Table 2  Summary of additional blood amino acid levels in the intermediate MSUD model and littermate controls as determined by tandem mass spectrometry. Samples were collected from mice that were 4–6 weeks of age. All values are mean +/- SEM.
MSUD Genotype  Alanine  Glutamate  Glutamine
(μmole/L)
control  225.2 ± 36.6 (11)  106.5 ± 10.5 (11)  67.8 ± 7.6 (11)
525A  175.0 ± 28.7 (10)  68.4 ± 7.7** (10)  58.0 ± 7.0 (10)
A  144.1 ± 16.9* (10)  65.9 ± 8.9** (10)  37.7 ± 6.5**,*** (10)
*: Significantly different from control (P < 0.05).
**: Significantly different from control (P < 0.01).
***: Significantly different from Line 525A (P < 0.05).