Subject   cI/CS a   cII/CS a   cIII/CS a   cIV/CS a   CS b
Muscle biopsy  S1  142  44∗  91  20∗  90
S2  47∗  11∗  32∗  3∗  374∗
S3  140  69  93  5∗  119
S4  58  100  42∗  8∗  29∗
S6  127  81  132  36∗  100
Skin biopsy  S1  128  58  105  61  101
S2  56  54∗  82  50∗  147
S4  58  98  104  25∗  150∗