Our case differs, however, in that the medullary lesion was confined to a tiny portion of the dorsal region, and seems too small to be responsible for expansion of the cervicomedullary lesion, suggesting that the latter, which is reminiscent of chronic progressive neuro-Behçet’s disease, results from a different pathological process. [12]. In neuro-Behçet’s disease, subacute brainstem encephalitis, which is the most common in parenchymal involvement, shows hypertense T2 lesion with contrast enhancement. Spontaneous self-remission without therapy has been reported, although, some patients develop a slowly progressive disease with insidiously advancing brainstem atrophy [12].