected of having Prader-Willi syndrome. |
| TextSentencer_T5 | 596-716 | Sentence | denotes | DNA methylation analysis of SNRPN and D15S63, however, revealed an AS pattern, ie the maternal band was faint or absent. |
| TextSentencer_T6 | 717-837 | Sentence | denotes | Cytogenetic studies and microsatellite analysis demonstrated apparently normal chromosomes 15 of biparental inheritance. |
| TextSentencer_T7 | 838-937 | Sentence | denotes | We conclude that these patients have an imprinting defect and a previously unrecognised form of AS. |
| TextSentencer_T8 | 938-1034 | Sentence | denotes | The mild phenotype may be explained by an incomplete imprinting defect or by cellular mosaicism. |
| T1 | 0-169 | Sentence | denotes | A previously unrecognised phenotype characterised by obesity, muscular hypotonia, and ability to speak in patients with Angelman syndrome caused by an imprinting defect. |
| T2 | 170-357 | Sentence | denotes | The clinical features of Angelman syndrome (AS) comprise severe mental retardation, postnatal microcephaly, macrostomia and prognathia, absence of speech, ataxia, and a happy disposition. |
| T3 | 358-494 | Sentence | denotes | We report on seven patients who lack most of these features, but presented with obesity, muscular hypotonia and mild mental retardation. |
| T4 | 495-595 | Sentence | denotes | Based on the latter findings, the patients were initially suspected of having Prader-Willi syndrome. |
| T5 | 596-716 | Sentence | denotes | DNA methylation analysis of SNRPN and D15S63, however, revealed an AS pattern, ie the maternal band was faint or absent. |
| T6 | 717-837 | Sentence | denotes | Cytogenetic studies and microsatellite analysis demonstrated apparently normal chromosomes 15 of biparental inheritance. |
| T7 | 838-937 | Sentence | denotes | We conclude that these patients have an imprinting defect and a previously unrecognised form of AS. |
| T8 | 938-1034 | Sentence | denotes | The mild phenotype may be explained by an incomplete imprinting defect or by cellular mosaicism. |
PubCasesORDO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| AB1 | 195-212 | ORDO:72 | denotes | Angelman syndrome |
| AB2 | 278-289 | ORDO:141276 | denotes | macrostomia |
| TI1 | 120-137 | ORDO:72 | denotes | Angelman syndrome |
| AB3 | 573-594 | ORDO:739 | denotes | Prader-Willi syndrome |
DisGeNET
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T0 | 624-629 | gene:6638 | denotes | SNRPN |
| T1 | 663-665 | disease:C0162635 | denotes | AS |
| R1 | T0 | T1 | associated_with | SNRPN,AS |