Control Range   Zellweger Spectrum Range   Family 1   Family 5
II:3   II:2
VLCFA concentration (μmol/l)  C22:0  3.84–10.2  2.36–5.59  4.43  3.67
C24:0  7.76–17.66  5.41–13.39  8.36  8.58
C26:0  0.18–0.38  0.59–3.38  0.24  0.22
VLCFA ratio  C24:0/C22:0  1.55–2.3  2.08–3.4  1.89  2.34
C26:0/C22:0  0.03–0.07  0.11–1.17  0.05  0.06
DHAPAT activity [nmol/(2h × mg protein)]  5.4–10.6  0.1–0.9  7.1  14
ACOX1 immunoblot  72 kDa  +  +  +  +
52 kDa  +  −  +  +
20 kDa  ++  −  +  +
Thiolase immunoblot  44 kDa  −  +  −  −
41 kDa  +  −  +  +
α oxidation activity [pmol/(h × mg protein)]  phytanic acid substrate  28–95  0–10  34  39
β oxidation activity [pmol/(h × mg protein)]  C16:0 substrate  3,330–7,790  3,330–7,790  7,162  5,959
C26:0 substrate  800–2,040  50–350  1,088  1,013
pristanic acid substrate  790–1,690  0–30  1,092  756