MSUD Genotype  Alanine  Glutamate  Glutamine
(μmole/L)
+/+  196.1 ± 23.1 (6)  229.0 ± 12.0 (6)  76.8 ± 3.0 (6)
+/-  167.6 ± 9.9 (13)  251.0 ± 12.8 (13)  72.3 ± 1.6 (13)
-/-  94.6 ± 11.6* (5)  107.8 ± 4.8* (5)  50.4 ± 2.9* (5)