Id |
Subject |
Object |
Predicate |
Lexical cue |
TextSentencer_T1 |
0-73 |
Sentence |
denotes |
von Willebrand disease with G4022A mutation (vWd Sungnam): a case report. |
TextSentencer_T2 |
74-234 |
Sentence |
denotes |
A 10-year-old male patient affected by type 2 von Willebrand disease (vWD) and his family members were investigated by hemostatic and molecular genetic studies. |
TextSentencer_T3 |
235-527 |
Sentence |
denotes |
The propositus, who experienced frequent bleeding episodes, was characterized by a normal level of von Willebrand factor (vWF) antigen (54%), reduced vWF ristocetin cofactor activity (5%), decreased factor VIII clotting activity (25%) and absent high molecular weight multimers in the plasma. |
TextSentencer_T4 |
528-638 |
Sentence |
denotes |
An exon 28 fragment coding for the A1 and A2 domains was amplified by polymerase chain reaction and sequenced. |
TextSentencer_T5 |
639-777 |
Sentence |
denotes |
We found a heterozygous mutation (G4022A), producing an additional PstI restriction site, which resulted in the substitution of Arg578Gln. |
TextSentencer_T6 |
778-903 |
Sentence |
denotes |
Family studies, including the parents and a brother, were negative for this mutation and vWF abnormalities were not observed. |
TextSentencer_T7 |
904-1069 |
Sentence |
denotes |
We confirmed that G to A mutation in the region of the platelet glycoprotein Ib binding domain of vWF causes the qualitative type 2 defect in von Willebrand disease. |
T1 |
0-73 |
Sentence |
denotes |
von Willebrand disease with G4022A mutation (vWd Sungnam): a case report. |
T2 |
74-234 |
Sentence |
denotes |
A 10-year-old male patient affected by type 2 von Willebrand disease (vWD) and his family members were investigated by hemostatic and molecular genetic studies. |
T3 |
235-527 |
Sentence |
denotes |
The propositus, who experienced frequent bleeding episodes, was characterized by a normal level of von Willebrand factor (vWF) antigen (54%), reduced vWF ristocetin cofactor activity (5%), decreased factor VIII clotting activity (25%) and absent high molecular weight multimers in the plasma. |
T4 |
528-638 |
Sentence |
denotes |
An exon 28 fragment coding for the A1 and A2 domains was amplified by polymerase chain reaction and sequenced. |
T5 |
639-777 |
Sentence |
denotes |
We found a heterozygous mutation (G4022A), producing an additional PstI restriction site, which resulted in the substitution of Arg578Gln. |
T6 |
778-903 |
Sentence |
denotes |
Family studies, including the parents and a brother, were negative for this mutation and vWF abnormalities were not observed. |
T7 |
904-1069 |
Sentence |
denotes |
We confirmed that G to A mutation in the region of the platelet glycoprotein Ib binding domain of vWF causes the qualitative type 2 defect in von Willebrand disease. |