PubMed:10465113
Annnotations
PMID_GLOBAL
| Id | Subject | Object | Predicate | Lexical cue | mondo_id |
|---|---|---|---|---|---|
| T1 | 22-51 | DiseaseOrPhenotypicFeature | denotes | multiple epiphyseal dysplasia | 0016648 |
| T2 | 73-82 | DiseaseOrPhenotypicFeature | denotes | club foot | 0007342 |
| T3 | 191-212 | DiseaseOrPhenotypicFeature | denotes | diastrophic dysplasia | 0009107 |
| T4 | 291-306 | DiseaseOrPhenotypicFeature | denotes | achondrogenesis | 0019648 |
| T5 | 311-327 | DiseaseOrPhenotypicFeature | denotes | atelosteogenesis | 0000389 |
| T6 | 335-356 | DiseaseOrPhenotypicFeature | denotes | diastrophic dysplasia | 0009107 |
| T7 | 699-728 | DiseaseOrPhenotypicFeature | denotes | multiple epiphyseal dysplasia | 0016648 |
| T8 | 749-758 | DiseaseOrPhenotypicFeature | denotes | club foot | 0007342 |
| T9 | 820-849 | DiseaseOrPhenotypicFeature | denotes | multiple epiphyseal dysplasia | 0016648 |
| T10 | 940-952 | DiseaseOrPhenotypicFeature | denotes | Cleft palate | 0007336|0016064 |
| T12 | 1171-1177 | DiseaseOrPhenotypicFeature | denotes | defect | 0008568 |
| T13 | 1323-1352 | DiseaseOrPhenotypicFeature | denotes | Multiple epiphyseal dysplasia | 0016648 |
| T14 | 1414-1418 | DiseaseOrPhenotypicFeature | denotes | EDM1 | 0007561 |
| T15 | 1455-1459 | DiseaseOrPhenotypicFeature | denotes | EDM2 | 0010844 |
| T16 | 1624-1627 | DiseaseOrPhenotypicFeature | denotes | MED | 0016648 |
| T17 | 1629-1633 | DiseaseOrPhenotypicFeature | denotes | EDM4 | 0009189 |
sentences
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TextSentencer_T1 | 0-138 | Sentence | denotes | Recessively inherited multiple epiphyseal dysplasia with normal stature, club foot, and double layered patella caused by a DTDST mutation. |
| TextSentencer_T2 | 139-357 | Sentence | denotes | We have observed over 25 different mutations in the diastrophic dysplasia sulphate transporter gene (DTDST) in association with the recessive disorders achondrogenesis 1B, atelosteogenesis 2, and diastrophic dysplasia. |
| TextSentencer_T3 | 358-513 | Sentence | denotes | The c862t (R279W) transition is the most common mutation in non-Finnish patients, but in these disorders it is usually combined with other DTDST mutations. |
| TextSentencer_T4 | 514-729 | Sentence | denotes | We had not seen a case of homozygosity for c862t (R279W) until we analysed DNA from a 36 year old male with tall-normal stature (180 cm) who asked for genetic counselling for suspected multiple epiphyseal dysplasia. |
| TextSentencer_T5 | 730-786 | Sentence | denotes | He was treated for club foot and hip dysplasia at birth. |
| TextSentencer_T6 | 787-939 | Sentence | denotes | Skeletal changes consistent with multiple epiphyseal dysplasia, with the peculiar finding of a double layered patella, were recognised during childhood. |
| TextSentencer_T7 | 940-1015 | Sentence | denotes | Cleft palate, swelling of the ear pinna, and hitch hiker thumb were absent. |
| TextSentencer_T8 | 1016-1205 | Sentence | denotes | He was found to be homozygous, and both healthy parents heterozygous, for the R279W mutation in DTDST, and his fibroblasts showed a sulphate incorporation defect typical of DTDST disorders. |
| TextSentencer_T9 | 1206-1322 | Sentence | denotes | Counselling was given for a recessive disorder, thereby considerably reducing the probability of affected offspring. |
| TextSentencer_T10 | 1323-1478 | Sentence | denotes | Multiple epiphyseal dysplasia is more frequently caused by dominant mutations in the COMP (EDM1, McKusick 132400) and COL9A2 genes (EDM2, McKusick 600204). |
| TextSentencer_T11 | 1479-1652 | Sentence | denotes | A few other patients and families with features similar to our proband have been described previously and considered to have autosomal recessive MED (EDM4, McKusick 226900). |
| TextSentencer_T12 | 1653-1795 | Sentence | denotes | This observation confirms the existence of this entity and assigns it to the phenotypic spectrum associated with mutations at the DTDST locus. |
| T1 | 0-138 | Sentence | denotes | Recessively inherited multiple epiphyseal dysplasia with normal stature, club foot, and double layered patella caused by a DTDST mutation. |
| T2 | 139-357 | Sentence | denotes | We have observed over 25 different mutations in the diastrophic dysplasia sulphate transporter gene (DTDST) in association with the recessive disorders achondrogenesis 1B, atelosteogenesis 2, and diastrophic dysplasia. |
| T3 | 358-513 | Sentence | denotes | The c862t (R279W) transition is the most common mutation in non-Finnish patients, but in these disorders it is usually combined with other DTDST mutations. |
| T4 | 514-729 | Sentence | denotes | We had not seen a case of homozygosity for c862t (R279W) until we analysed DNA from a 36 year old male with tall-normal stature (180 cm) who asked for genetic counselling for suspected multiple epiphyseal dysplasia. |
| T5 | 730-786 | Sentence | denotes | He was treated for club foot and hip dysplasia at birth. |
| T6 | 787-939 | Sentence | denotes | Skeletal changes consistent with multiple epiphyseal dysplasia, with the peculiar finding of a double layered patella, were recognised during childhood. |
| T7 | 940-1015 | Sentence | denotes | Cleft palate, swelling of the ear pinna, and hitch hiker thumb were absent. |
| T8 | 1016-1205 | Sentence | denotes | He was found to be homozygous, and both healthy parents heterozygous, for the R279W mutation in DTDST, and his fibroblasts showed a sulphate incorporation defect typical of DTDST disorders. |
| T9 | 1206-1322 | Sentence | denotes | Counselling was given for a recessive disorder, thereby considerably reducing the probability of affected offspring. |
| T10 | 1323-1478 | Sentence | denotes | Multiple epiphyseal dysplasia is more frequently caused by dominant mutations in the COMP (EDM1, McKusick 132400) and COL9A2 genes (EDM2, McKusick 600204). |
| T11 | 1479-1652 | Sentence | denotes | A few other patients and families with features similar to our proband have been described previously and considered to have autosomal recessive MED (EDM4, McKusick 226900). |
| T12 | 1653-1795 | Sentence | denotes | This observation confirms the existence of this entity and assigns it to the phenotypic spectrum associated with mutations at the DTDST locus. |
PubmedHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 699-728 | HP_0002654 | denotes | multiple epiphyseal dysplasia |
| T2 | 708-728 | HP_0002656 | denotes | epiphyseal dysplasia |
| T3 | 749-758 | HP_0001762 | denotes | club foot |
| T4 | 749-753 | HP_0001217 | denotes | club |
| T5 | 763-776 | HP_0001385 | denotes | hip dysplasia |
| T6 | 820-849 | HP_0002654 | denotes | multiple epiphyseal dysplasia |
| T7 | 829-849 | HP_0002656 | denotes | epiphyseal dysplasia |
| T8 | 940-952 | HP_0000175 | denotes | Cleft palate |
| T9 | 1323-1352 | HP_0002654 | denotes | Multiple epiphyseal dysplasia |
| T10 | 1332-1352 | HP_0002656 | denotes | epiphyseal dysplasia |
| T11 | 1604-1623 | HP_0000007 | denotes | autosomal recessive |
DisGeNET5_variant_disease
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| 10465113-3#50#55#geners104893915 | 564-569 | geners104893915 | denotes | R279W |
| 10465113-3#185#214#diseaseC0026760 | 699-728 | diseaseC0026760 | denotes | multiple epiphyseal dysplasia |
| 50#55#geners104893915185#214#diseaseC0026760 | 10465113-3#50#55#geners104893915 | 10465113-3#185#214#diseaseC0026760 | associated_with | R279W,multiple epiphyseal dysplasia |
PubCasesHPO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| TI1 | 22-51 | HP:0002654 | denotes | multiple epiphyseal dysplasia |
| TI2 | 73-77 | HP:0001217 | denotes | club |
| TI3 | 88-110 | HP:0031174 | denotes | double layered patella |
| AB1 | 699-728 | HP:0002654 | denotes | multiple epiphyseal dysplasia |
| AB2 | 749-753 | HP:0001217 | denotes | club |
| AB3 | 763-776 | HP:0001385 | denotes | hip dysplasia |
| AB4 | 820-849 | HP:0002654 | denotes | multiple epiphyseal dysplasia |
| AB5 | 882-904 | HP:0031174 | denotes | double layered patella |
| AB6 | 940-952 | HP:0000175 | denotes | Cleft palate |
| AB7 | 1323-1352 | HP:0002654 | denotes | Multiple epiphyseal dysplasia |
PubCasesORDO
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| AB1 | 191-212 | ORDO:628 | denotes | diastrophic dysplasia |
| AB2 | 291-306 | ORDO:932 | denotes | achondrogenesis |
| AB3 | 335-356 | ORDO:628 | denotes | diastrophic dysplasia |
| AB4 | 1414-1418 | ORDO:93308 | denotes | EDM1 |
| AB5 | 1629-1633 | ORDO:93307 | denotes | EDM4 |
UBERON-AE
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| PD-UBERON-AE-B_T1 | 103-110 | http://purl.obolibrary.org/obo/UBERON_0002446 | denotes | patella |
| PD-UBERON-AE-B_T2 | 897-904 | http://purl.obolibrary.org/obo/UBERON_0002446 | denotes | patella |
| PD-UBERON-AE-B_T3 | 763-766 | http://purl.obolibrary.org/obo/UBERON_0001464 | denotes | hip |
| PD-UBERON-AE-B_T4 | 970-973 | http://purl.obolibrary.org/obo/UBERON_0001690 | denotes | ear |
| PD-UBERON-AE-B_T5 | 974-979 | http://purl.obolibrary.org/obo/UBERON_0001757 | denotes | pinna |
performance-test
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| PD-UBERON-AE-B_T1 | 103-110 | http://purl.obolibrary.org/obo/UBERON_0002446 | denotes | patella |
| PD-UBERON-AE-B_T2 | 897-904 | http://purl.obolibrary.org/obo/UBERON_0002446 | denotes | patella |
| PD-UBERON-AE-B_T3 | 763-766 | http://purl.obolibrary.org/obo/UBERON_0001464 | denotes | hip |
| PD-UBERON-AE-B_T4 | 970-973 | http://purl.obolibrary.org/obo/UBERON_0001690 | denotes | ear |
| PD-UBERON-AE-B_T5 | 974-979 | http://purl.obolibrary.org/obo/UBERON_0001757 | denotes | pinna |
NCBIDiseaseCorpus
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 22-51 | SpecificDisease:D010009 | denotes | multiple epiphyseal dysplasia |
| T2 | 73-82 | SpecificDisease:D003025 | denotes | club foot |
| T3 | 88-110 | DiseaseClass:C535504 | denotes | double layered patella |
| T4 | 191-212 | Modifier:C536170 | denotes | diastrophic dysplasia |
| T5 | 271-290 | DiseaseClass:D030342 | denotes | recessive disorders |
| T6 | 291-309 | SpecificDisease:C536016 | denotes | achondrogenesis 1B |
| T7 | 311-329 | SpecificDisease:C535395 | denotes | atelosteogenesis 2 |
| T8 | 335-356 | SpecificDisease:C536170 | denotes | diastrophic dysplasia |
| T9 | 699-728 | SpecificDisease:D010009 | denotes | multiple epiphyseal dysplasia |
| T10 | 749-758 | SpecificDisease:D003025 | denotes | club foot |
| T11 | 763-776 | SpecificDisease:D006618 | denotes | hip dysplasia |
| T12 | 820-849 | SpecificDisease:D010009 | denotes | multiple epiphyseal dysplasia |
| T13 | 882-904 | DiseaseClass:C535504 | denotes | double layered patella |
| T14 | 940-952 | SpecificDisease:D002972 | denotes | Cleft palate |
| T15 | 954-979 | DiseaseClass:D004427 | denotes | swelling of the ear pinna |
| T16 | 985-1002 | DiseaseClass:C536903 | denotes | hitch hiker thumb |
| T17 | 1189-1204 | SpecificDisease:D030342 | denotes | DTDST disorders |
| T18 | 1234-1252 | DiseaseClass:D030342 | denotes | recessive disorder |
| T19 | 1323-1352 | SpecificDisease:D010009 | denotes | Multiple epiphyseal dysplasia |
| T20 | 1414-1418 | SpecificDisease:OMIM:132400 | denotes | EDM1 |
| T21 | 1455-1459 | SpecificDisease:OMIM:600204 | denotes | EDM2 |
| T22 | 1624-1627 | SpecificDisease:D010009 | denotes | MED |
| T23 | 1629-1633 | SpecificDisease:OMIM:226900 | denotes | EDM4 |
NCBI-Disease-Train
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T1234 | 22-51 | SpecificDisease | denotes | multiple epiphyseal dysplasia | D010009 |
| T1235 | 73-82 | SpecificDisease | denotes | club foot | D003025 |
| T1236 | 88-110 | DiseaseClass | denotes | double layered patella | C535504 |
| T1237 | 191-212 | Modifier | denotes | diastrophic dysplasia | C536170 |
| T1238 | 271-290 | DiseaseClass | denotes | recessive disorders | D030342 |
| T1239 | 291-309 | SpecificDisease | denotes | achondrogenesis 1B | C536016 |
| T1240 | 311-329 | SpecificDisease | denotes | atelosteogenesis 2 | C535395 |
| T1241 | 335-356 | SpecificDisease | denotes | diastrophic dysplasia | C536170 |
| T1242 | 699-728 | SpecificDisease | denotes | multiple epiphyseal dysplasia | D010009 |
| T1243 | 749-758 | SpecificDisease | denotes | club foot | D003025 |
| T1244 | 763-776 | SpecificDisease | denotes | hip dysplasia | D006618 |
| T1245 | 820-849 | SpecificDisease | denotes | multiple epiphyseal dysplasia | D010009 |
| T1246 | 882-904 | DiseaseClass | denotes | double layered patella | C535504 |
| T1247 | 940-952 | SpecificDisease | denotes | Cleft palate | D002972 |
| T1248 | 954-979 | DiseaseClass | denotes | swelling of the ear pinna | D004427 |
| T1249 | 985-1002 | DiseaseClass | denotes | hitch hiker thumb | C536903 |
| T1250 | 1189-1204 | SpecificDisease | denotes | DTDST disorders | D030342 |
| T1251 | 1234-1252 | DiseaseClass | denotes | recessive disorder | D030342 |
| T1252 | 1323-1352 | SpecificDisease | denotes | Multiple epiphyseal dysplasia | D010009 |
| T1253 | 1414-1418 | SpecificDisease | denotes | EDM1 | OMIM:132400 |
| T1254 | 1455-1459 | SpecificDisease | denotes | EDM2 | OMIM:600204 |
| T1255 | 1624-1627 | SpecificDisease | denotes | MED | D010009 |
| T1256 | 1629-1633 | SpecificDisease | denotes | EDM4 | OMIM:226900 |
NCBI-Disease-Corpus-All
| Id | Subject | Object | Predicate | Lexical cue | database_id |
|---|---|---|---|---|---|
| T1234 | 22-51 | SpecificDisease | denotes | multiple epiphyseal dysplasia | D010009 |
| T1235 | 73-82 | SpecificDisease | denotes | club foot | D003025 |
| T1236 | 88-110 | DiseaseClass | denotes | double layered patella | C535504 |
| T1237 | 191-212 | Modifier | denotes | diastrophic dysplasia | C536170 |
| T1238 | 271-290 | DiseaseClass | denotes | recessive disorders | D030342 |
| T1239 | 291-309 | SpecificDisease | denotes | achondrogenesis 1B | C536016 |
| T1240 | 311-329 | SpecificDisease | denotes | atelosteogenesis 2 | C535395 |
| T1241 | 335-356 | SpecificDisease | denotes | diastrophic dysplasia | C536170 |
| T1242 | 699-728 | SpecificDisease | denotes | multiple epiphyseal dysplasia | D010009 |
| T1243 | 749-758 | SpecificDisease | denotes | club foot | D003025 |
| T1244 | 763-776 | SpecificDisease | denotes | hip dysplasia | D006618 |
| T1245 | 820-849 | SpecificDisease | denotes | multiple epiphyseal dysplasia | D010009 |
| T1246 | 882-904 | DiseaseClass | denotes | double layered patella | C535504 |
| T1247 | 940-952 | SpecificDisease | denotes | Cleft palate | D002972 |
| T1248 | 954-979 | DiseaseClass | denotes | swelling of the ear pinna | D004427 |
| T1249 | 985-1002 | DiseaseClass | denotes | hitch hiker thumb | C536903 |
| T1250 | 1189-1204 | SpecificDisease | denotes | DTDST disorders | D030342 |
| T1251 | 1234-1252 | DiseaseClass | denotes | recessive disorder | D030342 |
| T1252 | 1323-1352 | SpecificDisease | denotes | Multiple epiphyseal dysplasia | D010009 |
| T1253 | 1414-1418 | SpecificDisease | denotes | EDM1 | OMIM:132400 |
| T1254 | 1455-1459 | SpecificDisease | denotes | EDM2 | OMIM:600204 |
| T1255 | 1624-1627 | SpecificDisease | denotes | MED | D010009 |
| T1256 | 1629-1633 | SpecificDisease | denotes | EDM4 | OMIM:226900 |
NCBI-Disease-Corpus-2stage-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 22-51 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T2 | 73-82 | SpecificDisease | denotes | club foot |
| T3 | 291-309 | SpecificDisease | denotes | achondrogenesis 1B |
| T4 | 311-329 | SpecificDisease | denotes | atelosteogenesis 2 |
| T5 | 335-356 | SpecificDisease | denotes | diastrophic dysplasia |
| T6 | 699-728 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T7 | 749-758 | SpecificDisease | denotes | club foot |
| T8 | 763-776 | SpecificDisease | denotes | hip dysplasia |
| T9 | 820-849 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T10 | 1323-1352 | SpecificDisease | denotes | Multiple epiphyseal dysplasia |
| T11 | 1624-1627 | SpecificDisease | denotes | MED |
NCBI-Disease-Corpus-rezarta-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 22-51 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T2 | 73-82 | SpecificDisease | denotes | club foot |
| T3 | 291-309 | DiseaseClass | denotes | achondrogenesis 1B |
| T4 | 311-329 | DiseaseClass | denotes | atelosteogenesis 2 |
| T5 | 335-356 | DiseaseClass | denotes | diastrophic dysplasia |
| T6 | 699-728 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T7 | 749-758 | SpecificDisease | denotes | club foot |
| T8 | 763-776 | SpecificDisease | denotes | hip dysplasia |
| T9 | 820-849 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T10 | 1323-1352 | SpecificDisease | denotes | Multiple epiphyseal dysplasia |
| T11 | 1624-1627 | Modifier | denotes | MED |
NCBI-Disease-Corpus-4oGuideline-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 22-51 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T2 | 73-82 | SpecificDisease | denotes | club foot |
| T3 | 88-110 | SpecificDisease | denotes | double layered patella |
| T4 | 291-356 | CompositeMention | denotes | achondrogenesis 1B, atelosteogenesis 2, and diastrophic dysplasia |
| T5 | 699-728 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T6 | 749-758 | SpecificDisease | denotes | club foot |
| T7 | 763-776 | SpecificDisease | denotes | hip dysplasia |
| T8 | 820-849 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T9 | 882-904 | SpecificDisease | denotes | double layered patella |
| T10 | 1234-1252 | DiseaseClass | denotes | recessive disorder |
| T11 | 1323-1352 | SpecificDisease | denotes | Multiple epiphyseal dysplasia |
| T12 | 1604-1627 | DiseaseClass | denotes | autosomal recessive MED |
NCBI-Disease-Corpus-Simple-All
| Id | Subject | Object | Predicate | Lexical cue |
|---|---|---|---|---|
| T1 | 22-51 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T2 | 57-71 | Modifier | denotes | normal stature |
| T3 | 73-82 | SpecificDisease | denotes | club foot |
| T4 | 88-110 | Modifier | denotes | double layered patella |
| T5 | 191-212 | SpecificDisease | denotes | diastrophic dysplasia |
| T6 | 291-309 | SpecificDisease | denotes | achondrogenesis 1B |
| T7 | 311-329 | SpecificDisease | denotes | atelosteogenesis 2 |
| T8 | 335-356 | SpecificDisease | denotes | diastrophic dysplasia |
| T9 | 622-641 | Modifier | denotes | tall-normal stature |
| T10 | 699-728 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T11 | 749-758 | SpecificDisease | denotes | club foot |
| T12 | 763-776 | SpecificDisease | denotes | hip dysplasia |
| T13 | 820-849 | SpecificDisease | denotes | multiple epiphyseal dysplasia |
| T14 | 882-904 | Modifier | denotes | double layered patella |
| T15 | 940-952 | Modifier | denotes | Cleft palate |
| T16 | 1323-1352 | SpecificDisease | denotes | Multiple epiphyseal dysplasia |
| T17 | 1604-1627 | CompositeMention | denotes | autosomal recessive MED |